scholarly journals Intraluminal EWSR1-CREB1 gene rearranged, low-grade myxoid sarcoma of the pulmonary artery resembling extraskeletal myxoid chondrosarcoma (EMC)

2018 ◽  
Vol 74 (3) ◽  
pp. 526-530 ◽  
Author(s):  
Isabelle Opitz ◽  
Olivia Lauk ◽  
Didier Schneiter ◽  
Silvia Ulrich ◽  
Francesco Maisano ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Low Grade ◽  
Extraskeletal Myxoid Chondrosarcoma ◽  
Myxoid Chondrosarcoma ◽  
Myxoid Sarcoma

Primary pulmonary myxoid sarcoma withEWSR1-CREB1fusion, resembling extraskeletal myxoid chondrosarcoma: Case report with a review of Literature

2012 ◽  
Vol 62 (12) ◽  
pp. 817-822 ◽  
Author(s):  
Susumu Matsukuma ◽  
Masanori Hisaoka ◽  
Kiyohaya Obara ◽  
Takako Kono ◽  
Hiroaki Takeo ◽  
...  
Keyword(s):  
Case Report ◽  
Extraskeletal Myxoid Chondrosarcoma ◽  
Review Of Literature ◽  
Myxoid Chondrosarcoma ◽  
Myxoid Sarcoma

scholarly journals Extraskeletal Myxoid Chondrosarcoma with Small Bowel Metastasis Causing Bowel Obstruction

2012 ◽  
Vol 2012 ◽  
pp. 1-4 ◽  
Author(s):  
Ernesto Bustinza-Linares ◽  
Francisco Socola ◽  
Vinicius Ernani ◽  
Shelly A. Miller ◽  
Jonathan C. Trent
Keyword(s):  
Small Bowel ◽  
Medical Community ◽  
Low Grade ◽  
Extraskeletal Myxoid Chondrosarcoma ◽  
Myxoid Chondrosarcoma ◽  
Small Bowel Metastasis ◽  
First Case ◽  
Mesenteric Fat ◽  
History Of ◽  
Hemoccult Test

A 28-year-old female with history of chest wall extraskeletal myxoid chondrosarcoma (EMC) presented to the emergency department complaining of two weeks of lightheadedness and fatigue. Laboratories showed hemoglobin of 7.6 g/dL and a positive hemoccult test. Upper and lower endoscopies were unremarkable, and the patient was discharged after blood transfusion. The next day she returned to the ED with left-sided weakness and perioral numbness. Brain CT scan revealed a 6 cm right frontal mass with midline shift and edema that required urgent craniotomy with resection of a hemorrhagic tumor. The patient continued dropping her hemoglobin, and CT scans showed a rounded 3 cm small bowel mass in the mid ileum. Repeat upper endoscopy revealed a 2 × 2 cm ulcerated mass in the fourth portion of the duodenum. The patient was taken to the operating room and was found to have two lesions; one in the distal duodenum and a second one in the mid ileum causing small bowel intussusception. Pathology was consistent with metastatic EMC grade 2/3, involving the bowel and mesenteric fat. Extraskeletal myxoid chondrosarcoma (EMC) is a rare soft-tissue sarcoma with unique features that distinguishes, it from other sarcomas. It has been often described as a low-grade sarcoma although there are certain characteristics like high mitotic activity and the presence of focal regions of Ki67 staining above 25% that correlate with aggressive behavior of the tumor. This is the first case of EMC metastatic to the small bowel to be reported to the medical community.

