scholarly journals Combined mitral valve replacement associated with the Bentall procedure, diaphragmatic hernia repair and reconstruction of the pectus excavatum in a 26-year-old patient with Marfan syndrome

2016 ◽  
Vol 2 ◽  
pp. 135-139
Author(s):  
Piotr Stępiński ◽  
Tomasz Stankowski ◽  
Sleiman Sebastian Aboul-Hassan ◽  
Anna Szymańska ◽  
Jakub Marczak ◽  
...  
Keyword(s):  
Mitral Valve ◽  
Hernia Repair ◽  
Marfan Syndrome ◽  
Valve Replacement ◽  
Mitral Valve Replacement ◽  
Diaphragmatic Hernia ◽  
Pectus Excavatum ◽  
Bentall Procedure ◽  
Diaphragmatic Hernia Repair

scholarly journals Echocardiographic versus Histologic Findings in Marfan Syndrome

2015 ◽  
Vol 42 (1) ◽  
pp. 30-34 ◽  
Author(s):  
Xiaoyan Gu ◽  
Yihua He ◽  
Zhian Li ◽  
Jiancheng Han ◽  
Jian Chen ◽  
...  
Keyword(s):  
Mitral Valve ◽  
Mitral Regurgitation ◽  
Aortic Regurgitation ◽  
Marfan Syndrome ◽  
Valve Replacement ◽  
Mitral Valve Replacement ◽  
Severe Mitral Regurgitation ◽  
Severe Aortic Regurgitation ◽  
Myxomatous Degeneration ◽  
Histologic Changes

This retrospective study attempted to establish the prevalence of multiple-valve involvement in Marfan syndrome and to compare echocardiographic with histopathologic findings in Marfan patients undergoing valvular or aortic surgery. We reviewed echocardiograms of 73 Marfan patients who underwent cardiovascular surgery from January 2004 through October 2009. Tissue histology was available for comparison in 29 patients. Among the 73 patients, 66 underwent aortic valve replacement or the Bentall procedure. Histologic findings were available in 29 patients, all of whom had myxomatous degeneration. Of 63 patients with moderate or severe aortic regurgitation as determined by echocardiography, 4 had thickened aortic valves. The echocardiographic findings in 18 patients with mitral involvement included mitral prolapse in 15. Of 11 patients with moderate or severe mitral regurgitation as determined by echocardiography, 4 underwent mitral valve repair and 7 mitral valve replacement. Histologic findings among mitral valve replacement patients showed thickened valve tissue and myxomatous degeneration. Tricuspid involvement was seen echocardiographically in 8 patients, all of whom had tricuspid prolapse. Two patients had severe tricuspid regurgitation, and both underwent repair. Both mitral and tricuspid involvement were seen echocardiographically in 7 patients. Among the 73 patients undergoing cardiac surgery for Marfan syndrome, 66 had moderate or severe aortic regurgitation, although their valves manifested few histologic changes. Eighteen patients had mitral involvement (moderate or severe mitral regurgitation, prolapse, or both), and 8 had tricuspid involvement. Mitral valves were most frequently found to have histologic changes, but the tricuspid valve was invariably involved.

Single-stage open repair of severe asymmetric pectus excavatum and mitral valve replacement in connective tissue disease

2021 ◽  
pp. 021849232110140
Author(s):  
Cheong Ping Pau ◽  
Kee Soon Chong ◽  
Mohd Azhari Yakub ◽  
Alizan Abdul Khalil
Keyword(s):  
Mitral Valve ◽  
Valve Replacement ◽  
Mitral Valve Replacement ◽  
Pectus Excavatum ◽  
Pedicled Flap ◽  
Single Stage ◽  
Left Hemithorax ◽  
Mammary Arteries ◽  
Internal Mammary ◽  
The Right

We present a 14-year-old boy with Loey–Dietz syndrome with severe mitral regurgitation, pectus excavatum and scoliosis. The Haller index was 25. The heart was displaced into the left hemithorax. The right inferior pulmonary vein was very close to the sternum and vertebral body. Single-stage surgery was performed. An osseo-myo-cutaneous pedicled flap was created by sterno-manubrial junction dislocation and rib resection with bilateral internal mammary arteries supplying the flap. Cardiopulmonary bypass and mitral valve replacement was performed. The defect was bridged with three straight plates. The flap was laid on top and anchored. Early outcome at three months was good.

scholarly journals David procedure for aortic root aneurysm in the background of Marfan syndrome patient with severe kyphoscoliosis and previous mitral valve replacement

2021 ◽  
Author(s):  
Mohd Faizal Effendi Zulkifli ◽  
Muhamad Azri Muhamad Marican ◽  
Mohamad Arif Muhammad Nor ◽  
Abdul Muiz Jasid ◽  
Mohd Hamzah Kamarulzaman
Keyword(s):  
Coronary Artery ◽  
Mitral Valve ◽  
Marfan Syndrome ◽  
Valve Replacement ◽  
Aortic Root ◽  
Pectus Excavatum ◽  
Syndrome Patient ◽  
Root Repair ◽  
Valve Sparing ◽  
Aortic Root Repair

Cardiac complication is one of the diseases that usually develop in Marfan syndrome patient such as mitral valve regurgitation and aortic root aneurysm. Apart from that, other congenital anomalies also tend to occur in this group of patients such as pectus excavatum and scoliosis. We report a case of successful high-risk surgery involving a Marfan syndrome patient who had underlying severe kyphoscoliosis and previous mitral valve replacement that underwent redo sternotomy and valve sparing aortic root repair (David procedure). The surgery was challenging due to the need to perform redo-sternotomy on severe pectus patient, performing valve sparing aortic root repair, and complicated with injury to right coronary artery require modified Cabrol modification for implantation of the coronary artery. The available literature about redo sternotomy on severe pectus excavatum for aortic root repair is limited, hence this paper aims to highlight the successful of performing the procedure, and the complication that might occur during the procedure.

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