scholarly journals Recklinghausen neurofibromatosis variant

2021 ◽  
Vol XXX (3-4) ◽  
pp. 52-53
Author(s):  
Z. A. Zalyalova ◽  
F. Y. Yusupov ◽  
L. Y. Mukhametshina
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Peripheral Nerves ◽  
Skin Pigmentation ◽  
Hereditary Disease ◽  
Internal Organs ◽  
The Central Nervous System ◽  
Bone Anomalies

Neurofibromatosis is a hereditary disease characterized by the presence of many tumors located in the skin, along the peripheral nerves, in the central nervous system, skin pigmentation with bone anomalies, and damage to internal organs.

FEATURES OF THE PRODUCTION TECHNOLOGY LOW-PROTEIN FOODS

2021 ◽  
Vol 14 (3(53)) ◽  
pp. 98-104
Author(s):  
Alexey Iosifovich Grigel
Keyword(s):  
Amino Acids ◽  
Central Nervous System ◽  
Nervous System ◽  
Life Support ◽  
Hereditary Disease ◽  
Bakery Products ◽  
Severe Damage ◽  
Low Protein ◽  
The Central Nervous System ◽  
Manufacturing Technologies

Phenylketonuria is a hereditary disease associated with a violation of the metabolism of amino acids, in particular phenylalanine. It is accompanied by the accumulation of phenylalanine and its toxic products in the tissues, which leads to severe damage to the central nervous system, manifested, in particular, in a violation of mental development. An important component of the life support of such patients is the observance of a low-protein diet. The article describes the features of manufacturing technologies for lowprotein products, including such as low-protein pasta and cereals, low-protein dry mixes, small-piece bakery products. The technological process and equipment for the production of low-protein products are described, as well as the characteristics of the intake range of products are given.

Degeneration of skeletal muscle, peripheral nerves, and the central nervous system in transgenic mice overexpressing wild-type prion proteins

Cell ◽  
1994 ◽  
Vol 76 (1) ◽  
pp. 117-129 ◽  
Author(s):  
David Westaway ◽  
Stephen J. DeArmond ◽  
Juliana Cayetano-Canlas ◽  
Darlene Groth ◽  
Dallas Foster ◽  
...  
Keyword(s):  
Skeletal Muscle ◽  
Central Nervous System ◽  
Nervous System ◽  
Transgenic Mice ◽  
Peripheral Nerves ◽  
Prion Proteins ◽  
Wild Type ◽  
The Central Nervous System

STUDIES ON THE ANATOMY OF LYMNAEA HUMILIS SAY

1957 ◽  
Vol 35 (6) ◽  
pp. 751-768 ◽  
Author(s):  
Bruce M. McCraw
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Male Copulatory Organ ◽  
Vas Deferens ◽  
Lymnaea Stagnalis ◽  
Copulatory Organ ◽  
Accessory Structure ◽  
Internal Organs ◽  
Distinct Entity ◽  
The Central Nervous System

The topographic anatomy of Lymnaea humilis is described, giving the relative positions of the various internal organs. A description of the anatomy of the cephalic hemocoele is also given. Like Lymnaea stagnalis the central nervous system of L. humilis consists of the paired cerebral, buccal, pedal, pleural, and parietal ganglia and the unpaired abdominal ganglion. The nerves arising from the central nervous system are described and particular attention was devoted to the nerves arising from the pedal ganglia and innervating the foot; fourteen new nerves are named or described. The reproductive system of L. humilis is divided into: (a) the ovotestis and its duct, (b) the female system, and (c) the male system. In reproductively active snails, the female system is the largest of the three portions, and consists of the uterus, oothecal gland, vagina, and seminal receptacle. An accessory structure, the albumen gland, is very large in L. humilis. The male system consists of the upper and lower prostate, vas deferens, and male copulatory organ. The connections between the hermaphrodite duct and the male and female systems show considerable structural consolidation compared to these connections in L. stagnalis. The muciparous gland is not a distinct entity in L. humilis.

scholarly journals Filament proteins in central, cranial, and peripheral mammalian nerves.

