scholarly journals Aortic Root Replacement for Annuloaortic Ectasia in Ehlers-Danlos Syndrome.

2002 ◽  
Vol 31 (4) ◽  
pp. 288-291
Author(s):  
Hiroshi Kumano ◽  
Akimitsu Yamaguchi ◽  
Tatsuya Kiji ◽  
Hiroyuki Maruhashi ◽  
Satoshi Kato
Keyword(s):  
Aortic Root ◽  
Aortic Root Replacement ◽  
Ehlers Danlos Syndrome ◽  
Annuloaortic Ectasia ◽  
Danlos Syndrome

scholarly journals Should the transverse aortic arch be replaced simultaneously with aortic root replacement for annuloaortic ectasia in marfan syndrome?

2004 ◽  
Vol 127 (5) ◽  
pp. 1373-1380 ◽  
Author(s):  
Osamu Tagusari ◽  
Hitoshi Ogino ◽  
Junjiro Kobayashi ◽  
Ko Bando ◽  
Kenji Minatoya ◽  
...  
Keyword(s):  
Aortic Arch ◽  
Marfan Syndrome ◽  
Aortic Root ◽  
Aortic Root Replacement ◽  
Annuloaortic Ectasia

Aortic root dilatation in Ehlers-Danlos syndrome types I, II and III A report of five cases

2008 ◽  
Vol 53 (6) ◽  
pp. 460-465 ◽  
Author(s):  
George E. Tiller ◽  
Suzanne B. Cassidy ◽  
Christine Wensel ◽  
Richard J. Wenstrup
Keyword(s):  
Aortic Root ◽  
Ehlers Danlos Syndrome ◽  
Aortic Root Dilatation ◽  
Danlos Syndrome

Cross-Sectional and Longitudinal Assessment of Aortic Root Dilation and Valvular Anomalies in Hypermobile and Classic Ehlers-Danlos Syndrome

2011 ◽  
Vol 158 (5) ◽  
pp. 826-830.e1 ◽  
Author(s):  
Carrie L. Atzinger ◽  
Richard A. Meyer ◽  
Philip R. Khoury ◽  
Zhiqian Gao ◽  
Brad T. Tinkle
Keyword(s):  
Aortic Root ◽  
Longitudinal Assessment ◽  
Cross Sectional ◽  
Ehlers Danlos Syndrome ◽  
Danlos Syndrome

scholarly journals Aortic Root Dilatation in Children and Adolescents At Al-Hawary General Hospital, & National Benghazi Cardiac Center -Libya

2021 ◽  
Vol 36 (4) ◽  
pp. 300-307
Author(s):  
Rasmia H. Feituri ◽  
Hanan El Megasbi ◽  
Mariam M. El maadani ◽  
Amal Khazm
Keyword(s):  
Aortic Valve ◽  
Children And Adolescents ◽  
Marfan Syndrome ◽  
Aortic Root ◽  
Ehlers Danlos Syndrome ◽  
Aortic Root Dilatation ◽  
Adrenergic Blockers ◽  
Danlos Syndrome ◽  
Cardiac Center

Isolated dilatation of the aortic root and/or ascending aorta is a rare but well-known cardiovascular manifestation, can be caused by a variety of congenital or acquired conditions; that lead to the weakening of the aortic wall. The study aimed to detect the cause and the rate of the aortic root dilatation in children and adolescents, and to assess the effect of the Beta-adrenergic blockers in preventing further dilatation in the aortic root. A case series study was perform with five years of follow-up at Al-Hawary General Hospital, National Benghazi Cardiac Center. A total of 91 patients were seen with ascending aortic dilatation and/or root dilatation during the period from 6/2016 - 6/2021 included in the study diagnosed by clinical examination, chest x-ray, and echocardiogram. The diagnosis in 34/91(37%) was Tetralogy of fallout (TOF) and truncus arteriosus, 57/91 (63%) was dilated aortic root, 25/57 (44%) bicuspid aortic valve (BAV), 22/57 (38.5%) Marfan syndrome, 4/57(7%) Noonan syndrome, 2/57(3.5%) Turner syndrome, 3/57(5%) Ehlers-Danlos syndrome, 1/57(2%) idiopathic. Follow-up results of three months – five years: 57/91 patients with aortic root dilatation were followed up, none of the Marfan syndrome and Ehlers-Danlos syndrome patients who received beta-blockers had shown progression in the dilatation of the aortic root, and all patients who had bicuspid aortic valve did not show any progression in the dilatation without using medication. Conclusions: Dilated aortic root is a common finding in Marfan syndrome, bicuspid aortic root, and Ehlers-Danlos syndrome, and its progress could be decreased by using beta-adrenergic blockers in rapidly progressing dilation.

Natural history of aortic root dilation through young adulthood in a hypermobile Ehlers-Danlos syndrome cohort

2017 ◽  
Vol 173 (6) ◽  
pp. 1467-1472 ◽  
Author(s):  
Alyssa Ritter ◽  
Carrie Atzinger ◽  
Brandon Hays ◽  
Jeanne James ◽  
Amy Shikany ◽  
...  
Keyword(s):  
Natural History ◽  
Young Adulthood ◽  
Aortic Root ◽  
Ehlers Danlos Syndrome ◽  
History Of ◽  
Danlos Syndrome

Ventricular energetics in aortic root replacement for annuloaortic ectasia with aortic regurgitation

2009 ◽  
Vol 24 (1) ◽  
pp. 41-45 ◽  
Author(s):  
Yoshihisa Tanoue ◽  
Yukihiro Tomita ◽  
Shigeki Morita ◽  
Ryuji Tominaga
Keyword(s):  
Aortic Regurgitation ◽  
Aortic Root ◽  
Aortic Root Replacement ◽  
Annuloaortic Ectasia
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