Large Vestibular Aqueduct Syndrome Presenting with Mixed Hearing Loss and an Intact Mobile Ossicular Chain

2000 ◽  
Vol 10 (5) ◽  
pp. 204-206 ◽  
Author(s):  
Bülent Mamıkoğlu ◽  
Brandon Bentz ◽  
Richard J. Wiet
Keyword(s):  
Hearing Loss ◽  
Ossicular Chain ◽  
Vestibular Aqueduct ◽  
Mixed Hearing Loss ◽  
Large Vestibular Aqueduct Syndrome ◽  
Large Vestibular Aqueduct

Hyperbaric oxygen therapy for sudden sensorineural hearing loss in large vestibular aqueduct syndrome

2013 ◽  
Vol 128 (S1) ◽  
pp. S50-S54 ◽  
Author(s):  
H Shilton ◽  
M Hodgson ◽  
G Burgess
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Hyperbaric Oxygen ◽  
Hyperbaric Oxygen Therapy ◽  
Oxygen Therapy ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Vestibular Aqueduct ◽  
Large Vestibular Aqueduct Syndrome ◽  
Large Vestibular Aqueduct

AbstractIntroduction:We report the first use in Australia of hyperbaric oxygen therapy for sudden hearing loss following head trauma in a child with large vestibular aqueduct syndrome.Case report:A 12-year-old boy with large vestibular aqueduct syndrome presented with significant hearing loss following head trauma. He was treated with steroids and hyperbaric oxygen therapy, with good improvement of hearing thresholds on audiography. This case represents the first reported use of hyperbaric oxygen therapy for this indication in Australia, following a few previous reports of patients in Japan. We review the literature on management of acute sensorineural hearing loss in large vestibular aqueduct syndrome. The reported case demonstrates a potentially beneficial therapy for a rare condition that usually results in an inevitable decline in hearing.Conclusion:Hyperbaric oxygen therapy can be tolerated well by children, and may represent a potential treatment for sudden sensorineural hearing loss in patients with large vestibular aqueduct syndrome.

Large Vestibular Aqueduct Syndrome: A Case Study

2005 ◽  
Vol 16 (10) ◽  
pp. 822-828 ◽  
Author(s):  
Jackie L. Clark ◽  
Ross J. Roeser
Keyword(s):  
Hearing Loss ◽  
Hearing Aids ◽  
Hearing Aid ◽  
Behavioral Testing ◽  
Hearing Aid Fitting ◽  
Hearing Sensitivity ◽  
Vestibular Aqueduct ◽  
Brainstem Response ◽  
Large Vestibular Aqueduct Syndrome ◽  
Large Vestibular Aqueduct

A 23-month-old female was referred for hearing aid fitting after failing newborn hearing screening and being diagnosed with significant hearing loss through subsequent diagnostic testing. Auditory brainstem response (ABR) and behavioral testing revealed a moderate-to-severe bilateral mixed hearing loss. Prior to the hearing aid evaluation, tympanostomy tubes had been placed bilaterally with little or no apparent change in hearing sensitivity. Initial testing during the hearing aid fitting confirmed earlier findings, but abnormal middle ear results were observed, requiring referral for additional otologic management. Following medical clearance, binaural digital programmable hearing aids were fit using Desired Sensation Level parameters. Behavioral testing and probe microphone measures showed significant improvements in audibility. Decrease in hearing sensitivity was observed six months following hearing aid fitting. Radiological studies, ordered due to the mixed component and decreased hearing sensitivity, revealed large vestibular aqueduct syndrome (LVAS). Based on the diagnosis of LVAS, a cochlear implant was placed on the right ear; almost immediate speech-language gains were observed.

scholarly journals Large Vestibular Aqueduct Syndrome Associated with Sensorineural Hearing Loss. A Report of Two Cases.

1993 ◽  
Vol 86 (5) ◽  
pp. 641-645
Author(s):  
Masamitsu Senarita ◽  
Norihide Nishikawa ◽  
Akira Hara ◽  
Jun Kusakari ◽  
Yoshihisa Kurodaki
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Vestibular Aqueduct ◽  
Large Vestibular Aqueduct Syndrome ◽  
Large Vestibular Aqueduct

scholarly journals Sudden Sensorineural Hearing Loss in the Only Hearing Ear: Large Vestibular Aqueduct Syndrome

2016 ◽  
Vol 2016 ◽  
pp. 1-3
Author(s):  
Kemal Koray Bal ◽  
Onur Ismi ◽  
Helen Bucioglu ◽  
Yusuf Vayısoğlu ◽  
Kemal Gorur
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Social Life ◽  
English Literature ◽  
Delayed Diagnosis ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Vestibular Aqueduct ◽  
Large Vestibular Aqueduct Syndrome ◽  
Large Vestibular Aqueduct

Sudden hearing loss in the only hearing ear cases are rarely published in the English literature; most of the cases are idiopathic. It is an otologic emergency needing urgent treatment. Delayed diagnosis can interfere with patient’s social life with interrupting the verbal communication. In this case report we presented a 33-year-old female patient having sudden sensorineural hearing loss in the only hearing ear diagnosed as bilateral large vestibular aqueduct syndrome.

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