scholarly journals Congenital Midureteric Stricture: Challenges in Diagnosis and Management

2015 ◽  
Vol 2015 ◽  
pp. 1-5 ◽  
Author(s):  
Raashid Hamid ◽  
Nisar A. Bhat ◽  
Kumar Abdul Rashid

Background. Congenital midureteric stricture (MUS) is a rare malformation. We report our experience with five cases seen over a period of 4 years from 2010 to 2014.Materials and Methods. The study was based on the retrospective analysis of five patients diagnosed as having MUS. Diagnosis was suspected after fetal ultrasonography (USG) in one patient and magnetic resonance urography (MRU) in four patients. Retrograde pyelography (RGP) was performed on three patients. The final diagnosis was confirmed during surgical exploration in all the patients.Results. MRU was found to be a good investigation method. It showed the site of obstruction in the ureter in all instances. Intravenous urography detected proximal ureteric dilatation present in two of the patients. RGP delineates the level of stricture and the course of ureter, as shown in our cases. All patients had significant obstruction on the affected side. Four patients underwent ureteroureterostomy, all of whom had satisfactory results. In one patient, ureteric reimplantation was carried out due to distal small ureteric caliber.Conclusion. This rare entity is often misdiagnosed initially as pelviureteric junction obstruction. MRU is an excellent option for the anatomical location and functional assessment of the involved system. At the time of surgical correction of a ureteral obstruction, RGP is a useful adjunct for delineating the stricture level and morphology.

2016 ◽  
Vol 19 (1) ◽  
pp. 028
Author(s):  
Shengjun Wu ◽  
Peng Teng ◽  
Yiming Ni ◽  
Renyuan Li

Coronary sinus aneurysm (CSA) is an extremely rare entity. Herein, we present an unusual case of an 18-year-old symptomatic female patient with a giant CSA. Secondary vena cava aneurysms were also manifested. The final diagnosis was confirmed by enhanced computed tomography (CT) and cardiac catheterization. As far as we know, it is the first case that such a giant CSA coexists with secondary vena cava aneurysms. Considering the complexity of postoperative reconstruction, we believe that heart transplantation may be the optimal way for treatment. The patient received anticoagulant due to the superior vena cava (SVC) thrombosis while waiting for a donor.


2021 ◽  
Author(s):  
Yuri Noda ◽  
Chisato Ohe ◽  
Mitsuaki Ishida ◽  
Kimiaki Okano ◽  
Kaori Sando ◽  
...  

Abstract Background: Odontogenic tumors arising from extra-alveolar sites are extremerly rare. Dentinogenic ghost cell tumor (DGCT) is an uncommon odontogenic neoplasm characterized by CTNNB1 mutation, ghost cell appearance, and dentinoid-like calcification. We present a case of an ectopic DGCT arising from a calcifying odontogenic cyst in the floor of the mouth. Case presentation: A 72-year-old man presented with a painless sublingual swelling. Imaging revealed a multi-lobulated, solid-cyst mass on the floor of the mouth. Cytology showed folded epithelial clusters composed of basaloid cells, keratinized material, and dentinoid matrix. Histology also revealed a multi-cystic, cribriform to solid nest. Immunohistochemically, CK19, CK5/6, bcl-2, and p63 were diffuse positive. CTNTTB1 mutation was detected, leading to the final diagnosis of an ectopic DGCT. There was no recurrence during a 6-month follow-up. Conclusion: This is the first report to comprehensively describe the clinicopathological features of an ectopic DGCT of odontogenic origin, developing similarly to that of a true odontogenic DGCT. Accurate diagnosis of this rare entity is necessary to avoid overtreatment.


2013 ◽  
Vol 2013 ◽  
pp. 1-3 ◽  
Author(s):  
Ioannis Anastasiou ◽  
Ioannis Katafigiotis ◽  
Christos Pournaras ◽  
Evangelos Fragkiadis ◽  
Ioannis Leotsakos ◽  
...  

Macroscopic hematuria regards the 4% to 20% of all urological visits. Renal artery aneurysms (RAAs) are detected in approximately 0.01%–1% of the general population, while intraparenchymal renal artery aneurysms (IPRAAs) are even more rarely detected in less than 10% of patients with RAAs. We present a case of a 58-year-old woman that came into the emergency room (ER) complaining of a gross hematuria during the last four days. Although in the ER room the first urine sample was clear after a cough episode, a severe gross hematuria began which led to a hemodynamically unstable patient. Finally, a radical nephrectomy was performed, and an IPRAA was the final diagnosis. A cough deteriorating hematuria could be attributed to a ruptured intraparenchymal renal artery aneurysm, which even though constitutes a rare entity, it is a life-threatening medical emergency.


