scholarly journals Uncorrected Tetralogy of Fallot in a 25-Year Old Nigerian African

2011 ◽  
Vol 4 ◽  
pp. CCRep.S6805 ◽  
Author(s):  
Dike B. Ojji ◽  
Akinola O. Babalola ◽  
Ayodele O. Falase
Keyword(s):  
Congenital Heart Disease ◽  
Tetralogy Of Fallot ◽  
Congenital Heart ◽  
Ventricular Hypertrophy ◽  
Left Ventricular ◽  
Cyanotic Congenital Heart Disease ◽  
Corrective Surgery ◽  
Mammary Arteries ◽  
Pulmonary Shunting ◽  
Internal Mammary

Tetralogy of Fallot is the most common form of cyanotic congenital heart disease. Survival after the age of 12 years without corrective surgery is rare. We present the case of a 25 year-old man with uncorrected tetralogy of Fallot. Possible reasons for the longetivity in this patient are left ventricular hypertrophy and systemic to pulmonary shunting through internal mammary arteries.

Endothelial function state following repair of cyanotic congenital heart diseases

2013 ◽  
Vol 25 (2) ◽  
pp. 222-227 ◽  
Author(s):  
Mohammad Reza Sabri ◽  
Hooman Daryoushi ◽  
Mojgan Gharipour
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Endothelial Function ◽  
Tetralogy Of Fallot ◽  
Congenital Heart ◽  
Cyanotic Congenital Heart Disease ◽  
Vascular Endothelial ◽  
Vascular Endothelial Function ◽  
Flow Mediated Dilatation ◽  
The Mean

AbstractBackgroundRepairing cyanotic congenital heart disease may be associated with preserving endothelial function. The present study aimed to evaluate vascular endothelial function in patients with repaired cyanotic congenital heart disease.MethodsIn a case–control study conducted in 2012 in Isfahan, Iran, 42 consecutive patients aged <35 years who had suffered from different types of cyanotic congenital heart disease and had undergone complete repair of their congenital heart defect were assessed in regard to their endothelial function state by measuring flow-mediated dilatation and other cardiac function indices. They were paired with 42 sex- and age-matched healthy controls.ResultsThe mean flow-mediated dilatation was lower in patients with repaired cyanotic congenital heart disease than in the controls [6.14±2.78 versus 8.16±1.49 respectively (p<0.001)]. Significant adverse correlations were found between flow-mediated dilatation, age, and body mass indexes, in those who underwent repair surgery. In addition, flow-mediated dilatation had a positive association with the shortening fraction, ejection fraction, and tricuspid annular plane systolic excursion value, and it was also inversely associated with carotid intima-media thickness and the myocardial performance index. The mean of the flow-mediated dilatation was significantly higher in the group with tetralogy of Fallot along with complete repair before the age of 2.5 years and also in those patients with total anomalous pulmonary venous connection or transposition of the great arteries repaired with an arterial switch operation before 6 months of age, compared with the other two subgroups. This includes patients with a tetralogy of Fallot defect repaired after 4 years of age and those with complex cyanotic congenital heart disease that was repaired after 2.5 years of age (mean age at repair 9±6.1 years).ConclusionEarly repair of a cyanotic defect can result in the protection of vascular endothelial function and prevent the occurrence of vascular accidents at an older age.

scholarly journals Recurrent cerebral abscess in tetralogy of Fallot

2016 ◽  
Vol 44 (5) ◽  
pp. 206
Author(s):  
Wanty Sahli ◽  
J M Ch Pelupessy
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Ventricular Septal Defect ◽  
Right Ventricular ◽  
Tetralogy Of Fallot ◽  
Congenital Heart ◽  
Ventricular Hypertrophy ◽  
Septal Defect ◽  
Pulmonary Stenosis ◽  
Cerebral Abscess

Tetralogy of Fallot (TF) classically consistsof the combination of right ventricularoutflow obstruction (pulmonary stenosis),ventricular septal defect (VSD), overridingaorta, and right ventricular hypertrophy. Thedegree of pulmonary stenosis and VSD determine thevariety of clinical manifestations.This type of congenital heart disease accountsfor about 10% of all congenital cardiac deformitiesand is the most common cyanotic lesion after thefirst year of life. Cerebral abscess is a serious com-plication in TF and is usually seen after the age of 2years.

