scholarly journals Successful maintenance hemodialysis with permanent vascular catheter in a patient with recessive dystrophic epidermolysis bullosa hereditaria

2009 ◽  
Vol 42 (11) ◽  
pp. 899-904
Author(s):  
Hiyori Suzuki ◽  
Hiroaki Io ◽  
Katsuhiko Asanuma ◽  
Yukihiko Takeda ◽  
Isao Ohsawa ◽  
...  
Keyword(s):  
Epidermolysis Bullosa ◽  
Maintenance Hemodialysis ◽  
Dystrophic Epidermolysis Bullosa ◽  
Recessive Dystrophic Epidermolysis Bullosa ◽  
Epidermolysis Bullosa Hereditaria

scholarly journals Maintenance Hemodialysis Using Native Arteriovenous Fistula in a Patient with Severe Generalized Recessive Dystrophic Epidermolysis Bullosa

2016 ◽  
Vol 6 (2) ◽  
pp. 96-100 ◽  
Author(s):  
Takayasu Ito ◽  
Eiji Ishikawa ◽  
Hiroshi Matsuo ◽  
Mika Fujimoto ◽  
Tomohiro Murata ◽  
...  
Keyword(s):  
Arteriovenous Fistula ◽  
Epidermolysis Bullosa ◽  
Cutaneous Squamous Cell Carcinoma ◽  
Maintenance Hemodialysis ◽  
End Stage Kidney Disease ◽  
Term Survival ◽  
Dystrophic Epidermolysis Bullosa ◽  
Recessive Dystrophic Epidermolysis Bullosa ◽  
End Stage

Renal failure and infectious disease are strongly associated with morbidity and mortality in patients with severe generalized recessive dystrophic epidermolysis bullosa (RDEB-sev gen). However, it is reportedly difficult to introduce hemodialysis with an arteriovenous fistula (AVF). We encountered a 32-year-old man with RDEB-sev gen in whom hemodialysis with a native AVF was introduced that favorably affected his long-term survival. This patient eventually died because of cachexia related to the recurrence of cutaneous squamous cell carcinoma 51 months after hemodialysis introduction. We believe that in this patient, the frequency of vascular access troubles related to infection or reduction of blood flow was probably low as a result of hemodialysis with his native AVF. Thus, it seems likely that patients with RDEB-sev gen with end stage kidney disease who are on hemodialysis can be successfully managed with a native AVF.

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