Primitive neuroectodermal tumour of kidney with thrombosis of the inferior vena cava and good responsive to surgical and medical treatment: description of a case and revision of literature

2017 ◽  
Vol 85 (3) ◽  
pp. 127-129
Author(s):  
Giovanni L. Giliberto ◽  
Carmelo A. Di Franco ◽  
Bruno Rovereto
Keyword(s):  
Inferior Vena Cava ◽  
Inferior Vena ◽  
Histopathological Examination ◽  
Vena Cava ◽  
Nodal Metastasis ◽  
Small Cells ◽  
Retroperitoneal Lymphadenectomy ◽  
Primitive Neuroectodermal Tumour ◽  
Computed Tomographic ◽  
Neuroectodermal Tumour

Primitive neuroectodermal tumour (PNET) of kidney is a rare cancer typical of young adults with few cases described in the literature. We report a case of renal PNET in a 31-year-old man who presented to our department with a computed tomographic (CT)-scan revealing a large renal mass of 20 cm, massive thrombosis of the inferior vena cava (IVC). The patient underwent radical nephrectomy with contextual retroperitoneal lymphadenectomy and resection of IVC needing Dacron prosthesis substitution. Definitive histopathological examination showed PNET of kidney infiltrating ipsilateral adrenal gland, massive cava thrombosis with infiltration of vena cava wall and one lymph nodal metastasis. Postoperative PET-scan showed metastatic lesions in bilateral adrenal glands and pancreas. The patient received chemotherapy, and currently, he is in follow-up after 26 months from first diagnosis without any sign of recurrence of disease. Kidney PNET usually is associated with poor prognosis, so, it needs an early identification and differentiation from other similar small cells tumours in order to obtain a good response to the treatments.

scholarly journals Primitive Neuroectodermal Tumour Invading the Inferior Vena Cava

2020 ◽  
Author(s):  
Ali Mir ◽  
Marzieh Lashkari ◽  
Fatemeh Jafari ◽  
Behnam Molavi
Keyword(s):  
Inferior Vena Cava ◽  
Inferior Vena ◽  
Spindle Cell ◽  
Present Report ◽  
Vena Cava ◽  
Primitive Neuroectodermal Tumour ◽  
Spindle Cell Neoplasm ◽  
Neuroectodermal Tumour ◽  
Cell Neoplasm

In the present report, we describe our experience with a 44-year-old male with abnormal retroperitoneal primitive neuroectodermal tumours (PNETs) in our hospital, who was operated on with a spindle cell neoplasm diagnosis.

scholarly journals Renal primitive neuroectodermal tumour: Case series and brief review

2014 ◽  
Vol 8 (3-4) ◽  
pp. 241
Author(s):  
Tadeusz Kroczak ◽  
Rajan Sharda ◽  
Darrel Drachenberg ◽  
Turki Al-Essawi
Keyword(s):  
Literature Review ◽  
Inferior Vena Cava ◽  
Primitive Neuroectodermal Tumor ◽  
Inferior Vena ◽  
Vena Cava ◽  
Case Series ◽  
Primitive Neuroectodermal Tumour ◽  
Pathologic Features ◽  
Rare Malignancy ◽  
Pathologic Analysis

Renal primitive neuroectodermal tumor is a rare malignancy. These tumours rarely present with caval involvement. We report 2 cases of primitive neuroectodermal tumours (PNETs) with inferior vena cava involvement. The initial presentation and outcomes differed significantly. The diagnosis was confirmed using histologic and pathologic analysis. We present a brief literature review and an outline of typical clinical and pathologic features of renal PNETs.

Flattened inferior vena cava: A normal finding on unenhanced abdominal computed tomographic scan

1996 ◽  
Vol 3 (1) ◽  
pp. 16-19
Author(s):  
Ronald H. Wachsberg ◽  
Charles D. Levine ◽  
Stephen R. Baker
Keyword(s):  
Inferior Vena Cava ◽  
Inferior Vena ◽  
Vena Cava ◽  
Normal Finding ◽  
Computed Tomographic ◽  
Computed Tomographic Scan

scholarly journals Leiomyosarcoma of the inferior vena cava

Medicina ◽  
2010 ◽  
Vol 46 (3) ◽  
pp. 200 ◽  
Author(s):  
Edita Bieliūnienė ◽  
Giedrė Kavaliauskienė ◽  
Dalia Mitraitė ◽  
Eglė Jonaitienė ◽  
Algidas Basevičius ◽  
...  
Keyword(s):  
Inferior Vena Cava ◽  
Inferior Vena ◽  
Histopathological Examination ◽  
Vena Cava ◽  
Retroperitoneal Tumor ◽  
Therapeutic Modality ◽  
Rare Tumor ◽  
Resonance Imaging ◽  
Middle Segment ◽  
Reliable Diagnosis

Leiomyosarcoma is a rare tumor of mesenchymal origin usually affecting the inferior vena cava. Early diagnosis is essential before surgical resection, which is the only therapeutic modality that prolongs patients’ survival. Ultrasonography, computer tomography, and magnetic resonance imaging are the main imaging modalities in this case. Combined with guided biopsies, they form the mainstay of reliable diagnosis. We report a case with retroperitoneal tumor arising from the middle segment of the inferior vena cava. Radiological examination revealed retroperitoneal tumor and helped to choose surgical treatment. Histopathological examination confirmed the diagnosis of leiomyosarcoma of the inferior vena cava.

Computed Tomographic Demonstration of Anomalous Inferior Vena Cava with Azygos Continuation

1980 ◽  
Vol 4 (3) ◽  
pp. 398-402 ◽  
Author(s):  
Robert J. Churchill ◽  
George Wesby ◽  
Richard E. Marsan ◽  
Rogelio Moncada ◽  
Carlos J. Reynes ◽  
...  
Keyword(s):  
Inferior Vena Cava ◽  
Inferior Vena ◽  
Vena Cava ◽  
Computed Tomographic ◽  
Azygos Continuation ◽  
Anomalous Inferior Vena Cava

Fainting as an unusual presentation of a large inferior vena cava leiomyosarcoma

2014 ◽  
Vol 30 (7) ◽  
pp. 492-495
Author(s):  
Giuseppe Massimiliano De Luca ◽  
Angela Gurrado ◽  
Andrea Marzullo ◽  
Giuseppe Piccinni ◽  
Riccardo Memeo ◽  
...  
Keyword(s):  
Inferior Vena Cava ◽  
Inferior Vena ◽  
Histopathological Examination ◽  
Vena Cava ◽  
En Bloc Resection ◽  
Postoperative Recovery ◽  
Bloc Resection ◽  
Whole Body ◽  
En Bloc ◽  
Primary Tumors

Objectives Primary tumors of the inferior vena cava are rare, with leiomyosarcoma representing the vast majority. Method A 60-year-old man was admitted in emergency for fainting and mild anemia. A whole-body computed tomography revealed a retroperitoneal mass of approximately 8 cm in diameter, invading the lumen of the inferior vena cava, extending to the renal vein confluence. An en bloc resection of the solid mass was performed. Macroscopically the tumor did not seem to insist on the resection margin. Results Histopathological examination confirmed the diagnosis of leiomyosarcoma of the inferior vena cava. Postoperative recovery was uneventful and the patient was discharged after eight days, starting adjuvant chemotherapy. During the follow-up, the patient did not show other fainting episode, and at 24 months he is disease free. Conclusions: Unusually, fainting could even be the isolated sign of a large leiomyosarcoma of the inferior vena cava, also when it affects its middle portion.

Sign in / Sign up

Export Citation Format

Share Document