scholarly journals Monosotic fibrous dysplasia and solitary intramuscular myxoma of the head and neck: A unique presentation of Mazabraud's syndrome and a literature review

2015 ◽  
Vol 10 (5) ◽  
pp. 3087-3094 ◽  
Author(s):  
SHUITING FU ◽  
ZHUOWEI TIAN ◽  
CHENPING ZHANG ◽  
YUE HE
Keyword(s):  
Literature Review ◽  
Head And Neck ◽  
Fibrous Dysplasia ◽  
Intramuscular Myxoma ◽  
Mazabraud’S Syndrome

Intramuscular Myxoma and fibrous dysplasia of bone — Mazabraud's syndrome

1997 ◽  
Vol 38 (3) ◽  
pp. 368-371 ◽  
Author(s):  
M. Court-Payen ◽  
L. Ingemann Jensen ◽  
B. Bjerregaard ◽  
G. Schwarz Lausten ◽  
B. Skjoldbye
Keyword(s):  
Fibrous Dysplasia ◽  
Intramuscular Myxoma ◽  
Mazabraud’S Syndrome ◽  
Fibrous Dysplasia Of Bone

Fibrous Dysplasia Associated with Intramuscular Myxoma(Mazabraud's Syndrome): A Case Report

1999 ◽  
Vol 40 (5) ◽  
pp. 975
Author(s):  
Kyung Ah Chun ◽  
Ki Tae Kim ◽  
Young Joo Kim ◽  
Lee So Maeng ◽  
Eun Jung Lee
Keyword(s):  
Case Report ◽  
Fibrous Dysplasia ◽  
Intramuscular Myxoma ◽  
Mazabraud’S Syndrome

Mazabraud’s syndrome: Intramuscular myxoma associated with fibrous dysplasia

2004 ◽  
Vol 10 (2) ◽  
pp. 121-123 ◽  
Author(s):  
Fevziye Kabukcuoglu ◽  
Yavuz Kabukcuoglu ◽  
Banu Yilmaz ◽  
Yesim Erdem ◽  
Ismail Evren
Keyword(s):  
Fibrous Dysplasia ◽  
Intramuscular Myxoma ◽  
Mazabraud’S Syndrome

Intramuscular Myxoma and fibrous dysplasia of bone — Mazabraud's syndrome

1997 ◽  
Vol 38 (3) ◽  
pp. 368-371 ◽  
Author(s):  
M. Court-Payen ◽  
L. Ingemann Jensen ◽  
B. Bjerregaard ◽  
G. Schwarz Lausten ◽  
B. Skjoldbye
Keyword(s):  
Fibrous Dysplasia ◽  
Intramuscular Myxoma ◽  
Mazabraud’S Syndrome ◽  
Fibrous Dysplasia Of Bone

Solitary intramuscular myxoma with monostotic fibrous dysplasia as a rare variant of Mazabraud’s syndrome

2007 ◽  
Vol 36 (6) ◽  
pp. 523-529 ◽  
Author(s):  
Makoto Endo ◽  
Akira Kawai ◽  
Eisuke Kobayashi ◽  
Yuki Morimoto ◽  
Umio Yamaguchi ◽  
...  
Keyword(s):  
Fibrous Dysplasia ◽  
Rare Variant ◽  
Intramuscular Myxoma ◽  
Mazabraud’S Syndrome

scholarly journals Mazabraud's Syndrome: A Case Report and Up-To-Date Literature Review

2019 ◽  
Vol 19 (6) ◽  
pp. 885-893 ◽  
Author(s):  
Fabio Vescini ◽  
Alberto Falchetti ◽  
Veronica Tonelli ◽  
Maria Carpentieri ◽  
Claudia Cipri ◽  
...  
Keyword(s):  
Case Report ◽  
Zoledronic Acid ◽  
Fibrous Dysplasia ◽  
Quadriceps Muscle ◽  
Intramuscular Myxoma ◽  
Rare Form ◽  
Promising Alternative ◽  
Acid Therapy ◽  
Mazabraud’S Syndrome ◽  
Long Term Treatment

Objective: Mazabraud's syndrome is a rare form of bone fibrous dysplasia associated with intramuscular myxomas. Fibrous dysplasia, is generally localized to pelvis and femur and it results in a fragile bone with deformities, pain, pathological fractures and functional impairment. Intramuscular myxomas, are rare benign mesenchymal neoplasms that exceptionally may evolve to malignant forms. Methods: This case report describes a 66-year-old woman with Mazabraud’s Syndrome (MS), characterized both by monostotic right femur fibrous dysplasia and by a solitary intramuscular myxoma at the right quadriceps muscle, that underwent a long-term treatment (4 years) with intravenous zoledronic acid. Results: Zoledronic acid therapy rapidly lowered bone pain together with a reduction of intramuscular myxoma volume, but did not affect the extension of fibrous dysplasia. No adverse effects have been observed during treatment. Conclusion: Highly active bisphosphonates are commonly used for the treatment of bone metabolic disorders and they are generally well tolerated. Zoledronic acid may represent a promising alternative to surgical intervention in MS, although its use in rare form of bone fibrous dysplasias is still controversial.

Tophaceous gout presenting as a dorsal nasal lump

2005 ◽  
Vol 119 (6) ◽  
pp. 492-494 ◽  
Author(s):  
J P Hughes ◽  
Silvana Di Palma ◽  
J Rowe-Jones
Keyword(s):  
Literature Review ◽  
Head And Neck ◽  
Soft Tissues ◽  
Neck Region ◽  
Endoscopic Technique ◽  
Tophaceous Gout ◽  
Head And Neck Region ◽  
Nasal Bones ◽  
Aesthetic Rhinoplasty ◽  
Emergency Tracheotomy

A literature review reveals that gout has been described as affecting many sites in the head and neck region, both in the arthritic and tophaceous form. Gout can often mimic malignancy or infection, and has been described as causing acute airway problems requiring emergency tracheotomy. Here we describe the first published case of tophaceous gout affecting the soft tissues overlying the nasal bones. The patient presented with a bony, hard, dorsal hump and requested aesthetic rhinoplasty.We also describe an endoscopic technique for removal of tophi using a powered microdebrider system with a protected burr head. Endoscopic powered microdebrider blade excision of tophi affecting the limbs has already been described, with reduced complications when compared with conventional curettage and debridement techniques. This is the first such application to the nose.

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