scholarly journals Staged Repair for a Patient with Infracardiac Total Anomalous Pulmonary Venous Connection Complicated by Hypoplastic Left Heart Complex

2016 ◽  
Vol 45 (1) ◽  
pp. 32-36
Author(s):  
Tomohiro Nakata ◽  
Tadashi Ikeda ◽  
Kenji Minakata ◽  
Kazuhiro Yamazaki ◽  
Hisashi Sakaguchi ◽  
...  
Keyword(s):  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Anomalous Pulmonary Venous Connection ◽  
Hypoplastic Left Heart Complex

Total anomalous pulmonary venous connection mimicking hypoplastic left heart syndrome

2021 ◽  
pp. 1-3
Author(s):  
Ryohei Matsuoka ◽  
Jun Muneuchi ◽  
Yoshie Ochiai
Keyword(s):  
Left Ventricle ◽  
Systemic Circulation ◽  
Z Score ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Transverse Arch ◽  
Anomalous Pulmonary Vein ◽  
Pulmonary Arterial ◽  
Left Heart Syndrome ◽  
Anomalous Pulmonary Venous Connection

Abstract A newborn with supracardiac total anomalous pulmonary venous connection vein presented the small left ventricle with z score of −7.5, retrograde blood supply in the transverse arch, and the dutcus-dependent systemic circulation. The patient underwent the repair of the anomalous pulmonary vein and bilateral pulmonary arterial banding soon after the birth and then transcatheter pulmonary arterial debanding at the age of 10 months because of an appropriate growth of the left ventricle.

scholarly journals Hypoplastic left heart complex.

1967 ◽  
Vol 4 (2) ◽  
pp. 83-87 ◽  
Author(s):  
E D Alberman ◽  
J M Fedrick ◽  
W H Schutt
Keyword(s):  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Hypoplastic Left Heart Complex

scholarly journals Growth of hypoplastic mitral valves in hypoplastic left heart complex and similar constellations after anatomical left superior vena cava correction

2020 ◽  
Vol 59 (1) ◽  
pp. 236-243
Author(s):  
Robert A Cesnjevar ◽  
Frank Harig ◽  
Moritz Dietz ◽  
Muhannad Alkassar ◽  
Wolfgang Waellisch ◽  
...  
Keyword(s):  
Superior Vena Cava ◽  
Coronary Sinus ◽  
Superior Vena ◽  
Vena Cava ◽  
Innominate Vein ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Mitral Inflow ◽  
Z Scores ◽  
Hypoplastic Left Heart Complex

Abstract OBJECTIVES Left superior vena cava (LSVC)-related obstruction of mitral inflow is a rare finding in patients with complex cardiac anomalies like hypoplastic left heart complex. We report our experience by establishing a left superior to right superior caval vein continuity (innominate vein creation by direct LSVC–right superior vena cava end-to-side-anastomosis), and coronary sinus unroofing if indicated for LSVC-related mitral inflow obstruction. METHODS Nineteen patients (median age: 1.0 ± 0.3 years; range: 7 days–4.8 years) underwent anatomical correction of LSVC without the use of foreign material in conjunction with repair or palliation of congenital anomalies in a single centre between April 2015 and November 2019. Indications for the procedure were LSVC-related obstruction of left ventricular inflow due to a dilated coronary sinus. Additional procedures included mitral (n = 7) or atrioventricular (n = 3) valve surgery, right ventricular to pulmonary artery conduit (n = 3), first stage palliation (n = 3) or biventricular repair (n = 5) of hypoplastic left heart complex. Three patients needed secondary mitral valve replacement (n = 3). RESULTS All LSVC or coronary sinus-related obstructions were effectively relieved. No patient died early, 2 patients died late after the procedure. One patient needed stenting of the superior vena cava below the unobstructed cephalad vein anastomosis at the former right superior vena cava-cannulation-site. Follow-up was complete and demonstrated an 89.5% survival after 2.5 ± 0.4 years. Innominate vein patency was 100% documented by echocardiography (n = 19), cardiac catheterization (n = 6) or both. Mean mitral valve z-scores before the operation were −1.7 ± 0.2 (range −3.8 to 0.3) and increased to 0.7 ± 0.2 (range −0.7 to 1.9) after LSVC repair. CONCLUSIONS Anatomical correction by surgical creation of an innominate vein is an effective method to relieve LSVC-related obstructions and promotes mitral valvar growth. Mitral ring sizes were at least normalized after surgery at the time of discharge. Further prospective follow-up studies to evaluate the growth potential of left-sided heart structures by reporting cardiac z-scores are needed to evaluate the true impact of coronary sinus unroofing.

Comparability of Z-Score Equations of Cardiac Structures in Hypoplastic Left Heart Complex

2013 ◽  
Vol 26 (11) ◽  
pp. 1314-1321 ◽  
Author(s):  
Martijn H.T. den Dekker ◽  
Martijn G. Slieker ◽  
A. Christian Blank ◽  
Felix Haas ◽  
Matthias W. Freund
Keyword(s):  
Z Score ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Hypoplastic Left Heart Complex

Case report: duct dependency in hypoplastic left heart complex can be reversible without surgery

2020 ◽  
pp. 1-4
Author(s):  
Abdullah N. Alhuzaimi
Keyword(s):  
Case Report ◽  
Left Ventricle ◽  
Aortic Arch ◽  
Loading Condition ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Resource Limitations ◽  
Hypoplastic Left Heart Complex

Abstract We describe an infant with duct-dependent hypoplastic left heart complex with moderate hypoplasia of the left ventricle and aortic arch who was not operated due to resource limitations. The left-sided structures grew remarkably due to favourable loading condition changes of the left ventricle, allowing weaning from prostaglandin at the age of 3 months and discharging the patient without intervention.

Totally anomalous pulmonary venous connection through the right lung and via a “Scimitar” vein to the inferior caval vein

1993 ◽  
Vol 3 (1) ◽  
pp. 85-87
Author(s):  
Rakesh Dua ◽  
Christine McTigue ◽  
James.L Wilkinson
Keyword(s):  
Pulmonary Vein ◽  
Pulmonary Veins ◽  
Left Lung ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Caval Vein ◽  
Inferior Caval Vein ◽  
The Right ◽  
Left Heart Syndrome ◽  
Anomalous Pulmonary Venous Connection

AbstractWe report a case of totally anomalous pulmonary venous connection in which the two pulmonary veins from the left lung joined to form a common vein which then passed across the midline into a hypoplastic right lung and, after receiving small veins from the right lung, passed inferiorly, exiting the lung below the hilum as a “scimitar” vein and terminating in the inferior caval vein. A separate pulmonary vein from the right lung passed inferiorly independently and joined the “scimitar” vein before it entered the inferior caval vein. There was an associated hypoplastic left heart syndrome.

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