SPECIAL ARTICLE

PEDIATRICS ◽  
1956 ◽  
Vol 17 (1) ◽  
pp. 93-103
Author(s):  
Samuel O. Sapin ◽  
Ephraim Donoso ◽  
Eugene Braunwald ◽  
Arthur Grishman
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Left Ventricular Hypertrophy ◽  
Right Ventricular ◽  
Congenital Heart ◽  
Ventricular Hypertrophy ◽  
Left Ventricular ◽  
Right Ventricular Hypertrophy ◽  
Diagnostic Tools

Vectorcardiography is a method of graphically registering the total electrical activity of the heart and presents this in 3 dimensions. The technique of obtaining vectorcardiograms and the determination of the electrocardiogram from the vector loop are discussed in a simplified manner. The characteristics of normal and abnormal vectorcardiograms in infants, children and adults are presented. Electrocardiograms in different conditions, e.g. conduction delay, right ventricular hypertrophy and normal variants may be indistinguishable, particularly in infancy. However, the vectorcardiogram clearly differentiates these entities. The diagnostic accuracy of the electrocardiogram and vectorcardiogram was compared in a series of patients with unilateral ventricular hypertrophy due to congenital heart disease. The vectorcardiogram was superior to the electrocardiogram in diagnosing unilateral right ventricular hypertrophy as well as left ventricular hypertrophy. However, both the electrocardiogram and the vectorcardiogram are of greater value in detecting right than left ventricular hypertrophy. The absence of right ventricular hypertrophy in the vectorcardiogram militates strongly against the existence of predominant right ventricular hypertrophy. Axis deviation in the standard leads as a result of the vectorcardiographic studies is considered to be of little diagnostic importance. The chief contribution of the vectorcardiogram in congenital heart disease is in the determination of the type of predominant ventricular hypertrophy and this renders it a most valuable addition to the diagnostic tools available in this field.

Pregnancy Management in a Parturient with Tetralogy of Fallot

2018 ◽  
pp. 257-266
Author(s):  
Yi Deng ◽  
Shobana Murugan
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Life Expectancy ◽  
Tetralogy Of Fallot ◽  
Lower Risk ◽  
Congenital Heart ◽  
Cyanotic Congenital Heart Disease ◽  
Cardiovascular Changes ◽  
The Past

Tetralogy of Fallot (ToF) is the most prevalent cyanotic congenital heart disease (CHD) at birth and is also the most common repaired cyanotic CHD encountered as an adult. Over the past several decades surgical improvement has made great strides in lowering morbidity/mortality and extending life expectancy of these patients, and most will reach adulthood and achieve pregnancy. Management of a parturient with either repaired or unrepaired ToF must be individualized and requires thorough workup and participation from multiple disciplines, but overall outcomes can be excellent with lower risk to mother and fetus compared to other types of cyanotic CHD. Because many parturients with repaired ToF have clinically silent disease until late, it is imperative for anesthesiologists to familiarize themselves with potential complications and pitfalls regarding cardiovascular changes during pregnancy and how they affect peripartum CHD management.

scholarly journals Trans-atrial, Trans-pulmonary Repair of Tetralogy of Fallot in Older Children and Adults:

2004 ◽  
Vol 3 (3) ◽  
pp. 67
Author(s):  
B Koirala ◽  
R Koirala ◽  
J Sharma ◽  
S Pradhan ◽  
A Acharya ◽  
...  
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Retrospective Study ◽  
Tetralogy Of Fallot ◽  
Congenital Heart ◽  
Surgical Repair ◽  
Cyanotic Congenital Heart Disease ◽  
Favorable Outcome ◽  
Older Children ◽  
National Heart

Tetralogy of Fallot is the most common cyanotic congenital heart disease and has an favorable outcome if dealt with in time. Here we present the retrospective study of immediate outcome of surgical repair of Fallot's Tetralogy carried out at Shahid Gangalal National Heart Centre, Kathmandu, Nepal.

Sign in / Sign up

Export Citation Format

Share Document