EP12.08: Prenatal diagnosis of an extremely rare case of double outlet left ventricle (DOLV) with hypoplastic right ventricle

2019 ◽  
Vol 54 (S1) ◽  
pp. 304-304
Author(s):  
S. Medandrao
Keyword(s):  
Prenatal Diagnosis ◽  
Left Ventricle ◽  
Right Ventricle ◽  
Rare Case ◽  
Hypoplastic Right Ventricle

Prenatal diagnosis of tricuspid atresia with hypoplastic right ventricle associated with truncus arteriosus communis type II

2009 ◽  
Vol 281 (2) ◽  
pp. 255-259 ◽  
Author(s):  
Gabriele Tonni ◽  
Marco Panteghini ◽  
Alessandro Ventura ◽  
Maria Paola Bonasoni ◽  
Giulia Rognoni ◽  
...  
Keyword(s):  
Prenatal Diagnosis ◽  
Right Ventricle ◽  
Tricuspid Atresia ◽  
Truncus Arteriosus ◽  
Type Ii ◽  
Hypoplastic Right Ventricle

Changes of management in a patient with double outlet left ventricle

1999 ◽  
Vol 9 (6) ◽  
pp. 602-605 ◽  
Author(s):  
Omar Galal ◽  
Liv Hatle ◽  
Zohair Al Halees
Keyword(s):  
Left Ventricle ◽  
Right Ventricle ◽  
Color Doppler ◽  
Pulmonary Trunk ◽  
Biventricular Repair ◽  
Color Doppler Echocardiography ◽  
Patient Reported ◽  
Hypoplastic Right Ventricle ◽  
Aortic Homograft ◽  
The Right

AbstractDouble outlet left ventricle is an extremely rare anomaly. Until recently, the diagnosis was usually established by angiography or at postmortem. There are only a few reports describing the echocar-diographic findings in this lesion, and as far as we know, no report showing the anatomy as well as the velocity and pattern of flow by color Doppler echocardiography. The patient reported here underwent surgery at the age of four years, when an aortic homograft was placed between the right ventricle and the pulmonary trunk. This biventricular repair had to be changed into a Fontan-type procedure, 15 years later since the hypoplastic right ventricle did not grow adequately.

scholarly journals SURGICAL CORRECTION OF DOUBLE OUTLET LEFT VENTRICLE ASSOCIATED WITH HYPOPLASTIC RIGHT VENTRICLE : Direct Anastomosis of Right Atraial Appendage and Pulmonary Artery

1979 ◽  
Vol 43 (8) ◽  
pp. 768-774 ◽  
Author(s):  
TOSHIYUKI KATOGI ◽  
SHIGEYUKI TAKEUCHI ◽  
KEIICHIRO KATSUMOTO ◽  
TOYOKI FUKUDA ◽  
MIKITO MORISHITA ◽  
...  
Keyword(s):  
Left Ventricle ◽  
Pulmonary Artery ◽  
Right Ventricle ◽  
Surgical Correction ◽  
Hypoplastic Right Ventricle ◽  
Direct Anastomosis

scholarly journals Incidence and Outcomes of Patients with Functionally Univentricular Heart Born in Latvia, 2007 to 2015

Medicina ◽  
2018 ◽  
Vol 54 (3) ◽  
pp. 44
Author(s):  
Katrina Rutka ◽  
Inguna Lubaua ◽  
Elina Ligere ◽  
Amanda Smildzere ◽  
Valts Ozolins ◽  
...  
Keyword(s):  
Cardiac Surgery ◽  
Left Ventricle ◽  
Right Ventricle ◽  
High Mortality ◽  
Heart Defects ◽  
University Hospital ◽  
Univentricular Heart ◽  
Hypoplastic Left Ventricle ◽  
Hypoplastic Right Ventricle ◽  
Surgery Center

Background and Objectives: A functionally univentricular heart is the term used to describe congenital heart defects where it is impossible to restore two pumping chambers. These lesions are associated with high mortality, morbidity, and medical resource utilization. The aim of this study was to review incidence and outcomes of patients with a functionally univentricular heart at the only pediatric cardiac surgery center in Latvia. Methods: We performed a retrospective review of medical records of (i) all children with a functionally univentricular heart treated at the Clinic of Pediatric Cardiology and Cardiac Surgery, and (ii) all prenatally diagnosed cases of univentricular heart at Children’s Clinical University Hospital in Latvia. We reviewed data regarding children born from January 1, 2007, to December 31, 2015. The children’s cardiac anatomy and interventions were categorized in accordance with the International Pediatric and Congenital Cardiac Code (v3.3). Results: During the study period, 49 patients with a functionally univentricular heart were admitted to Children’s Clinical University Hospital with a corrected incidence of 0.69 per 1000 live births per year. There were 26 patients that had a hypoplastic left ventricle, and 22 patients that had a hypoplastic right ventricle, while one patient had an indeterminate ventricle. Thirty (61.2%) patients had died by the end of data collection. Twenty-one of the 30 deaths occurred before or immediately after stage I surgical palliation. Cumulative neonatal and 5-year survival of patients with a hypoplastic right ventricle was 81.8% and 63.6%, respectively; for patients with hypoplastic left ventricle—46.2% and 17.3%, respectively. Discussion: This is the first mid-term outcome study of patients with a univentricular heart in Latvia. The high mortality reflects the challenges of a small-volume, developing congenital cardiac surgery center. Data from this study will be used as a baseline for quality improvement.

Isolated ventricular inversion with hypoplastic right ventricle and pulmonary stenosis in an adolescent with situs solitus: a rare combination

2021 ◽  
pp. 1-3
Author(s):  
Anand K. Mishra ◽  
Sanjeev H. Naganur ◽  
Ruchit Patel ◽  
Vidur Bansal ◽  
Pratyaksha Rana
Keyword(s):  
Right Ventricle ◽  
Rare Case ◽  
Pulmonary Stenosis ◽  
Cardiac Malformation ◽  
Rare Combination ◽  
Congenital Cardiac Malformation ◽  
Hypoplastic Right Ventricle ◽  
Situs Solitus ◽  
Atrioventricular Discordance ◽  
Isolated Ventricular Inversion

Abstract Isolated ventricular inversion with situs solitus is a severe and rare congenital cardiac malformation characterised by an atrioventricular discordance but with ventriculo-arterial concordance. Here, we present the rare case of an adolescent with isolated ventricular inversion and hypoplasia of the left-sided morphological right ventricle and pulmonary stenosis, a first of its kind to be reported in the literature.

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