scholarly journals Sensorineural Hearing Loss and Systemic Autoimmune Disease: The Experience of a Systemic Immune-Mediated Diseases Unit

Cureus ◽  
2021 ◽  
Author(s):  
Renata Ribeiro ◽  
João F Serôdio ◽  
Marta C Amaral ◽  
Joana A Duarte ◽  
Carolina Durão ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Autoimmune Disease ◽  
Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Systemic Autoimmune Disease ◽  
Immune Mediated

Sudden Sensorineural Hearing Loss: Supporting the Immunologic Theory

2002 ◽  
Vol 111 (11) ◽  
pp. 989-997 ◽  
Author(s):  
José Ramón García Berrocal ◽  
Rafael Ramírez-Camacho
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Sudden Hearing Loss ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Systemic Autoimmune Disease ◽  
Pathological Findings ◽  
Diagnostic Challenge ◽  
Membranous Labyrinth ◽  
Immune Mediated

Sudden deafness constitutes a diagnostic challenge. Classically, 2 causes, viral and vascular, are considered in the origin of idiopathic sudden hearing loss. More recently added to the list of possibilities are rupture of the membranous labyrinth and immune-mediated sensorineural hearing loss. The latter can be either primary and localized to the inner ear or, in perhaps fewer than one third of cases, secondary to generalized systemic autoimmune disease. The purpose of the present review is to define immune-mediated sudden sensorineural hearing loss as a distinctive entity, on the basis of clinical, immunologic, and pathological findings, and suggest a profile of the typical patient.

Hearing and Sjögren's Syndrome

1996 ◽  
Vol 75 (10) ◽  
pp. 666-668 ◽  
Author(s):  
Martin S. Trott ◽  
Gordon B. Hughes ◽  
Leonard H. Calabrese ◽  
Barbara P. Barna ◽  
Richard H. Nodar
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Sjögren’S Syndrome ◽  
Sjögren's Syndrome ◽  
Lymphocyte Transformation ◽  
Sjogren’S Syndrome ◽  
Sjogren's Syndrome ◽  
Sensorineural Hearing ◽  
Immune Mediated ◽  
Sjögren‘S Syndrome

Immune sensorineural hearing loss is manifested in several systemic immune diseases.1,2 Although hearing loss has been previously documented in patients with Sjögren's syndrome (SS),3 the effect of SS on hearing is unclear. This prospective study was designed to assess the presence of hearing loss in 14 patients with SS and, if sensorineural hearing loss was present, to determine if the hearing loss was immune-mediated. Patients were evaluated with basic audiologic tests as well as for cellular immune inner ear reactivity as measured by the lymphocyte transformation test (LTT).4 Three patients had evidence of sensorineural hearing loss. Two patients had a positive LTT without evidence of sensorineural hearing loss. This preliminary study suggests that SS may not directly cause sensorineural hearing loss, immune-mediated or otherwise.

Effects of testosterone in the treatment of immune-mediated sensorineural hearing loss

2003 ◽  
Vol 260 (6) ◽  
pp. 316-319 ◽  
Author(s):  
Ki-Hong Chang ◽  
Shi-Nae Park ◽  
Sang W. Yeo ◽  
Byung-Do Suh
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Immune Mediated

Sweet's disease and profound, bilateral, sensorineural hearing loss

2009 ◽  
Vol 124 (1) ◽  
pp. 105-107 ◽  
Author(s):  
S Cheng ◽  
M da Cruz
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Cochlear Implantation ◽  
Definitive Diagnosis ◽  
Sensorineural Hearing ◽  
Immune Mediated ◽  
Inner Ear Disease ◽  
Bilateral Sensorineural Hearing Loss ◽  
Loss Of Hearing ◽  
Hearing Outcomes

AbstractObjective:We report a case of Sweet's disease associated with rapid, profound loss of hearing, against a background of progressive, bilateral, sensorineural hearing loss.Results:The clinical features were indistinguishable from those of immune-mediated inner ear disease. Establishment of a definitive diagnosis was a challenge due to the absence of a reliable diagnostic test. The patient was unresponsive to extensive immunosuppressive therapy and subsequently underwent cochlear implantation, with good hearing outcomes.Conclusions:Profound, bilateral, sensorineural hearing loss in the context of Sweet's disease may be related to the underlying immunological aetiology. Cochlear implantation can successfully restore hearing when immunotherapy fails.

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