scholarly journals SURGICAL CORRECTION OF DOUBLE OUTLET LEFT VENTRICLE ASSOCIATED WITH HYPOPLASTIC RIGHT VENTRICLE : Direct Anastomosis of Right Atraial Appendage and Pulmonary Artery

1979 ◽  
Vol 43 (8) ◽  
pp. 768-774 ◽  
Author(s):  
TOSHIYUKI KATOGI ◽  
SHIGEYUKI TAKEUCHI ◽  
KEIICHIRO KATSUMOTO ◽  
TOYOKI FUKUDA ◽  
MIKITO MORISHITA ◽  
...  
Keyword(s):  
Left Ventricle ◽  
Pulmonary Artery ◽  
Right Ventricle ◽  
Surgical Correction ◽  
Hypoplastic Right Ventricle ◽  
Direct Anastomosis

scholarly journals 97 An unusual combination of rare congenital heart defects in a 70 years old lady complaining worsening dyspnea

2021 ◽  
Vol 23 (Supplement_G) ◽  
Author(s):  
Matteo Bellettini ◽  
Antonio Montefusco ◽  
Andrea Angelini ◽  
Fulvio Orzan ◽  
Fabrizio D’Ascenzo ◽  
...  
Keyword(s):  
Coronary Artery ◽  
Left Ventricle ◽  
Pulmonary Artery ◽  
Right Ventricle ◽  
Tricuspid Regurgitation ◽  
Congenital Heart ◽  
Pulmonary Valve ◽  
Pulmonary Regurgitation ◽  
Subaortic Membrane ◽  
The Right

Abstract Methods and results A 70-year-old woman presented to our outpatient clinic complaining of worsening dyspnoea in the last 3 months. She had a medical history of hypertension, diabetes, dyslipidemia, and paroxysmal atrial fibrillation. We performed a comprehensive evaluation starting with a transthoracic echocardiogram that showed a dilatation of right ventricle with normal function, severe pulmonary regurgitation, and moderate tricuspid regurgitation with estimated pulmonary artery systolic pressure of 55 mmHg; the left ventricle had normal dimension and function, with mild aortic and mitral regurgitation, and a subaortic membrane which caused a mild obstruction (maximum gradient 17 mmHg). The cardiac magnetic resonance (CMR) confirmed the enlargement of the right ventricle and of the pulmonary artery trunk (51 mm) and the severity of pulmonary regurgitation (regurgitant fraction of 41%). CMR also clearly showed the VSD just below the subaortic membrane and the left to right shunt with a jet that appeared to proceed straight from the left ventricle through the pulmonary valve (Figure 1A). The estimated Qp/Qs was 1.6 and no intramyocardial late enhancement was present. Pulmonary pressures and pulmonary vascular resistance were normal at the right heart catheterization and the Qp/Qs ratio calculated invasively was 1.45. Considering patient high-risk profile for coronary artery disease, a coronary angiography was also performed showing an abnormal origin of the right coronary artery (RCA) from the mid-portion of the left anterior descending coronary artery (LAD) with two significant stenosis: one involving the bifurcation of RCA and the other the mid-portion of the LAD (Figure 1B). The coronary computed tomography angiography (CCTA) showed a benign course of the RCA anterior to the pulmonary artery towards the auriculoventricular groove (Figure 1C, D). Taking into account all these findings, multidisciplinary heart team decided to perform a cardiac surgery intervention of pulmonary valve and trunk replacement, closure of ventricular septal defect and two coronary bypass grafts on LAD and RCA. Conclusions This case represents a combination of some rare congenital heart abnormalities where multimodality cardiovascular imaging techniques were essential to establish a proper diagnosis and to plan an adequate surgical repair. We hypothesize that the peculiar orientation of the VSD jet may have caused the pulmonary trunk dilatation considering that neither the shunt, nor the pulmonary pressure appear to have been of sufficient magnitude to cause it. Pulmonary ectasia and the damage inflicted by the jet to the cusps of the valve have led to the severe valvular insufficiency. While aortic and tricuspid regurgitation are known to be associated with VSD, to the best of our knowledge this is the first report of pulmonary regurgitation secondary to VSD.

Changes of management in a patient with double outlet left ventricle

1999 ◽  
Vol 9 (6) ◽  
pp. 602-605 ◽  
Author(s):  
Omar Galal ◽  
Liv Hatle ◽  
Zohair Al Halees
Keyword(s):  
Left Ventricle ◽  
Right Ventricle ◽  
Color Doppler ◽  
Pulmonary Trunk ◽  
Biventricular Repair ◽  
Color Doppler Echocardiography ◽  
Patient Reported ◽  
Hypoplastic Right Ventricle ◽  
Aortic Homograft ◽  
The Right

AbstractDouble outlet left ventricle is an extremely rare anomaly. Until recently, the diagnosis was usually established by angiography or at postmortem. There are only a few reports describing the echocar-diographic findings in this lesion, and as far as we know, no report showing the anatomy as well as the velocity and pattern of flow by color Doppler echocardiography. The patient reported here underwent surgery at the age of four years, when an aortic homograft was placed between the right ventricle and the pulmonary trunk. This biventricular repair had to be changed into a Fontan-type procedure, 15 years later since the hypoplastic right ventricle did not grow adequately.

Does hypoplasia of one pulmonary artery preclude a definitive repair in pulmonary atresia, intact ventricular septum, and hypoplastic right ventricle?

1995 ◽  
Vol 10 (3) ◽  
pp. 158-162 ◽  
Author(s):  
Kiyoshi Suzuki ◽  
Katsuhiko Tatsuno ◽  
Shigekazu Mimori ◽  
Yasuo Murakami ◽  
Shouzaburoh Doi ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Right Ventricle ◽  
Pulmonary Atresia ◽  
Ventricular Septum ◽  
Intact Ventricular Septum ◽  
Hypoplastic Right Ventricle ◽  
Definitive Repair
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