scholarly journals A Rare Case of Granulomatosis With Polyangiitis Presenting as Retroperitoneal Fibrosis in the Peri-Iliac Region Causing Hydronephrosis

Cureus ◽  
2021 ◽  
Author(s):  
Kristijan Šoštarič ◽  
Tina Lovrec Krstić ◽  
Aleš Slanič ◽  
Primož Caf
Keyword(s):  
Rare Case ◽  
Granulomatosis With Polyangiitis ◽  
Retroperitoneal Fibrosis ◽  
Iliac Region

scholarly journals A Rare Case of Granulomatosis with Polyangiitis-Related Periaortitis at the Ascending Aorta

2019 ◽  
Vol 80 (3) ◽  
pp. 537
Author(s):  
Sang Hyup Hong ◽  
Gil-Sun Hong ◽  
Choong Wook Lee ◽  
Gi Hong Kim
Keyword(s):  
Rare Case ◽  
Granulomatosis With Polyangiitis ◽  
Ascending Aorta

scholarly journals Retroperitoneal fibrosis with periaortitis: A case report of an unusual form of presentation of granulomatosis with polyangiitis

2016 ◽  
Vol 19 ◽  
pp. 121-124
Author(s):  
Elizabeth Manuely González Revilla ◽  
Araceli Abad Fernandez ◽  
María Teresa Río Ramirez ◽  
Sara Calero Pardo ◽  
María Antonia Juretschke Moragues
Keyword(s):  
Case Report ◽  
Granulomatosis With Polyangiitis ◽  
Retroperitoneal Fibrosis ◽  
Unusual Form

scholarly journals A rare case of complex cardiac involvement in granulomatosis with polyangiitis

2017 ◽  
Vol 127 (1) ◽  
pp. 63-65
Author(s):  
Rafał Gałąska ◽  
Dorota Kulawiak‑Gałąska ◽  
Zenobia Czuszyńska ◽  
Anna Masiak ◽  
Zbigniew Zdrojewski ◽  
...  
Keyword(s):  
Rare Case ◽  
Cardiac Involvement ◽  
Granulomatosis With Polyangiitis

scholarly journals Giant Thrombosis at Left Anterior Descending Artery Aneurysm in a 10-Year Old Boy with Granulomatosis with Polyangiitis

2020 ◽  
Vol 2020 ◽  
pp. 1-5
Author(s):  
Ehsan Aghaei Moghadam ◽  
Nahid Aslani ◽  
Helia Mojtabavi ◽  
Farnoosh Larti ◽  
Azin Ghamari ◽  
...  
Keyword(s):  
Differential Diagnosis ◽  
Coronary Artery ◽  
Rare Case ◽  
Granulomatosis With Polyangiitis ◽  
Coronary Artery Aneurysm ◽  
Artery Aneurysm ◽  
Necrotizing Vasculitis ◽  
Annual Incidence Rate ◽  
Case Presentation ◽  
Coronary Aneurysms

Granulomatosis with polyangiitis (GPA), necrotizing vasculitis of small and medium-sized vessels, is traditionally believed to mainly affect respiratory tract with additional focal kidney involvements as its primary manifestations with a relatively rare annual incidence rate of 20-50 cases per million. Six percent of the affected cases have cardiac involvements; among which, aneurysms comprise the lowest penetrance. By this paper, we aim to cast light on clinical diagnostic and treatment methods of a rare case presentation, a 10-year-old male GPA patient, diagnosed with massive thrombosis at his coronary artery aneurysm. GPA should be considered as differential diagnosis of prolong fever and coronary aneurysms in adolescents.

scholarly journals A challenging diagnosis of MPO-C-ANCA EGPA

2019 ◽  
Vol 12 (7) ◽  
pp. e228621
Author(s):  
Gareth Lim ◽  
Sheryl Lim ◽  
Shang-Ian Tee ◽  
Chai Yiing Ling
Keyword(s):  
Nasopharyngeal Carcinoma ◽  
Rare Case ◽  
Granulomatosis With Polyangiitis ◽  
Late Onset ◽  
Rare Condition ◽  
Eosinophilic Granulomatosis With Polyangiitis ◽  
Mononeuritis Multiplex ◽  
Atypical Presentations ◽  
Eosinophilic Granulomatosis ◽  
Proximal Myopathy

Eosinophilic granulomatosis with polyangiitis (EGPA) is a multisystemic small-vessel vasculitic disease that can present with positive MPO-P-ANCA (myeloperoxidase–perinuclear–anti-neutrophil cytoplasmic antibody). It is a rare condition that is difficult to diagnose. We present the case of a 64-year-old man with late-onset adult asthma and treated nasopharyngeal carcinoma who initially presented to us with proximal myopathy. Thereafter, he developed a constellation of fleeting symptoms which included rhinosinusitis, mononeuritis multiplex, skin vasculitis and arthritis. Blood investigations showed that he had eosinophilia, and skin biopsy demonstrated dermal vasculitis with eosinophils. He was found to be MPO-C-ANCA positive, and although initially thought to have granulomatosis with polyangiitis, the diagnosis was later revised to EGPA. This case highlights the diagnostic challenges with atypical presentations of EGPA and also presents a rare case of positive MPO-C-ANCA that has never been described in EGPA before.

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