scholarly journals Non-invasive assessment of paediatric cystic fibrosis liver disease and the role of microRNAs in disease mechanism

2019 ◽  
Author(s):  
Diego Calvopina Heredia
Keyword(s):  
Cystic Fibrosis ◽  
Liver Disease ◽  
Disease Mechanism ◽  
Non Invasive

Semi-Quantitative Ultrasonographic Evaluation of NAFLD

2020 ◽  
Vol 26 (32) ◽  
pp. 3915-3927 ◽  
Author(s):  
Stefano Ballestri ◽  
Claudio Tana ◽  
Maria Di Girolamo ◽  
Maria Cristina Fontana ◽  
Mariano Capitelli ◽  
...  
Keyword(s):  
Liver Disease ◽  
Fatty Liver ◽  
Imaging Techniques ◽  
Metabolic Complications ◽  
Nonalcoholic Fatty Liver ◽  
Non Invasive ◽  
Increased Risk ◽  
Risk Of Progression ◽  
Progressive Liver Disease

: Nonalcoholic fatty liver disease (NAFLD) embraces histopathological entities ranging from the relatively benign simple steatosis to the progressive form nonalcoholic steatohepatitis (NASH), which is associated with fibrosis and an increased risk of progression to cirrhosis and hepatocellular carcinoma. NAFLD is the most common liver disease and is associated with extrahepatic comorbidities including a major cardiovascular disease burden. : The non-invasive diagnosis of NAFLD and the identification of subjects at risk of progressive liver disease and cardio-metabolic complications are key in implementing personalized treatment schedules and follow-up strategies. : In this review, we highlight the potential role of ultrasound semiquantitative scores for detecting and assessing steatosis severity, progression of NAFLD, and cardio-metabolic risk. : Ultrasonographic scores of fatty liver severity act as sensors of cardio-metabolic health and may assist in selecting patients to submit to second-line non-invasive imaging techniques and/or liver biopsy.

scholarly journals Non-invasive tools for detection of liver disease in children and adolescents with cystic fibrosis

2021 ◽  
Vol 0 (0) ◽  
pp. 0-0
Author(s):  
Antonella Tosco ◽  
Angela Sepe ◽  
Alice Castaldo ◽  
Andrea Catzola ◽  
Chiara Cimbalo ◽  
...  
Keyword(s):  
Cystic Fibrosis ◽  
Liver Disease ◽  
Children And Adolescents ◽  
Non Invasive

The role of IDA scintigraphy in the follow-up of liver disease in patients with cystic fibrosis

2002 ◽  
Vol 23 (7) ◽  
pp. 673-681 ◽  
Author(s):  
J. A. FOSTER ◽  
W. H. RAMSDEN ◽  
S. P. CONWAY ◽  
J. M. TAYLOR ◽  
C. ETHERINGTON
Keyword(s):  
Cystic Fibrosis ◽  
Liver Disease

Cystic fibrosis-associated liver disease

2018 ◽  
Author(s):  
Eirini Kyrana ◽  
Anil Dhawan
Keyword(s):  
Cystic Fibrosis ◽  
Liver Disease ◽  
Magnetic Resonance ◽  
Liver Biopsy ◽  
Clinical Features ◽  
Transient Elastography

The chapter on cystic fibrosis-associated liver disease discusses the pathophysiology and clinical features of this condition. In addition it covers diagnosis, including liver biopsy, transient elastography, the role of endoscopy and magnetic resonance retrograde cholangiopancreatography, and then discusses management including the role of transplantation.

scholarly journals Night Blindness in Cystic Fibrosis: The Key Role of Vitamin A in the Digestive System

Nutrients ◽  
2019 ◽  
Vol 11 (8) ◽  
pp. 1876 ◽  
Author(s):  
Lorenzo Norsa ◽  
Laura Zazzeron ◽  
Marialaura Cuomo ◽  
Laura Claut ◽  
Anna Marta Clotilde Bulfamante ◽  
...  
Keyword(s):  
Cystic Fibrosis ◽  
Liver Disease ◽  
Vitamin A ◽  
Low Income ◽  
Vitamin A Deficiency ◽  
Intestinal Failure ◽  
Intestinal Resection ◽  
Low Income Countries ◽  
Cholestatic Liver Disease

Vitamin A is a fundamental micronutrient that regulates various cellular patterns. Vitamin A deficiency (VAT) is a worldwide problem and the primary cause of nocturnal blindness especially in low income countries. Cystic fibrosis (CF) is a known risk factor of VAD because of liposoluble vitamin malabsorption due to pancreatic insufficiency. We describe a case of a 9-year-old girl who experienced recurrent episodes of nocturnal blindness due to profound VAD. This little girl is paradigmatic for the explanation of the key role of the gut–liver axis in vitamin A metabolism. She presents with meconium ileus at birth, requiring intestinal resection that led to a transient intestinal failure with parenteral nutrition need. In addition, she suffered from cholestatic liver disease due to CF and intestinal failure-associated liver disease. The interaction of pancreatic function, intestinal absorption and liver storage is fundamental for the correct metabolism of vitamin A.

scholarly journals Non-Invasive Evaluation of Cystic Fibrosis Related Liver Disease in Adults with ARFI, Transient Elastography and Different Fibrosis Scores

PLoS ONE ◽  
2012 ◽  
Vol 7 (7) ◽  
pp. e42139 ◽  
Author(s):  
Thomas Karlas ◽  
Marie Neuschulz ◽  
Annett Oltmanns ◽  
Andrea Güttler ◽  
David Petroff ◽  
...  
Keyword(s):  
Cystic Fibrosis ◽  
Liver Disease ◽  
Transient Elastography ◽  
Non Invasive ◽  
Related Liver Disease ◽  
Invasive Evaluation
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