scholarly journals A Rare and Unexpected Cause of Pulmonary Hypertension: Pulmonary Capillary Hemangiomatosis

2016 ◽  
Vol 38 (2) ◽  
pp. 75-77
Author(s):  
Gonca Koc ◽  
Selim Doganay ◽  
Nuri Tutar ◽  
Olgun Kontas ◽  
Inci Gulmez ◽  
...  
Keyword(s):  
Pulmonary Hypertension ◽  
Pulmonary Capillary ◽  
Pulmonary Capillary Hemangiomatosis

Pulmonary Capillary Hemangiomatosis Associated with Primary Pulmonary Hypertension

Medicine ◽  
2002 ◽  
Vol 81 (6) ◽  
pp. 417-424 ◽  
Author(s):  
PEDRO ALMAGRO ◽  
JOAQUIM JULIÀ ◽  
MARIA SANJAUME ◽  
GUADALUPE GONZÁLEZ ◽  
JAUME CASALOTS ◽  
...  
Keyword(s):  
Pulmonary Hypertension ◽  
Primary Pulmonary Hypertension ◽  
Pulmonary Capillary ◽  
Pulmonary Capillary Hemangiomatosis

Pulmonary Capillary Hemangiomatosis: A Rare Cause of Pulmonary Hypertension

CHEST Journal ◽  
2015 ◽  
Vol 148 (4) ◽  
pp. 989A
Author(s):  
Glenda Euceda ◽  
Michael Denson ◽  
Steven Sieber ◽  
David Oelberg
Keyword(s):  
Pulmonary Hypertension ◽  
Pulmonary Capillary ◽  
Pulmonary Capillary Hemangiomatosis

An autopsy case of pulmonary capillary hemangiomatosis without evidence of pulmonary hypertension

2001 ◽  
Vol 439 (4) ◽  
pp. 586-592 ◽  
Author(s):  
Hajime Umezu ◽  
Makoto Naito ◽  
Kumiko Yagisawa ◽  
Akira Hattori ◽  
Yoshifusa Aizawa
Keyword(s):  
Pulmonary Hypertension ◽  
Autopsy Case ◽  
Pulmonary Capillary ◽  
Pulmonary Capillary Hemangiomatosis

PULMONARY CAPILLARY HEMANGIOMATOSIS: A CONSIDERATION IN UNEXPLAINED PULMONARY HYPERTENSION

CHEST Journal ◽  
2005 ◽  
Vol 128 (4) ◽  
pp. 460S ◽  
Author(s):  
D.L. Bedsole ◽  
Katrin Klemm ◽  
George L. Zorn ◽  
Keith M. Wille
Keyword(s):  
Pulmonary Hypertension ◽  
Pulmonary Capillary ◽  
Pulmonary Capillary Hemangiomatosis

scholarly journals Familial Pulmonary Capillary Hemangiomatosis Early in Life

2011 ◽  
Vol 2011 ◽  
pp. 1-6
Author(s):  
Johannes Wirbelauer ◽  
Helge Hebestreit ◽  
Alexander Marx ◽  
Eugene J. Mark ◽  
Christian P. Speer
Keyword(s):  
Pulmonary Hypertension ◽  
Respiratory Failure ◽  
Viral Infections ◽  
Main Bronchus ◽  
Ductus Arteriosus ◽  
Clinical Signs ◽  
Systemic Steroid ◽  
Bronchial Obstruction ◽  
Pulmonary Capillary ◽  
Pulmonary Capillary Hemangiomatosis

Background. Pulmonary capillary hemangiomatosis (PCH) is a rare disease, especially in infancy. Four infants have been reported up to the age of 12 months. So far, no familial patients are observed at this age.Patients. We report three siblings, two female newborns and a foetus of 15-week gestation of unrelated, healthy parents suffering from histologically proven PCH. The first girl presented with increased O2requirements shortly after birth and patentductus arteriosus(PDA). She subsequently developed progressive respiratory failure and pulmonary hypertension and died at the age of five months. The second girl presented with clinical signs of bronchial obstruction at the age of three months. The work-up showed a PDA—which was surgically closed—pulmonary hypertension, and bronchial wall instability with stenosis of the left main bronchus. Transient oxygen therapy was required with viral infections. The girl is now six years old and clinically stable without additional O2requirements. Failure to thrive during infancy and a somewhat delayed development may be the consequence of the disease itself but also could be attributed to repeated episodes of respiratory failure and a long-term systemic steroid therapy. The third pregnancy ended as spontaneous abortion. The foetus showed histological signs of PCH.Conclusion. Despite the differences in clinical course, the trias of PCH, PDA, and pulmonary hypertension in the two life born girls suggests a genetic background.

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