1981 ◽  
Vol 88 (1) ◽  
pp. 67-72 ◽  
Author(s):  
P F Davison ◽  
R N Jones
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Glial Fibrillary Acidic Protein ◽  
Peripheral Nerves ◽  
Mammalian Cells ◽  
Cranial Nerves ◽  
Protein Subunit ◽  
The Central Nervous System ◽  
10 Nm Filaments ◽  
Peptide Maps

Several classes of 10-nm filaments have been reported in mammalian cells and they can be distinguished by the size of their protein subunit. We have studied the distribution of these filaments in nerves from calves and other mammals. From the display on polyacrylamide electrophoretic gels of proteins in extracts from fibroblast and central, cranial and peripheral nerves, we cut the appropriate stained bands and prepared iodinated peptide maps. The similarities between the respective maps provide strong evidence for the presence of vimentin in cranial and peripheral nerves. The glial fibrillary acidic protein was found in axon preparations from the central nervous system, but was not identified in distal segments of some cranial nerves, nor in peripheral nerve.

Expression of the integrin alpha 6 beta 4 in peripheral nerves: localization in Schwann and perineural cells and different variants of the beta 4 subunit

1994 ◽  
Vol 107 (2) ◽  
pp. 543-552 ◽  
Author(s):  
C.M. Niessen ◽  
O. Cremona ◽  
H. Daams ◽  
S. Ferraresi ◽  
A. Sonnenberg ◽  
...  
Keyword(s):  
Central Nervous System ◽  
Polymerase Chain Reaction ◽  
Nervous System ◽  
Peripheral Nerves ◽  
Northern Blot Analysis ◽  
The Other ◽  
Chain Reaction ◽  
The Central Nervous System ◽  
Polymerase Chain ◽  
Integrin Alpha 6

Integrin alpha 6 beta 4 is expressed in human peripheral nerves, but not in the central nervous system. This integrin heterodimer has previously been found in perineural fibroblast-like cells and in Schwann cells (SCs), which both assemble a basement membrane but do not form hemidesmosomes. We show here that in SCs, which had formed a myelin sheath, alpha 6 beta 4 was enriched in the proximity of the nucleus, at Ranvier paranodal areas and at Schmitt-Lanterman clefts; alpha 6 beta 4 was also found at the grooved interface between small axons and non-myelinating SCs. Immunoprecipitation of human peripheral nerves, in combination with Western blotting showed that beta 4 is associated with the alpha 6A subunit. Northern blot analysis of human peripheral nerves showed a single beta 4 transcript of 6 kb. Using the reverse transcriptase polymerase chain reaction, we detected two mRNA species, one for the most common (−70, -53) form of beta 4 and the other encoding the (+53) variant of beta 4. Cultured SCs were devoid of alpha 6 beta 4 but expressed alpha 6 beta 1, indicating that SCs lose beta 4 expression when contact with neurons is lost. Thus, resting SCs in contact with axons express alpha 6A in combination with beta 4, irrespective of myelin formation. We suggest that alpha 6 beta 4 expressed in SCs plays a role in peripheral neurogenesis.

To the treatment of nervous diseases by parenteral administration of milk

1926 ◽  
Vol 22 (5-6) ◽  
pp. 748-749
Author(s):  
G. Pervushin
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Peripheral Nerves ◽  
Combined Treatment ◽  
Full Recovery ◽  
Parenteral Administration ◽  
The Central Nervous System

Prof. VV Korelin (Psycho-Neur. Jur., 1926, issue I), having applied this treatment at 23 patients, observed full recovery in 8 cases, syphilis of the central nervous system, at combined treatment with mercury, - 4 sl., Inflammation of peripheral nerves - 3 sl. And epidemic meningitis - 1 sl.); further, in 3 cases this treatment gave improvement, and in others remained without result.

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