scholarly journals Sporadic supravalvular stenosis in a young man

2013 ◽  
Vol 96 (1) ◽  
pp. 27
Author(s):  
KM Ghodduci ◽  
M Antic ◽  
K Tanaka ◽  
D Verdries ◽  
D Kerkhove
Keyword(s):  
Supravalvular Stenosis

scholarly journals Surgical outcome of isolated congenital supravalvular pulmonary stenosis: a case series

2019 ◽  
Vol 3 (2) ◽  
Author(s):  
Vikas Kumar ◽  
Sachin Mahajan ◽  
Vivek Jaswal ◽  
Shyam Kumar Singh Thingnam
Keyword(s):  
Pulmonary Stenosis ◽  
Main Pulmonary Artery ◽  
Tertiary Care ◽  
Case Series ◽  
Surgical Correction ◽  
Medium Term ◽  
Constriction Band ◽  
Supravalvular Stenosis ◽  
Mid Term Results

Abstract Background Supravalvular stenosis of main pulmonary artery is a rare anomaly characterized by the presence of constriction band just above the pulmonary valve. It is mostly acquired after intervention on the pulmonary trunk or less commonly is congenital in origin associated with complex congenital cardiac malformations and very rarely can present as an isolated native congenital supravalvular pulmonary stenosis (SPS). Case summary We present a series of four cases of isolated congenital SPS who underwent surgical correction at our tertiary care institute over 8 years. Mean age of the patients was 2.25 ± 0.96 years with all of them being males. Mean peak systolic gradient across the stenosis was 82 ± 21.48 mmHg ranging from 60 mmHg to 110 mmHg. There was no early and medium-term mortality with 100% survival at mean follow-up of 31 months (range 7–85 months). Discussion Surgical correction of congenital SPS carries excellent early and mid-term results with almost no mortality and very low risk of re-intervention for restenosis.

VITAMIN D AND CRANIOFACIAL AND DENTAL ANOMALIES OF SUPRAVALVULAR STENOSIS

PEDIATRICS ◽  
1969 ◽  
Vol 43 (1) ◽  
pp. 1-2
Author(s):  
Richard D. Rowa ◽  
Robert E. Cooke
Keyword(s):  
Vitamin D ◽  
Mental Retardation ◽  
Pulmonary Stenosis ◽  
Vascular Disorder ◽  
Dental Anomalies ◽  
Older Children ◽  
The Past ◽  
Sick Children ◽  
Supravalvular Stenosis ◽  
Pediatric Disorders

Few pediatric disorders have undergone such fascinating extensions to their clinical picture as has been the case in idiopathic hypercalcemia of infancy during the past decade. Features of the infantile illness were described in the early 1950 by workers in England and Europe. Ten years later an apparently unrelated vascular disorder comprising a peculiar facies, mental retardation, supravalvular aortic and pulmonary stenosis and dental anomalies was reported from New Zealand and Germany. Black and Bonham Carter, at the Hospital for Sick Children, Great Ormond Street, through recognizing a similarity between the facial apperance of these retarded older children and the elfin facies characteristic of infantile hypercalcemia, were able to postulate a relationship between the two clinical entities.

scholarly journals Aortopulmonary Fistula after Multiple Pulmonary Artery Stenting and Dilatation for Postarterial Switch Supravalvular Stenosis

2015 ◽  
Vol 2015 ◽  
pp. 1-3
Author(s):  
Maude Pagé ◽  
Oana Nastase ◽  
Frédéric Maes ◽  
Joëlle Kefer ◽  
Thierry Sluysmans ◽  
...  
Keyword(s):  
Heart Failure ◽  
Pulmonary Artery ◽  
Arterial Switch Operation ◽  
Covered Stent ◽  
Unusual Complication ◽  
Switch Operation ◽  
The Face ◽  
Timely Fashion ◽  
Aortopulmonary Fistula ◽  
Supravalvular Stenosis

We present a case of iatrogenic aortopulmonary fistula following pulmonary artery (PA) stenting late after arterial switch operation (ASO) for D-transposition of the great arteries (D-TGA), an unusual complication that may be encountered more frequently in contemporary adult cardiology clinics. The diagnosis should be sought in the face of unexplained heart failure in patients who underwent ASO and subsequent PA angioplasty. Treatment should be instituted in a timely fashion, and options include surgical correction or implantation of a duct occluder or covered stent.

scholarly journals Late reoperation after proximal repair of supravalvular stenosis for diffuse form of Williams–Beuren syndrome

2020 ◽  
Vol 3 ◽  
pp. 79-81
Author(s):  
Shintaro Katahira ◽  
Yukiharu Sugimura ◽  
Artur Lichtenberg ◽  
Payam Akhyari
Keyword(s):  
Diffuse Form ◽  
Supravalvular Stenosis

scholarly journals Supravalvular stenosis after disc mitral valve replacement

1971 ◽  
Vol 62 (5) ◽  
pp. 810-812 ◽  
Author(s):  
Albert K. Rogers ◽  
Jacob R. Morgan ◽  
Alan D. Forker ◽  
Richard G. Fosburg
Keyword(s):  
Mitral Valve ◽  
Valve Replacement ◽  
Mitral Valve Replacement ◽  
Supravalvular Stenosis
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