scholarly journals Pulmonary agenesis

2022 ◽  
Author(s):  
Liz Silverstone
Keyword(s):  
Pulmonary Agenesis

Mitral Valve Replacement in an Adult with Left Pulmonary Agenesis

2015 ◽  
Vol 18 (3) ◽  
pp. 109
Author(s):  
Huseyin Saskin ◽  
Mustafa Idiz ◽  
Cagri Duzyol ◽  
Huseyin Macika ◽  
Rezan Aksoy
Keyword(s):  
Mitral Valve ◽  
Vitamin A ◽  
Valve Replacement ◽  
Viral Infections ◽  
Vitamin A Deficiency ◽  
Pulmonary Agenesis ◽  
Pulmonary Vessels ◽  
Live Births ◽  
Factors Associated ◽  
Female Predominance

Pulmonary agenesis is associated with the absence of pulmonary vessels, bronchi, or parenchyma. This condition usually occurs between the 4th and 5th week of gestation during the embryonic phase. Etiopathogenic factors associated with pulmonary agenesis are not fully understood. In the literature, genetic and teratogenic factors, viral infections, and vitamin-A deficiency are shown to be associated with pulmonary agenesis [Malcon 2012]. This condition may be seen unilaterally or bilaterally. Although the precise rate of incidence is unknown, it is estimated to occur in one of every 10,000 to 12,000 live births [Yetim 2011]. There is a 1.3:1 female predominance with unilateral agenesis [Halilbasic 2013]

scholarly journals Late presentation of unilateral lung agenesis in adulthood

2021 ◽  
Vol 52 (1) ◽  
Author(s):  
Arshed Hussain Parry ◽  
Mujahed Abdulsattar Ibrahim Raheem ◽  
Hussam Hassan Ismail ◽  
Osama Sharaf
Keyword(s):  
Main Bronchus ◽  
Left Lung ◽  
Left Hemithorax ◽  
Late Adulthood ◽  
Pulmonary Agenesis ◽  
Opaque Hemithorax ◽  
Dismal Prognosis ◽  
Mediastinal Shift ◽  
Lung Agenesis ◽  
Unilateral Pulmonary Agenesis

Abstract Background Pulmonary agenesis is a rare congenital anomaly with a reported prevalence of about 1 in 100,000 births. It may be bilateral or unilateral. Among the unilateral form, left lung agenesis is more common (70%); however, it is the right lung agenesis which carries a dismal prognosis due to the frequent association with a gamut of other congenital anomalies and greater degree of mediastinal shift leading to tracheo-bronchial and vascular distortion. The patients of unilateral pulmonary agenesis usually present in infancy or early childhood. Presentation in late adulthood as seen in our patient is rare. We present a case of left pulmonary agenesis that was diagnosed in 4th decade of life. Case presentation A 36-year-old male presented with gradually progressive exertional dyspnea of 1 month duration. Clinical examination revealed tachycardia and tachypnea. Chest radiograph showed opaque left hemithorax with ipsilateral mediastinal shift. Computed tomography clinched the diagnosis by demonstrating absence of left main bronchus, lung and left pulmonary artery with shift of heart, and great mediastinal vessels into left hemithorax. The patient was managed conservatively and discharged with attachment to out-patient department for regular follow-up. Conclusion Presentation of unilateral lung agenesis in late adulthood, as seen in the present case is extremely rare. This case report highlights that, a rare condition like unilateral pulmonary agenesis, should be considered in the list of differentials in an adult presenting with opaque hemithorax with ipsilateral mediastinal shift on radiography.

scholarly journals Pulmonary agenesis: A case report with review of literature

2013 ◽  
Vol 2013 (2) ◽  
pp. 14 ◽  
Author(s):  
Mir Sumsam Ali Khurram ◽  
Sundari Pratap Rao ◽  
Akkena Vamshipriya
Keyword(s):  
Case Report ◽  
Review Of Literature ◽  
Pulmonary Agenesis

Late diagnosis of pulmonary agenesis

2021 ◽  
Vol 14 (10) ◽  
pp. e245233
Author(s):  
Diana Alexandra Pimenta ◽  
Filipa Lemos Aguiar ◽  
Beatriz Celeiros Fernandes ◽  
Rui Rolo
Keyword(s):  
Early Childhood ◽  
Clinical Presentation ◽  
Lung Parenchyma ◽  
Asthma Diagnosis ◽  
Cardiovascular Malformations ◽  
Surgical Interventions ◽  
Pulmonary Agenesis ◽  
History Of ◽  
Lung Infections ◽  
Respiratory Complaints

Pulmonary agenesis is defined as the complete absence of one or both lungs, including the bronchi, bronchioles, vasculature and lung parenchyma. Most of these malformations are detected in early childhood. A residual number remains asymptomatic and undiagnosed until adulthood. The clinical presentation is wide, ranging from asymptomatic to respiratory complaints like dyspnoea, respiratory distress and a history of recurrent lung infections. This case presents a 54-year-old woman with complaints of coughing, dyspnoea for medium exertion and wheezing for a couple of months. Based on the results of complementary diagnosis methods, right pulmonary agenesis was diagnosed without other malformations. Simultaneously, an asthma diagnosis was also performed. The treatment of pulmonary agenesis is symptomatic. Simultaneous cardiovascular malformations could require surgical interventions. This case demonstrates that pulmonary agenesis may remain undiagnosed, be identified incidentally, and have a good and long prognosis.

Unilateral Pulmonary Agenesis Without Mediastinal Displacement

1997 ◽  
Vol 90 (3) ◽  
pp. 335-337 ◽  
Author(s):  
ARLENE S. ROQUE ◽  
EDWARD M. BURTON ◽  
R FREDERICK BOEDY ◽  
GREER FALLS ◽  
JATINDER S. BHATIA
Keyword(s):  
Pulmonary Agenesis ◽  
Unilateral Pulmonary Agenesis

Pulmonary agenesis with esophageal atresia and tracheoesophageal fistula

1987 ◽  
Vol 22 (2) ◽  
pp. 125-126 ◽  
Author(s):  
Kazue Takayanagi ◽  
Elizabieta Grochowska ◽  
Samier Abu-El Nas
Keyword(s):  
Esophageal Atresia ◽  
Tracheoesophageal Fistula ◽  
Pulmonary Agenesis

Prenatal diagnosis of unilateral pulmonary agenesis in a pregnant woman undergoing chronic hemodialysis due to chronic renal failure

2009 ◽  
Vol 29 (7) ◽  
pp. 707-709 ◽  
Author(s):  
Taro Nonaka ◽  
Akira Kikuchi ◽  
Naoko Kido ◽  
Yasuhiro Takahashi ◽  
Kyoko Yamada ◽  
...  
Keyword(s):  
Renal Failure ◽  
Pregnant Woman ◽  
Prenatal Diagnosis ◽  
Chronic Renal Failure ◽  
Chronic Hemodialysis ◽  
Pulmonary Agenesis ◽  
Unilateral Pulmonary Agenesis

scholarly journals Displacement of the heart caused by pulmonary agenesis

Heart ◽  
2002 ◽  
Vol 88 (3) ◽  
pp. 277-277 ◽  
Author(s):  
T R D Shaw
Keyword(s):  
Pulmonary Agenesis
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