Primary pulmonary myxoid sarcoma, a potential mimic of metastatic extraskeletal myxoid chondrosarcoma

Pathology ◽  
2017 ◽  
Vol 49 (7) ◽  
pp. 792-794 ◽  
Author(s):  
Roh Yanagida ◽  
Bonnie L. Balzer ◽  
Robert J. Mckenna ◽  
Clark B. Fuller
Keyword(s):  
Extraskeletal Myxoid Chondrosarcoma ◽  
Myxoid Chondrosarcoma ◽  
Myxoid Sarcoma

scholarly journals Extraskeletal myxoid chondrosarcoma: a case report with adjuvant intraoperative treatment

2020 ◽  
Vol 2020 (12) ◽  
Author(s):  
Stefano Bacchetti ◽  
Enrico Pegolo ◽  
Gianluigi Adani ◽  
Antonio Macrì ◽  
Claudia Andreetta ◽  
...  
Keyword(s):  
Case Report ◽  
Systemic Chemotherapy ◽  
Early Stage ◽  
Standard Of Care ◽  
Popliteal Fossa ◽  
Low Grade ◽  
Extraskeletal Myxoid Chondrosarcoma ◽  
Rare Form ◽  
Myxoid Chondrosarcoma ◽  
Mesenchymal Neoplasm

Abstract Extraskeletal myxoid chondrosarcoma is a rare form of malignant mesenchymal neoplasm mainly localized into the limbs, particularly in the thigh and popliteal fossa. It has been classified as a low-grade sarcoma so far, but it shows a tendency to relapse and metastasize. In the early stage of disease, surgery represents the only chance of cure. In case of diffuse metastatic disease, systemic chemotherapy with anthracyclines is the standard of care. In this paper, we present a case of a patient affected by this rare disease and the analysis of radiological, surgical and histopathological aspects.

scholarly journals A LOW GRADE TUMOR, EXTRA SKELETAL MYXOID CHONDROSARCOMA, WITH METASTATIC POTENTIAL: A CASE REPORT

2019 ◽  
Vol 3 (7) ◽  
Author(s):  
Sushil Kumar Shukla ◽  
Viney Kumar ◽  
Smita Chandra
Keyword(s):  
Soft Tissue ◽  
Soft Tissues ◽  
Histopathological Examination ◽  
Specific Treatment ◽  
Metastatic Potential ◽  
Low Grade ◽  
Extraskeletal Myxoid Chondrosarcoma ◽  
Soft Tissue Neoplasm ◽  
Myxoid Chondrosarcoma ◽  
Myxoid Matrix

Extraskeletal Myxoid Chondrosarcoma (EMC) is a rare soft tissue sarcoma of uncertain differentiation characterized by abundant myxoid matrix located in the soft tissues. It affects mainly the soft tissues of the proximal end of long bones. EMC has a male preference, and this occurs in soft tissue area in patients who are more than 40 years old. The present case was 63 year old female diagnosed as EMC on histopathological examination with immuno–histochemical confirmation and after eight months presented with pulmonary and inguinal metastasis. EMC is a rare tumor should be considered in the differential diagnosis of myxoid soft tissue neoplasm. Therefore, a multi-modal approach, having distinct clinical, cytological, histo-pathological, immunohistochemical features and cytogenetics analysis, must be necessary in establishing a more definitive diagnosis, which may finally lead to a more targeted and specific treatment for patients.         Keywords: Extraskeletal myxoid chondrosarcoma, Inguinal metastasis, low grade tumor, IHC

scholarly journals A Case of Extraskeletal Myxoid Chondrosarcoma.

1998 ◽  
Vol 47 (1) ◽  
pp. 113-117
Author(s):  
Noburo Hashimoto ◽  
Kazutoshi Nomura ◽  
Mako Hirano ◽  
Tetsuya Fukumoto ◽  
Suguru Ohshima
Keyword(s):  
Extraskeletal Myxoid Chondrosarcoma ◽  
Myxoid Chondrosarcoma

Extraskeletal myxoid chondrosarcoma: A report of a gynecologic case

2005 ◽  
Vol 98 (3) ◽  
pp. 498-501 ◽  
Author(s):  
Mildred R. SantaCruz ◽  
Lori Proctor ◽  
David B. Thomas ◽  
Paola A. Gehrig
Keyword(s):  
Extraskeletal Myxoid Chondrosarcoma ◽  
Myxoid Chondrosarcoma
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