2012 ◽  
Vol 2 (1) ◽  
pp. 47-49
Author(s):  
Kamlesh Dekate ◽  
L.S Poonja

Abstract According to the WHO (2005) classification of odontogenic tumors, Desmoplastic Ameloblastoma is recognized as a variant of ameloblastoma. This rare entity differs from the other forms of ameloblastoma in its anatomical location, morphology, and radiographic appearance. Due to its unusual clinic-pathological presentation, this tumor mimics various odontogenic as well as non odontogenic neoplasms. We are presenting a rare case of desmoplastic ameloblastoma in the maxilla in a 53 year old male with regards to its clinical and radiographical and histological viewpoints.


2017 ◽  
Vol 4 (11) ◽  
pp. 3756 ◽  
Author(s):  
Alberto Manuel Gonzalez Chavez ◽  
Alain Garcia Vazquez ◽  
Diego Abelardo Alvarez Hernandez ◽  
Mario Andres Gonzalez Chavez ◽  
Ricardo Ray Huacuja Blanco ◽  
...  

Transverse colon diverticulitis is a rare entity, described for the first time in 1944 by Thompson and Fox. Even more uncommon if presented with diverticular perforation of the colon. When ranking diverticula distribution by their anatomical location site, it has been set up that transverse colon is involved in an average of 10% of the cases, but diverticulitis or inflammation of these sacculations in this anatomical region only occurs in 0.5-2.5% of the cases. Female, 44 years old, who came to emergency room with acute abdominal pain as colic of 24 hours of evolution, Acute cholecystitis was considered as a first diagnostic possibility. Pain persistence and peritoneal irritation lead to an abdominal contrasted tomography (contrast IV). Oval formations protruding from the gut lumen in ascending and transverse colon were found, corresponding to diverticula. Patient was admitted in hospital and maintained in fasting period and with a double antibiotic scheme she was discharged on the 5th day of hospital stay. Transverse colon diverticulitis is a rare entity, there exist less than 50 cases reported in worldwide literature but it has been determined that patients with transverse colon diverticulitis are 15 and 20 years younger than patients with left colon diverticulitis. That is, average age of manifestation is about 45 years old. 85% of the cases have been described in women. Reports managed it successfully with antibiotics. The present report could be achieved favourably with a double antibiotic scheme, with no need of surgery.


2021 ◽  
Vol 20 (1) ◽  
pp. 177-180
Author(s):  
Md Jahangir Hossain Bhuiyan ◽  
Md Mohibul Aziz ◽  
Md Omar Faruk ◽  
Md Mahbub Hasan

Splenic cysts are rarely detected, and clinically diagnosed commonly as spleenomegaly . Thenature of the cyst could not be diagnosed pre-operatively because of its’ anatomical location andonly be confirmed by the histopathological assessments. These cysts are found as a sequel ofsplenic infarct followed by the abscess formation. This is a very rare condition of a minor boy ofonly 10 years’ old who presented with a hugely enlarged spleen. The common investigation(s)did not prove that it was in the haematological conditions. Ultrasonogram (USG) investigationshows spleenomegaly due to the cystic lesion. CT scan of the abdomen showed large andwell defined cystic mass which was 13.4cmX7.9cmX15.3cm in size, multi-loculated, septated,sharply demarcated as such well delineated cyst. After necessary preparation like vaccination,blood grouping, cross matching and other fitness, laparotomy and total spleenectomy was doneas the cyst occupied most of the Splenic tissue. The post operative recovery was uneventful andthe final diagnosis was confirmed by histopatholgical examinations as epidermoid cyst of thespleen. The patient was followed up for two consecutive months and not a single complicationwas noticed. Bangladesh Journal of Medical Science Vol.20(1) 2021 p.177-180


2014 ◽  
Vol 4 (1) ◽  
pp. 67-70 ◽  
Author(s):  
P Devani ◽  
Hira Lal ◽  
A Thakral

The purpose of this report is to present radiological features of a rare entity called Parry-Romberg syndrome (also known as Progressive hemifacial atrophy). The authors report one rare case of a 18 year old female patient with Parry-Romberg syndrome, accompanied by a brief review of literature and various radiological features of this entity. Final diagnosis of a Parry-Romberg syndrome was made on clinical and radiological grounds. Radiologists should be familiar with various radiographic, CT and MRI findings observed in this disorder. DOI: http://dx.doi.org/10.3126/njr.v4i1.11571 Nepalese Journal of Radiology, Vol.4(1) 2014: 67-70


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