Large Vestibular Aqueduct Syndrome: A Case Study

2005 ◽  
Vol 16 (10) ◽  
pp. 822-828 ◽  
Author(s):  
Jackie L. Clark ◽  
Ross J. Roeser
Keyword(s):  
Hearing Loss ◽  
Hearing Aids ◽  
Hearing Aid ◽  
Behavioral Testing ◽  
Hearing Aid Fitting ◽  
Hearing Sensitivity ◽  
Vestibular Aqueduct ◽  
Brainstem Response ◽  
Large Vestibular Aqueduct Syndrome ◽  
Large Vestibular Aqueduct

A 23-month-old female was referred for hearing aid fitting after failing newborn hearing screening and being diagnosed with significant hearing loss through subsequent diagnostic testing. Auditory brainstem response (ABR) and behavioral testing revealed a moderate-to-severe bilateral mixed hearing loss. Prior to the hearing aid evaluation, tympanostomy tubes had been placed bilaterally with little or no apparent change in hearing sensitivity. Initial testing during the hearing aid fitting confirmed earlier findings, but abnormal middle ear results were observed, requiring referral for additional otologic management. Following medical clearance, binaural digital programmable hearing aids were fit using Desired Sensation Level parameters. Behavioral testing and probe microphone measures showed significant improvements in audibility. Decrease in hearing sensitivity was observed six months following hearing aid fitting. Radiological studies, ordered due to the mixed component and decreased hearing sensitivity, revealed large vestibular aqueduct syndrome (LVAS). Based on the diagnosis of LVAS, a cochlear implant was placed on the right ear; almost immediate speech-language gains were observed.

Hearing Loss, Control, and Demographic Factors Influencing Hearing Aid Use Among Older Adults

1998 ◽  
Vol 41 (3) ◽  
pp. 527-537 ◽  
Author(s):  
Dean C. Garstecki ◽  
Susan F. Erler
Keyword(s):  
Older Adults ◽  
Hearing Loss ◽  
Hearing Aids ◽  
Psychological Control ◽  
Hearing Aid ◽  
Demographic Factors ◽  
Ego Strength ◽  
Hearing Sensitivity ◽  
Hearing Aid Use ◽  
Hearing Handicap

Preference for non-use of hearing aids among older adults who are candidates for amplification remains to be explained. Clinical studies have examined the contribution of consumer attitudes, behaviors, and life circumstances to this phenomenon. The present study extends the interests of earlier investigators in that it examines psychological control tendencies in combination with hearing loss and demographic variables among older adults who elected to accept (adherents) or ignore (nonadherents) advice from hearing professionals to acquire and use hearing aids. One hundred thirty-one individuals participated by completing measures of hearing, hearing handicap, psychological control, depression, and ego strength. Participants were asked to provide demographic information and personal opinions regarding hearing aid use. Adherence group and gender differences were noted on measures of hearing sensitivity, psychological control, and demographic factors. Female adherents demonstrated greater hearing loss and poorer word recognition ability but less hearing handicap, higher internal locus of control, higher ego strength, and fewer depressive tendencies than female nonadherents. They reported demographic advantages. Female adherents assumed responsibility for effective communication. Although male adherents and nonadherents did not differ significantly demographically, male adherents were more accepting of their hearing loss, took responsibility for communication problems, and found hearing aids less stigmatizing. Implications for clinical practice and future clinical investigations are identified and discussed. Results are expected to be of interest to clinicians, clinical investigators, and health care policymakers.

Hyperbaric oxygen therapy for sudden sensorineural hearing loss in large vestibular aqueduct syndrome

2013 ◽  
Vol 128 (S1) ◽  
pp. S50-S54 ◽  
Author(s):  
H Shilton ◽  
M Hodgson ◽  
G Burgess
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Hyperbaric Oxygen ◽  
Hyperbaric Oxygen Therapy ◽  
Oxygen Therapy ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Vestibular Aqueduct ◽  
Large Vestibular Aqueduct Syndrome ◽  
Large Vestibular Aqueduct

AbstractIntroduction:We report the first use in Australia of hyperbaric oxygen therapy for sudden hearing loss following head trauma in a child with large vestibular aqueduct syndrome.Case report:A 12-year-old boy with large vestibular aqueduct syndrome presented with significant hearing loss following head trauma. He was treated with steroids and hyperbaric oxygen therapy, with good improvement of hearing thresholds on audiography. This case represents the first reported use of hyperbaric oxygen therapy for this indication in Australia, following a few previous reports of patients in Japan. We review the literature on management of acute sensorineural hearing loss in large vestibular aqueduct syndrome. The reported case demonstrates a potentially beneficial therapy for a rare condition that usually results in an inevitable decline in hearing.Conclusion:Hyperbaric oxygen therapy can be tolerated well by children, and may represent a potential treatment for sudden sensorineural hearing loss in patients with large vestibular aqueduct syndrome.

