Pulmonic Valve Stenosis, Atrial Septal Defect and Left-to-Right Interatrial Shunting with Intact Ventricular Septum

CHEST Journal ◽  
1980 ◽  
Vol 78 (5) ◽  
pp. 759-762 ◽  
Author(s):  
Ernest N. Arnett ◽  
Seena C. Aisner ◽  
Kenneth B. Lewis ◽  
Paul Tecklenberg ◽  
Robert K. Brawley ◽  
...  
Keyword(s):  
Atrial Septal Defect ◽  
Septal Defect ◽  
Ventricular Septum ◽  
Intact Ventricular Septum ◽  
Pulmonic Valve

scholarly journals A case of atrial septal defect associated with anomalous sinoatrial node artery in pulmonary atresia with intact ventricular septum

2021 ◽  
Author(s):  
Angela Di Candia ◽  
BIAGIO CASTALDI ◽  
Domenico Sirico ◽  
Giovanni Di Salvo
Keyword(s):  
Atrial Septal Defect ◽  
Septal Defect ◽  
Sinoatrial Node ◽  
Pulmonary Atresia ◽  
Ventricular Septum ◽  
Intact Ventricular Septum ◽  
Selective Angiography ◽  
Abnormal Coronary Artery ◽  
Asd Closure ◽  
Sinoatrial Node Artery

An 11-year-old boy affected by pulmonary atresia with intact ventricular septum (AP-IVS) was listed for percutaneous pulmonary valvuloplasty and closure of multi-fenestrated atrial septal defect (ASD). Intraprocedural transesophageal echocardiography arose the suspect of abnormal coronary artery pattern while selective angiography documented a single sinoatrial node artery (SANa) with an unusual retro-aortic course. As consequence, we proceeded to effectively close the defects with a not self-centering device placed in the most central side hole. This case supports the hypothesis that sometimes arrhythmic complication during ASD closure procedures might be due to unrecognized injury of the SANa.

scholarly journals Size of atrial septal defect after balloon atrial septostomy does not correlate with immediate improvement in oxygenation

2021 ◽  
Vol 4 (1) ◽  
pp. e000224
Author(s):  
Kartik Sehgal ◽  
Kunal Sehgal ◽  
Suraj Varma
Keyword(s):  
Atrial Septal Defect ◽  
Septal Defect ◽  
Defect Size ◽  
Ventricular Septum ◽  
Intact Ventricular Septum ◽  
Transposition Of Great Arteries ◽  
Physiological Variables ◽  
Balloon Atrial Septostomy ◽  
Atrial Septostomy ◽  
Before And After

ObjectiveTransposition of great arteries is a common cyanotic heart defect. Balloon atrial septostomy aims to improve circulatory mixing and oxygenation. Previous studies have combined infants with intact ventricular septum and those with ventricular septal defect. Additionally, the septostomy was performed much later after birth. The objectives were to ascertain any correlation between the atrial septal defect size and oxygenation, before and after septostomy, as well the change in parameters pre-post procedure.MethodsWe performed an audit of the last 10 years of clinical and echocardiographic data (2010–2020) for infants with transposition of great arteries with intact ventricular septum. A pediatric cardiologist, masked to clinical data, reviewed the images.ResultsOur study of 25 infants with transposition of great arteries with intact ventricular septum noted that the procedure was performed at a median [interquartile range (IQR)] of 3 (2, 4) hours after birth. Prostaglandin was administered to the majority of infants [20/25 (80%)]. While significant increases in partial pressure of oxygen (24±5 vs 40±6 mmHg, p<0.001) and preductal oxygen saturations (67%±18% vs 81%±11%, p=0.003) were noted, and while the atrial septal defect increased in size from 1.8±0.6 vs 4.8±0.7 mm (p<0.001), no correlation was noted between atrial septal defect size and oxygen saturations.ConclusionsIn our study of infants with transposition of great arteries and intact ventricular septum managed with balloon atrial septostomy, no correlation was noted between the atrial septal defect size and oxygen saturations. Pulmonary vascular resistance and pulmonary blood flow may be important physiological variables determining oxygenation.

Congenital absence of the pulmonic valve and tricuspid valve atresia with intact ventricular septum

1987 ◽  
Vol 59 (5) ◽  
pp. 482-484 ◽  
Author(s):  
Peter Forrest ◽  
Roberta M. Bini ◽  
James L. Wilkinson ◽  
Robert Arnold ◽  
John G.C. Wright ◽  
...  
Keyword(s):  
Tricuspid Valve ◽  
Congenital Absence ◽  
Ventricular Septum ◽  
Intact Ventricular Septum ◽  
Pulmonic Valve

Anatomic correction of complete transposition with ventricular septal defect in neonates: experience with 42 consecutive cases

1991 ◽  
Vol 1 (1) ◽  
pp. 101-103 ◽  
Author(s):  
Claude Planché ◽  
Alain Serraf ◽  
François Lacour-Gayet ◽  
Jacqueline Bruniaux ◽  
François Bouchart
Keyword(s):  
Left Ventricle ◽  
Ventricular Septal Defect ◽  
Septal Defect ◽  
Arterial Switch Operation ◽  
Systemic Circulation ◽  
Ventricular Septum ◽  
Intact Ventricular Septum ◽  
Complete Transposition ◽  
The Poor ◽  
Switch Operation

Perhaps paradoxically, it was in the form of complete transposition with a ventricular septal defect rather than an intact ventricular septum that the arterial switch operation was first successfully applied. This was, in part, because of the poor results of the physiologic repair in the presence of a ventricular septal defect, but more because the left ventricle, in the presence of the septal deficiency, is immediately suitable for supporting postoperatively the increased workload imposed on the systemic circulation. Spurred by this success, the procedure was then extended to neonates born with complete transposition and an intact ventricular septum and is currently employed with good results in this group.

