scholarly journals Mesenteric malignant peripheral nerve sheath tumor in a patient with von Recklinghausen's disease. Report of a case.

2001 ◽  
Vol 62 (6) ◽  
pp. 1534-1537 ◽  
Author(s):  
Yuichiro OTSUKA ◽  
Hironori KANEKO ◽  
Takashi ISHII ◽  
Masaaki YOSHINO ◽  
Tadaaki SIBA ◽  
...  
1989 ◽  
Vol 79 (6) ◽  
pp. 293-294 ◽  
Author(s):  
JF Pace ◽  
FA Spinosa

Schwannoma is a relatively uncommon tumor of the nerve sheath and is rare in the foot. The lesion is almost always benign, but when a major nerve is involved, parasthesia and anesthesia may result. In addition, the unlikely appearance of multiple schwannoma may signal the onset of von Recklinghausen's disease.


2004 ◽  
Vol 43 (154) ◽  
Author(s):  
Salamat Khan ◽  
A Chandra ◽  
N Jain ◽  
A Kumar ◽  
I U Khan

Von Recklinghausen's disease (VRD) is a rare genetic autosomal dominant disorder that affects the ectodermaltissues (nerve and skin). The cardinal features of this disorder are spots of increase pigmentation (cafe-au-lait spot, CAL), peripheral nerve tumours (neurofibromatosis) and iris hamartoma (Lisch nodule). Clinicaldiagnosis of VRD is based on the criteria given by National Institute of Health (NIH) because the mutationanalysis is laborious. Here, we are reporting a case of a family with VRD.Key Words: VonRecklinghausen's disease (VRD), Cafe-au-lait (CAL) spot, Lisch nodule,Neurofibromatosis (NF)


Sign in / Sign up

Export Citation Format

Share Document