Doty's Method (Two Sinus Reconstructions) of Supravalvular Aortic Stenosis in Williams's Syndrome

2009 ◽  
Vol 2 ◽  
pp. OJCS.S3721
Author(s):  
Osman Tiryakioglu ◽  
Selma Kenar Tiryakioglu ◽  
Hasan Ari ◽  
Hakan Vural ◽  
Ahmet Ozyazicioglu
Keyword(s):  
Aortic Valve ◽  
Aortic Stenosis ◽  
Digital Subtraction Angiography ◽  
Supravalvular Aortic Stenosis ◽  
Digital Subtraction ◽  
Heart Murmur ◽  
Glass Type ◽  
Coronary Obstruction ◽  
Localized Stenosis

We experienced a successful surgical Williams's syndrome case of extended aortoplasty by means of Doty's method (two sinus reconstructions) for congenital supravalvular aortic stenosis. Case was 29-year-old woman, who had no complaint except heart murmur and dyspnea. The retrograde aortography and Digital Subtraction Angiography (DSA) demonstrated localized stenosis just above the aortic valve, and it was an hour-glass type. This case showed excellent results. Doty's aortoplasty was favorable method for supravalvular aortic stenosis without deformity of aortic valve and coronary obstruction.

Surgical Experience with Doty's Repair for Supravalvular Aortic Stenosis

1996 ◽  
Vol 4 (1) ◽  
pp. 29-32
Author(s):  
Balram Airan ◽  
Sunil K Kaushal ◽  
Anil Bhan ◽  
Panangipalli Venugopal
Keyword(s):  
Aortic Valve ◽  
Aortic Stenosis ◽  
Coronary Sinus ◽  
Innominate Artery ◽  
Left Ventricular ◽  
Supravalvular Aortic Stenosis ◽  
Coarctation Of Aorta ◽  
Valve Function ◽  
Aortic Obstruction ◽  
The Right

The surgical treatment of severe supravalvular aortic stenosis by conventional, asymmetrical, one point patch aortoplasty across the narrowed area has been associated with a substantial incidence of residual stenosis and reoperations. Almost symmetrical relief of such stenosis was achieved with Doty's extended aortoplasty in 5 patients in whom left ventricular aortic gradient was reduced from 60–170 nun Hg to 0–25 mm Hg. This technique of inserting an inverted V-shaped gusset across the stenosed segment into the right coronary sinus and non-coronary sinus, restores the aortic root geometry, provides more predictable relief of aortic obstruction and also improves aortic valve function. Associated procedures involved relief of coarctation of aorta and innominate artery stenosis in 1 case and repair of aortic valve and mitral valve in another case.

scholarly journals Diffuse Supravalvular Aortic Stenosis: Surgical Repair in Adulthood

2009 ◽  
Vol 2009 ◽  
pp. 1-3 ◽  
Author(s):  
Giovanni Ferlan ◽  
Claudio De Pasquale ◽  
Concetta Losito ◽  
Annalisa Fiorella ◽  
Nicola Marraudino ◽  
...  
Keyword(s):  
Aortic Valve ◽  
Aortic Stenosis ◽  
Three Dimensional ◽  
Ascending Aorta ◽  
Supravalvular Aortic Stenosis ◽  
Mechanical Prosthesis ◽  
Computed Tomographic ◽  
Valve Function ◽  
Normal Shape

We present the case of a 54-year-old woman in which a diffuse congenital supravalvular aortic stenosis (SVAS) was associated with a severe aortic valve incompetence and heavy calcification of the aortic annulus. Repair consisted in resection of the ascending aorta, patch augmentation of the hypoplastic aortic root and annulus, placement of a 20 mm Dacron tubular graft (Vascutek, Renfrewshire, UK) and aortic valve replacement with a mechanical prosthesis (Sorin, Turin, Italy). Follow-up echocardiography demonstrated normal prosthetic valve function and a postoperative three-dimensional computed tomographic scan showed a normal shape of the reconstructed ascending aorta.

Mild Supravalvular Aortic Stenosis With Left Coronary Obstruction in a Neonate

2005 ◽  
Vol 79 (6) ◽  
pp. 2153-2155 ◽  
Author(s):  
Neville A.G. Solomon ◽  
Kirsten A. Finucane ◽  
Jonathan R. Skinner ◽  
Alan Kerr
Keyword(s):  
Aortic Stenosis ◽  
Supravalvular Aortic Stenosis ◽  
Coronary Obstruction
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