Is the function of all cardiac valves after the arterial switch operation influenced by an associated ventricular septal defect?

2011 ◽  
Vol 21 (4) ◽  
pp. 383-391
Author(s):  
J. Gabriel ◽  
H.-H. Scheld ◽  
T.D.T. Tjan ◽  
N. Osada ◽  
Thomas Krasemann
Keyword(s):  
Ventricular Septal Defect ◽  
Septal Defect ◽  
Arterial Switch Operation ◽  
Pulmonary Stenosis ◽  
Ventricular Septum ◽  
Intact Ventricular Septum ◽  
Cardiac Valves ◽  
Arterial Switch ◽  
Switch Operation

AbstractA ventricular septal defect in transposition of the great arteries is frequently closely related to the cardiac valves. The valvar function after arterial switch operation of patients with transposition of the great arteries and ventricular septal defect or intact ventricular septum was compared. We analysed the function of all cardiac valves in patients who underwent the arterial switch operations pre- and post-operatively, 1 year after the procedure and on follow-up. The study included 92 patients – 64 with transposition of the great arteries/intact ventricular septum and 28 with transposition of the great arteries/ventricular septal defect. The median age at surgery was 5.5 days in transposition of the great arteries/intact ventricular septum (0–73 days) and 7.0 days in transposition of the great arteries/ventricular septal defect (4–41 days). Follow-up was 51.7 months in transposition of the great arteries/intact ventricular septum (3.3–177.3 months) and 55 months in transposition of the great arteries/ventricular septal defect (14.6–164.7 months). Neo-aortic, neo-pulmonary, and mitral valvar function did not differ. Tricuspid regurgitation was more frequent 1 year post-operatively in transposition of the great arteries/ventricular septal defect (n = 4) than in transposition of the great arteries/intact ventricular septum. The prevalence of neo-aortic regurgitation and pulmonary stenosis increased over time, especially in patients with transposition of the great arteries/intact ventricular septum. The presence of a ventricular septal defect in patients undergoing arterial switch operation for transposition of the great arteries only has a minor bearing for the development of valvar dysfunction on the longer follow-up.

Aortic atresia with normal left ventricle and intact ventricular septum—a major form of subaortic stenosis complicating an atrioventricular septal defect with intact septal structures

1995 ◽  
Vol 5 (3) ◽  
pp. 282-285 ◽  
Author(s):  
Lucile Houyel ◽  
Véronique Zupana ◽  
Françoise Roset
Keyword(s):  
Left Ventricle ◽  
Septal Defect ◽  
Atrioventricular Septal Defect ◽  
Ventricular Septum ◽  
Subaortic Stenosis ◽  
Atrioventricular Valve ◽  
Intact Ventricular Septum ◽  
Extreme Form ◽  
Aortic Atresia ◽  
Major Form

SummaryWe report an unusual form of aortic atresia with a normal sized left ventricle, intact ventricular septum and isolated cleft of the left atrioventricular valve, with abnormal attachments creating both subaortic atresia and massive regurgitation across the left atrioventricular valve. This combination, never described before as far as we are aware, can be considered as an extreme form of subaortic stenosis complicating a very particular type of atrioventricular septal defect.

An echocardiographic study of diagnostic accuracy, prediction of surgical approach, and outcome for fetuses diagnosed with discordant ventriculo-arterial connections

2007 ◽  
Vol 17 (5) ◽  
pp. 528-534 ◽  
Author(s):  
Cécile J. Pascal ◽  
Ian Huggon ◽  
Gurleen K. Sharland ◽  
John M. Simpson
Keyword(s):  
Ventricular Septal Defect ◽  
Positive Predictive Value ◽  
Diagnostic Accuracy ◽  
Surgical Approach ◽  
Predictive Value ◽  
Aortic Coarctation ◽  
Septal Defect ◽  
Pulmonary Stenosis ◽  
Ventricular Septum ◽  
Intact Ventricular Septum

AbstractOur aims were to examine the diagnostic accuracy of prenatal diagnosis of concordant atrioventricular and discordant ventriculo-arterial connections, the accuracy of predictions made concerning the postnatal surgical approach, and a description of the different subtypes related to outcome. All fetuses were evaluated at a tertiary centre for fetal cardiology between January, 1994, and December, 2003. In this period, we identified congenitally malformed hearts in 1,835 fetuses, of whom 56 (3%) met the criterions of inclusion. Of the total, 30 (54%) had an intact ventricular septum, 9 (16%) had an associated ventricular septal defect, 7 (13%) had a ventricular septal defect and pulmonary stenosis, 1 (2%) had pulmonary stenosis and an intact ventricular septum, 8 (14%) had a ventricular septal defect and aortic coarctation, and 1 (2%) had coarctation of the aorta with an intact ventricular septum. All the discordant ventriculo-arterial connections were correctly identified. For associated ventricular septal defects, the diagnostic sensitivity was 96%, with specificity of 88%, positive predictive value of 85%, and negative predictive value of 97%. For aortic coarctation, the sensitivity was 100%, specificity 96%, positive predictive value 82%, and negative predictive value 100%. The prediction of the surgical approach was accurate in 41 of 48 cases (85%). For those fetuses with pulmonary stenosis and ventricular septal defect, the ratio of the diameters of the pulmonary trunk was shown to be helpful in predicting the possibility of an arterial switch as opposed to the Rastelli type of repair. Of the 49 liveborn infants, 46 were alive at 30 days (94%, with 95% confidence intervals from 83 to 99%), and 43 at one year (88%, 95% confidence intervals from 75 to 95%). Deaths were mainly related to the anatomy of the coronary arteries, and associated cardiac lesions.

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