scholarly journals Metastatic renal hemangiopericytoma: A rare case report

2009 ◽  
Vol 17 (1-2) ◽  
pp. 32-35 ◽  
Author(s):  
Ahmet Bilici ◽  
Oven Ustaalioglu ◽  
Mesut Seker ◽  
Tarik Salman ◽  
Akyildiz Igdem ◽  
...  

The hemangiopericytoma (HPC) of the kidney is extremely rare perivascular neoplasm. There are no specific radiological or clinical findings that can aid in preoperative diagnosis. In the world literature, only 41 cases of renal HPC have been previously documented. We report on a 56-year old woman with renal HPC of the right kidney who had lung metastasis at the time of diagnosis. The right radical nephrectomy was performed and the combination chemotherapy was given, postoperatively. After 3 cycles of chemotherapy, disease was stable, but progression was seen at the end of 6 courses of chemotherapy. The patient died due to progression of disease ten months later after the diagnosis. We suggested that for patients present with renal mass, renal HPC as well as the other renal tumors should be considered in the differential diagnosis.

Author(s):  
Xisheng Wang ◽  
Zejian Zhang ◽  
Xia Zhu ◽  
Wende Cheng ◽  
Jiqing Fang ◽  
...  

INTRODUCTION: It is a challenge to make accurate pre-surgical diagnosis for renal tumors. This study is to report the findings, management, and outcome of one rare case of ossification in a cystic renal mass. We present and discuss the pathological characteristics, radiologic features, and treatment alternatives of the patient. PATIENTS AND METHODS: A 38 years old female patient had intermittent epigastric pain and microscopic hematuria for two months. Computerized tomography (CT) scan and Magnetic Resonance imaging (MRI) showed a mass with rough edge and dense calcification in the upper pole of the right kidney and normal left kidney. Pre-operative diagnosis is cystic nephroma or cystic renal mass (Bosniak III type, Bosniak renal cyst classification). GFR was within normal limits for age and no other significant laboratory aberrations were noted. Patient underwent a right retroperitoneal laparoscopic partial nephrectomy (margin status was negative). A mini literature review was performed to highlight the principals of diagnosis and treatment of cystic renal mass with heterotopic ossification. RESULTS: The entire renal mass was successfully removed from upper pole of the right kidney by laparoscopic nephron sparing surgery. The size of renal mass is 38×35×30 mm3 with thick and hard capsular wall. The cystic cavity contains yellow lipid-like substances without stone. Histological examination revealed renal cyst in which the cyst wall reveals fibrosis and no obvious lining epithelium. The additional unique feature includes the presence of dense calcification and ossification in the renal mass. Localization tissue of yellow bone marrow was detected. No complications occurred in 9 months after surgery during follow-up. CONCLUSIONS: Cystic renal mass with heterotopic ossification is a rare case of non-malignant renal tumor. Whether surgery is needed depends to whether patients have symptoms. For symptom renal tumors, laparoscopic nephron sparing surgical procedure is recommended. Furthermore, complete surgical resection of the lesion is needed when the mass is suspected to be malignant. An accurate histologic diagnosis is key in its diagnosis.


2010 ◽  
Vol 1 (2) ◽  
pp. 125-127
Author(s):  
Vikram Kulkarni ◽  
Vidisha Athanikar ◽  
Trupti Katti

Abstract Objective To report a rare case of angioleiomyoma with regard to size, type (variant) and location. Case report 45 years old male presented with painless swelling on the right side of the face since 2 years. On examination, the swelling was 4 cm × 3 cm in size, firm in consistency with well-defined margins. It was not adhering to overlying skin and underlying structures. The swelling was excised and sent for histopathological diagnosis. It was reported as solid variant of angioleiomyoma based on microscopic features. Conclusion According to the world literature, large angioleiomyoma on face is rare or not reported yet (usually less than 2 cm) and location (usually externar ear, tip of nose, lip). This case is presented for its uniqueness in size —large (4 cm x 3 cm); painlessness; variant; and location.


2017 ◽  
Vol 78 (02) ◽  
pp. e77-e80 ◽  
Author(s):  
Xin He ◽  
Tingting Yuan ◽  
Yuzhu Yan ◽  
Jinlu Yu ◽  
Dan Tong

AbstractPrimary osteosarcomas of the skull and skull base are rare and comprise < 2% of all skull tumors. In head and neck osteosarcomas, the chondroblastic subtype occurs most frequently, which has an exceedingly poor outcome, but its image characteristic remains unknown. Herein, we report a case in the right occipital bone of the skull base and the unique characteristics of image. Pathologic examination of the surgical specimens led to the diagnosis of chondroblastic osteosarcomas. We believe those image characteristics can improve the understanding of skull chondroblastic osteosarcoma and the preoperative diagnosis.


