Agenesis of dorsal pancreas causing extra hepatic portal vein obstruction in a patient of symptomatic cholelithiasis: a case report

Agenesis of dorsal pancreas (ADP) is an extremely rare entity. We report a case of 50 year old lady with complete agenesis of the dorsal pancreas presenting with extra-hepatic portal vein obstruction (EHPVO) with symptomatic gall stone disease. Contrast enhanced computed tomography (CECT) revealed a normal pancreatic head, but pancreatic body and tail were not visualized, pancreatic head was compressing upon the portal vein with marked luminal narrowing and cavernoma formation. Magnetic resonance imaging (MRI) and magnetic resonance cholangio pancreatography (MRCP) findings confirmed the CT findings of ADP.