TERATOCARCINOMA IN OVOTESTIS

Ovotestis refers to the presence of a gonad with histological existence of both ovaian follicles and Testicular tubular elements; this condition is labelled as True hermaphroditism. The gonads may be ovotestis bilateral or they may be ovary or testis on one side and an ovotestis on the other.

Ovotesticular Disorder of Sexual Development and Non-Palpable Testis

Disorders of sexual development (DSD) refers to a group of diseases that links the mismatch between an individual’s genetic and gonadal development and its phenotype. Ovotesticular DSD (true hermaphroditism) is one such disease, in which both male and female gonads are present. A 15-year-old boy with a history of surgery for non-palpable testis was examined due to bilateral gynecomastia and known gonosomal mosaic of Klinefelter syndrome. The external genital was matured as male and, in the left half of the scrotum, there was a testicle of normal size. Despite uncertain resistance on the right side, however, the right testis was not palpable. Revision of the right groin revealed a surprising finding in the form of an ovary with a dilated fallopian tube, both of which were completely removed. Surgical revision of the left testis with biopsy was performed. The surgery was completed with a bilateral mastectomy. The postoperative course was uncomplicated, and the boy is content and fully integrated into his peer group. True hermaphroditism is a rare type of DSD. In the case described, DSD was not exhibited until puberty, after an examination for gynecomastia. The case also confirms the necessity of clarification and long-term follow-up of patients with unclear findings during surgery for non-palpable testis. Diagnostic laparoscopy is clearly indicated in these situations.

Transverse Hermaphroditism in a male

At a meeting of the Pathological Society of London, February 6, 1894, Dr. Edgar Willett demonstrated the genitals of a 44-year-old Muschina who died of cerebral hemorrhage, which is an extremely rare case of true hermaphroditism in the sense of combining both sexes in one individual.

A case of labioscrotal ovotestis in Madagascar with review of the literature

Among the disorder sexual development which regroups several pathological entities, true hermaphroditism or Ovotestis disorder remains a rare variety. We report a case of true hermaphroditism, diagnosed at the age of 15 years. Despite the presence of sexual ambiguity at birth, the female gender has been declared. The presence of a female genital tract and secondary sexual characteristics has led the choice of scrotal excision. The surgical procedure, the histological study bestow the positive diagnosis and allowed to revise the sexual ambiguity.

Abordaje del recién nacido con alteraciones del desarrollo sexual

Introducción: Las alteraciones del desarrollo sexual en el recién nacido no es una condición infrecuente durante la práctica médica pero sí resulta ser un reto tanto en el abordaje diagnostico como en el terapéutico. Se definen como el conjunto de condiciones en donde el desarrollo del sexo cromosómico, gonadal o anatómico es atípico. Objetivos: Realizar un abordaje integral de las alteraciones del desarrollo sexual y reconocer la importancia de los equipos transdisciplinarios para el manejo de esta patología. Metodología: Se realizó una búsqueda de la literatura con las palabras clave Disorders of sex development, Ovotesticular disorders of sex development, True Hermaphroditism, Gonadal dysgenesis, Adrenal hyperplasia, congenital en cinco bases de datos bibliográficas, se limitó la búsqueda para artículos en idioma español o inglés de los últimos 10 años. Resultados: Se obtuvieron110 artículos de los cuales 36 fueron incluidos en esta revisión, los artículos revisados eran artículos originales, presentación de casos, consensos y artículos de revisión. Conclusiones: La sensibilización al personal de salud sobre esta condición es fundamental para realizar un diagnóstico y tratamiento oportuno, con el objetivo de evitar complicaciones en la salud del recién nacido. La asignación del sexo es uno de los problemas más relevantes para el manejo de esta patología; esta decisión deberá ser tomada por el equipo transdisciplinario de especialistas con experiencia en el tema en donde se realice una evaluación detallada e individual de cada caso