2011 ◽  
Vol 01 (01/03) ◽  
pp. 63-65
Author(s):  
Padma Shetty K. ◽  
Harish S. Permi ◽  
Michelle Mathias ◽  
Kishan Prasad ◽  
Teerthanath S. ◽  
...  

AbstractLiposarcoma in the inguinal region though rare are clinically significant lesions. Preoperative diagnosis is difficult since the clinical findings are very similar to that of inguinal hernia. We report a rare case of Liposarcoma of the spermatic cord in 85 year old male, clinically diagnosed as left sided indirect inguinal hernia. Surgical excision specimen showed multiple globular lipomatous masses which were yellowish and grey tan with areas of myxoid degeneration and necrosis seen. Microscopic examination showed adipocytes arranged in lobules with numerous blood vessels, lipoblasts and myxoid stroma confirming the diagnosis of myxoid liposarcoma. He is on regular follow up since two years without any recurrence or metastasis. Our case report highlights the importance of sampling and examination of fatty masses in the inguinal region to rule out the possibility of liposarcoma as they are mistaken for lipoma at surgery.


2020 ◽  
Vol 2020 (1) ◽  
Author(s):  
Edmund Wooi Keat Tan ◽  
Jason Bae Barco ◽  
Mutee Ur Rehman ◽  
Choon Chieh Tan

Abstract Osteomas are slow growing bone tumours and are often asymptomatic. Rarely, they can be present in the temporal bone—only few cases had been reported, with an incidence of 0.1–1%. We describe a case of an osteoma of the temporal bone (retromastoid) found in a 40 year old female, who presented with a slow growing swelling behind the right ear for 9 years. Diagnosis was made on non-contrast computed topography (CT) of the skull. Treatment is indicated in symptomatic cases or cosmetic reasons. Screening colonoscopy and genetic testing for familial adenomatous polyposis (FAP) and Gardner’s syndrome are advised.


2020 ◽  
Vol 2020 (8) ◽  
Author(s):  
Amjad Soltany ◽  
Ghazal Asaad ◽  
Rami Daher ◽  
Mouhannad Dayoub ◽  
Ali Khalil ◽  
...  

Abstract Ameloblastic fibrosarcoma (AFS) is a rare, aggressive malignant odontogenic tumor. AFS is seen most frequently in second and third decades of life. We are reporting a case of a low grade AFS in a 21-year-old male complaining of a painless swelling in the right side of the maxilla. The patient was treated with surgical excision followed by radiotherapy, which is considered the most effective approach for most of soft tissue sarcomas. AFS has a high-reported recurrence rate (up to 37%); therefore, long-term surveillance for recurrence is crucial.


2015 ◽  
Vol 04 (02) ◽  
pp. 102-104
Author(s):  
Sudipa Biswas ◽  
Suranjali Sharma ◽  
Sanjib Kumar Ghosh ◽  
Soumya Chakraborty

AbstractIn this rare case, found during routine dissection of head and neck in North Bengal Medical College on the right side of the neck, common carotid artery bifurcated at a higher level than usual and 1.25 cm below the bifurcation, gave a common origin of lingual and superior thyroid artery from its medial side (thyorolingual trunk). No such anomaly was noted on the left side. This type of combination of variations has important clinical implications.


2012 ◽  
Vol 127 (1) ◽  
pp. 67-69 ◽  
Author(s):  
T Al Balushi ◽  
J Z Naik ◽  
M Al Khabori

AbstractObjective:We present an extremely rare case of congenital cholesteatoma in identical twins.Method:Case report of congenital cholesteatoma in identical twins, and a literature review, are presented.Results:Both cases presented to the ENT out-patient clinic, but with different clinical pictures. Both were managed surgically.Conclusion:Congenital cholesteatoma presents as a whitish mass in the middle ear, with an intact tympanic membrane. It is a rare entity comprising between 3.7 and 24 per cent of total cholesteatoma cases. The key to its diagnosis is the absence of previous ear infection, ear surgery and local trauma. To our best knowledge, this paper represents the first report in the world literature of congenital cholesteatoma in identical twins.


2008 ◽  
Vol 123 (6) ◽  
pp. 673-675 ◽  
Author(s):  
M P A Clark ◽  
P M Pretorius ◽  
D Beaumont ◽  
C A Milford

AbstractObjective:We report an extremely rare case of congenital cholesteatoma affecting the occipital bone.Methods:We present a case report, plus a review of the world literature on similar lesions.Results:This case report describes the presentation and treatment of a congenital cholesteatoma arising in an apparently unique location within the occipital bone, with no effect on middle-ear structure or function. The different imaging characteristics of this lesion are described and illustrated. The discussion centres on the differentiation of this lesion from intradiploic epidermoid cysts, more commonly described in the neurosurgical literature. The possible methods of pathogenesis are discussed, along with treatment suggestions.Conclusion:Congenital cholesteatomas and intradiploic epidermoid cysts are indistinguishable both histologically and radiologically, and would appear to be the same disease.


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