scholarly journals A case of atrial septal defect associated with anomalous sinoatrial node artery in pulmonary atresia with intact ventricular septum

2021 ◽  
Author(s):  
Angela Di Candia ◽  
Biagio Castaldi ◽  
Domenico Sirico ◽  
Giovanni Di Salvo
Keyword(s):  
Atrial Septal Defect ◽  
Septal Defect ◽  
Sinoatrial Node ◽  
Pulmonary Atresia ◽  
Ventricular Septum ◽  
Intact Ventricular Septum ◽  
Sinoatrial Node Artery

scholarly journals A case of atrial septal defect associated with anomalous sinoatrial node artery in pulmonary atresia with intact ventricular septum

2021 ◽  
Author(s):  
Angela Di Candia ◽  
BIAGIO CASTALDI ◽  
Domenico Sirico ◽  
Giovanni Di Salvo
Keyword(s):  
Atrial Septal Defect ◽  
Septal Defect ◽  
Sinoatrial Node ◽  
Pulmonary Atresia ◽  
Ventricular Septum ◽  
Intact Ventricular Septum ◽  
Selective Angiography ◽  
Abnormal Coronary Artery ◽  
Asd Closure ◽  
Sinoatrial Node Artery

An 11-year-old boy affected by pulmonary atresia with intact ventricular septum (AP-IVS) was listed for percutaneous pulmonary valvuloplasty and closure of multi-fenestrated atrial septal defect (ASD). Intraprocedural transesophageal echocardiography arose the suspect of abnormal coronary artery pattern while selective angiography documented a single sinoatrial node artery (SANa) with an unusual retro-aortic course. As consequence, we proceeded to effectively close the defects with a not self-centering device placed in the most central side hole. This case supports the hypothesis that sometimes arrhythmic complication during ASD closure procedures might be due to unrecognized injury of the SANa.

Pulmonic Valve Stenosis, Atrial Septal Defect and Left-to-Right Interatrial Shunting with Intact Ventricular Septum

CHEST Journal ◽  
1980 ◽  
Vol 78 (5) ◽  
pp. 759-762 ◽  
Author(s):  
Ernest N. Arnett ◽  
Seena C. Aisner ◽  
Kenneth B. Lewis ◽  
Paul Tecklenberg ◽  
Robert K. Brawley ◽  
...  
Keyword(s):  
Atrial Septal Defect ◽  
Septal Defect ◽  
Ventricular Septum ◽  
Intact Ventricular Septum ◽  
Pulmonic Valve

scholarly journals Size of atrial septal defect after balloon atrial septostomy does not correlate with immediate improvement in oxygenation

2021 ◽  
Vol 4 (1) ◽  
pp. e000224
Author(s):  
Kartik Sehgal ◽  
Kunal Sehgal ◽  
Suraj Varma
Keyword(s):  
Atrial Septal Defect ◽  
Septal Defect ◽  
Defect Size ◽  
Ventricular Septum ◽  
Intact Ventricular Septum ◽  
Transposition Of Great Arteries ◽  
Physiological Variables ◽  
Balloon Atrial Septostomy ◽  
Atrial Septostomy ◽  
Before And After

ObjectiveTransposition of great arteries is a common cyanotic heart defect. Balloon atrial septostomy aims to improve circulatory mixing and oxygenation. Previous studies have combined infants with intact ventricular septum and those with ventricular septal defect. Additionally, the septostomy was performed much later after birth. The objectives were to ascertain any correlation between the atrial septal defect size and oxygenation, before and after septostomy, as well the change in parameters pre-post procedure.MethodsWe performed an audit of the last 10 years of clinical and echocardiographic data (2010–2020) for infants with transposition of great arteries with intact ventricular septum. A pediatric cardiologist, masked to clinical data, reviewed the images.ResultsOur study of 25 infants with transposition of great arteries with intact ventricular septum noted that the procedure was performed at a median [interquartile range (IQR)] of 3 (2, 4) hours after birth. Prostaglandin was administered to the majority of infants [20/25 (80%)]. While significant increases in partial pressure of oxygen (24±5 vs 40±6 mmHg, p<0.001) and preductal oxygen saturations (67%±18% vs 81%±11%, p=0.003) were noted, and while the atrial septal defect increased in size from 1.8±0.6 vs 4.8±0.7 mm (p<0.001), no correlation was noted between atrial septal defect size and oxygen saturations.ConclusionsIn our study of infants with transposition of great arteries and intact ventricular septum managed with balloon atrial septostomy, no correlation was noted between the atrial septal defect size and oxygen saturations. Pulmonary vascular resistance and pulmonary blood flow may be important physiological variables determining oxygenation.

Survival With Respect to Morphology in Pulmonary Atresia and Intact Ventricular Septum in Sweden

2021 ◽  
Vol 12 (1) ◽  
pp. 27-34
Author(s):  
Stina Manhem ◽  
Katarina Hanséus ◽  
Håkan Berggren ◽  
Britt-Marie Ekman-Joelsson
Keyword(s):  
Pulmonary Atresia ◽  
Early Time ◽  
Ventricular Septum ◽  
Intact Ventricular Septum ◽  
Early Group ◽  
Time Period ◽  
Medical Reports ◽  
One Year ◽  
Survival Risk ◽  
Late Group

Background: Patients born with pulmonary atresia and intact ventricular septum represent a challenge to pediatric cardiologists. Our objective was to study changes in survival with respect to morphology in all children born with pulmonary atresia and intact ventricular septum in Sweden during 36 years. Methods: A retrospective, descriptive study based on medical reports and echocardiographic examinations consisting of those born between 1980 and 1998 (early group) and those born between 1999 and 2016 (late group). Results: The cohort consists of 171 patients (early group, n = 86 and late group, n = 85) yielding an incidence of 4.35 and 4.46 per 100,000 live births, respectively. One-year survival in the early group was 76% compared to 92% in the late group ( P = .0004). For patients with membranous atresia, one-year survival increased from 78% to 98%, and for muscular pulmonary atresia, from 68% to 85%. In patients with muscular pulmonary atresia and ventriculocoronary arterial communications, there was no significant increase in survival. Risk factors for death were being born in the early time period hazard ratio (HR), 6; 95% CI (2.33-14.28) P = .0002, low birth weight HR, 1.26; 95% CI (1.14-1.4) P < .0001 and having muscular pulmonary atresia HR, 3.74; 95% CI (1.71-8.19) P = .0010. Conclusion: The incidence of pulmonary atresia and intact ventricular septum remained unchanged during the study period. Survival has improved, especially for patients with membranous pulmonary atresia, while being born with muscular pulmonary atresia is still a risk factor for death. To further improve survival, greater focus on patients with muscular pulmonary atresia and ventriculocoronary arterial communications is required.

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