scholarly journals Mobius Syndrome

2020 ◽  
Author(s):  
Keyword(s):  
Möbius Syndrome

Outcomes of Microneurovascular Facial Reanimation Using Masseteric Innervation in Patients With Long-Standing Facial Palsy Resulting From Cured Brainstem Lesions

Neurosurgery ◽  
2010 ◽  
Vol 67 (3) ◽  
pp. 663-674 ◽  
Author(s):  
Kartik G. Krishnan ◽  
Gabriele Schackert ◽  
Volker Seifert
Keyword(s):  
Loss Of Function ◽  
Muscle Flaps ◽  
Self Evaluation ◽  
Möbius Syndrome ◽  
Evaluation Scores ◽  
Facial Nerves ◽  
Facial Reanimation ◽  
Masseteric Nerve ◽  
Natural Emotion ◽  
The Individual

Abstract BACKGROUND The functions of the human face are not only of esthetic significance but also extend into metaphoric nuances of psychology. The loss of function of one or both facial nerves has a remarkable impact on patients' lives. OBJECTIVE To retrospectively analyze the functional outcomes of microneurovascular facial reanimation using masseteric innervation. METHODS Seventeen patients with irreparable facial paralysis resulting from benign lesions involving the facial nuclei (n = 14) or Möbius syndrome (n = 3) were treated with free muscle flaps for oral commissural reanimation using ipsilateral masseteric innervation and using temporalis muscle transfer for eyelid reanimation. Results were analyzed by the absolute commissural excursion and commissural excursion index and by a patient self-evaluation score. Presence of synkinesis was documented. Follow-up ranged from 8 to 48 months (mean, 26.4 months). RESULTS Normalization of the commissural excursion index was observed in 8 of 17 patients (47%), an improvement was seen in 7 of 17 (41%), and failure was observed in 2 of 17 (12%). The individual dynamics of absolute commissural excursion and commissural excursion index changes are presented. A natural smiling response was observed in 10 of 17 patients (59%) but not in the remaining 7 (41%). This response reflected the patient's ability to relay the natural emotion of smiling through the masseteric nerve. Patients' self-evaluation scores were a level higher than objective indices. CONCLUSIONS Innervation of free muscle flaps with the masseteric nerve for oral commissure reanimation might play an important role in patients with lesions of the facial nuclei (as in Möbius syndrome). Synkinesis persists for long periods after surgery. However, most of the patients learned to express their emotions by overcoming this phenomenon. Despite hypercorrection or inadequate correction, patients evaluated themselves favorably.

scholarly journals Combined Mobius Syndrome and Tarsal Kink Syndrome- A Unique Presentation.

2017 ◽  
Vol 15 (3) ◽  
Author(s):  
Dr Anuradha Raj ◽  
Prof. R. C. Nagpal ◽  
Prof. Renu Dhasmana ◽  
Dr. Amit Maitreya
Keyword(s):  
Facial Paralysis ◽  
Congenital Malformation ◽  
Neurological Disorder ◽  
Cranial Nerves ◽  
Tarsal Plate ◽  
Möbius Syndrome ◽  
Upper Lid

We describe the management of the congenital entropion with tarsal kink in a case of mobius syndrome. Mobius syndrome is extremely rare  congenital neurological disorder results from the underdevelopment of the sixth and seventh cranial nerves which causes  facial paralysis and inability to move the eyes from side to side.  A congenital malformation of the tarsus known as tarsal kink was the associated eyelid anomaly which caused upperlid entropion. A  two year old  girl presented with  both  eyelids entropion of left eye which was corrected by upper lid tarsotomy, marginal rotation and levator  suturing with tarsal plate and lower lid retractors were strengthened by their advancement to the tarsal plate.

scholarly journals PROBLEMATIC OF MÖBIUS SYNDROME- CASE STUDY

2016 ◽  
Vol 3 ◽  
pp. 160
Author(s):  
Jana Tabachová
Keyword(s):  
Intensive Care ◽  
Communication Skills ◽  
Motor Development ◽  
Cognitive Skills ◽  
Speech Development ◽  
Therapeutic Approaches ◽  
The Czech Republic ◽  
Möbius Syndrome ◽  
Specific Description

The article focuses on the problematic of Möbius syndrome, a specific description of a child with this syndrome. This is a very rare syndrome. At the time of diagnosing this girl‘s syndrome, doctors in the Czech Republic had almost no experience and had no seen any other child with Möbius syndrome. So she got the intensive care specific for this syndrome just before her third birthday. The aim of our study was to obtain data in motor development, cognitive skills and abilities and especially to obtain information about speech development. In this article, we try to capture the main therapeutic approaches that led to the development of communication skills and promote the development of all language levels. 

scholarly journals Expanded Mobius Syndrome

2001 ◽  
Vol 15 (6) ◽  
pp. 47
Author(s):  
J Gordon Millichap
Keyword(s):  
Möbius Syndrome

Long-Term Outcomes of Smile Reconstruction in Möbius Syndrome

2018 ◽  
Vol 141 (6) ◽  
pp. 868e-882e ◽  
Author(s):  
Irina Domantovsky ◽  
Jocelyne Copeland ◽  
Rachel M. Clancy ◽  
Ronald M. Zuker ◽  
Gregory H. Borschel
Keyword(s):  
Long Term Outcomes ◽  
Möbius Syndrome

THE MÖBIUS SYNDROME

1953 ◽  
Vol 35 (2) ◽  
pp. 437-444 ◽  
Author(s):  
Robert N. Richards
Keyword(s):  
Möbius Syndrome
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