Quality In, Quality Out: Supporting Good Outcomes for Children Who Wear Hearing Aids

2013 ◽  
Vol 23 (2) ◽  
pp. 31-42
Author(s):  
Marlene P. Bagatto
Keyword(s):  
Hearing Loss ◽  
Hearing Aids ◽  
Hearing Aid ◽  
Hearing Aid Fitting ◽  
Essential Components ◽  
Stage Process ◽  
Outcomes For Children ◽  
Key Aspects ◽  
Speech And Language Development ◽  
Fitting Hearing Aids

Fitting hearing aids to infants with hearing loss can be completed in a systematic and evidence-based manner. This is because there are clinical protocols and technologies available so that pediatric audiologists can fit hearing aids to their patients with hearing loss during the early months of life. Early hearing aid fitting supports speech and language development, however, the way in which the hearing aid is fitted can significantly impact the infant’s progress. A four-stage process for infant hearing aid fitting is offered as a framework with which to execute the essential components of the procedure. Key aspects of the pediatric hearing aid fitting process are described with a focus on elements that may impact an infant’s progress with hearing aids if not implemented.

Parent Hearing Aid Experiences in the United States

2013 ◽  
Vol 24 (01) ◽  
pp. 005-016 ◽  
Author(s):  
Karen Muñoz ◽  
Kristina Blaiser ◽  
Karianne Barwick
Keyword(s):  
United States ◽  
Hearing Loss ◽  
Hearing Aids ◽  
Hearing Aid ◽  
Wait Time ◽  
The United States ◽  
Population Based ◽  
Cross Sectional ◽  
Hearing Aid Fitting ◽  
Parent Experiences

Background: Children born with permanent hearing loss have the opportunity to receive services earlier as a result of newborn hearing screening (NHS). We conducted a survey to address three aspects within the early hearing detection and intervention (EHDI) process: (1) timeliness of service delivery, (2) hearing device access, and (3) hearing aid management. Parent experiences provide valuable information in identifying existing challenges for these components of the EHDI system. Purpose: The aim was to investigate parent experiences as they access and manage hearing aids for their child. Research Design: A cross-sectional, population-based survey was used. Study Sample: Three hundred fifty-two completed surveys from parents of children born between 1977 and 2010 were returned from 45 states in the United States. Data Collection and Analysis: Responses were obtained online and through the mail, and were analyzed using descriptive statistics. Results: Over time, the age of hearing loss identification has decreased to a median of 2 mo, age of first hearing aid fitting has decreased to a median of 5 mo, and the delay between hearing loss identification and hearing aid fitting has remained the same with a median of 2 mo. For children born between 2007 and 2010, the top three challenges parents reported in obtaining hearing aids were (1) paying for hearing aids, (2) accepting the need for hearing aids, and (3) wait time for an appointment. Almost one-half (48%) of the parents reported that they did not receive adequate support from their audiologist in how to check the function of their child's hearing aids. Conclusions: Significant progress has been made over the past two decades in reducing the age of hearing loss identification and hearing aid fitting for children who do not pass the NHS. However, many children continue to experience delays between hearing loss diagnosis and hearing aid fitting that exceed Joint Committee on Infant Hearing recommendations. The experiences parents reported provide valuable information about areas that need further investigation to improve the process for children with hearing loss.

scholarly journals Large Vestibular Aqueduct Syndrome Associated with Sensorineural Hearing Loss. A Report of Two Cases.

1993 ◽  
Vol 86 (5) ◽  
pp. 641-645
Author(s):  
Masamitsu Senarita ◽  
Norihide Nishikawa ◽  
Akira Hara ◽  
Jun Kusakari ◽  
Yoshihisa Kurodaki
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Vestibular Aqueduct ◽  
Large Vestibular Aqueduct Syndrome ◽  
Large Vestibular Aqueduct
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