scholarly journals Clear cell sarcoma of the kidney in Austrian children: Long‐term survival after relapse

2021 ◽  
Author(s):  
Waltraud Friesenbichler ◽  
Roswitha Lüftinger ◽  
Gabriele Kropshofer ◽  
Martin Henkel ◽  
Gabriele Amann ◽  
...  
2020 ◽  
Vol 6 (1) ◽  
Author(s):  
Takuhisa Okada ◽  
Yasumitsu Hirano ◽  
Shintaro Ishikawa ◽  
Hiroka Kondo ◽  
Toshimasa Ishii ◽  
...  

Abstract Background Clear cell sarcoma-like tumor of the gastrointestinal tract (CCSLTGT) is extremely rare. It is a mesenchymal neoplasm that usually forms in the small intestine of adolescents and young adults, is prone to local recurrence and metastasis, and has a high mortality rate. We report a patient with CCSLTGT with lymph node- and liver metastases, who continues to survive 6 years after initial surgical resection. Case presentation A 38-year-old woman presented with lightheadedness. Laboratory analysis revealed anemia (hemoglobin, 6.7 g/dL), and enhanced computed tomography (CT) demonstrated a mass in the small intestine, about 6 cm in diameter, with swelling of 2 regional lymph nodes. Double-balloon small intestine endoscopic examination revealed a tumor accompanied by an ulcer; the biopsy findings suggested a primary cancer of the small intestine. She was admitted, and we then performed a laparotomy for partial resection of the small intestine with lymph node dissection. Pathologic examination revealed CCSLTGT with regional lymph node metastases. About 3 years later, follow-up CT revealed a single liver metastasis. Consequently, she underwent a laparoscopic partial liver resection. Histopathologic examination confirmed that the liver metastasis was consistent with CCSLTGT. It has now been 3 years without a recurrence. Conclusion Repeated radical surgical resection with close follow-up may be the only way to achieve long-term survival in patients with CCLSTGT.


2013 ◽  
Vol 104 (3) ◽  
pp. 549-553
Author(s):  
Takahisa Suzuki ◽  
Hiroshi Furuse ◽  
Yutaka Kurita ◽  
Takeshi Imanishi ◽  
Keita Tamura ◽  
...  

2012 ◽  
Vol 61 (3) ◽  
pp. 600-603
Author(s):  
Shinichiro Tanaka ◽  
Kiyoshi Oka ◽  
Toshitake Yakushiji ◽  
Hiroo Sato ◽  
and Hiroshi Mizuta

1995 ◽  
Vol 15 (2) ◽  
pp. 327-332 ◽  
Author(s):  
Paul Ferbend ◽  
Susan E. Crawford ◽  
Frank Gonzalez-Crussi

2012 ◽  
Vol 26 (7) ◽  
pp. 734-738
Author(s):  
Eiji Yamada ◽  
Kazuhiko Kataoka ◽  
Toshiya Fujiwara ◽  
Motoki Matsuura

2013 ◽  
Vol 23 (2) ◽  
pp. 244-248 ◽  
Author(s):  
Stefania Noli ◽  
Sonia Cipriani ◽  
Giovanna Scarfone ◽  
Antonella Villa ◽  
Elena Grossi ◽  
...  

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