scholarly journals Symptoms, Audiometric and Vestibular Laboratory Findings, and Imaging in a Concurrent Superior Canal Dehiscence Syndrome and Vestibular Schwannoma: A Case Report

2020 ◽  
Vol 31 (01) ◽  
pp. 076-082
Author(s):  
Doug Garrison ◽  
Laura Barth ◽  
David Kaylie ◽  
Kristal Riska
Keyword(s):  
Hearing Loss ◽  
Case Report ◽  
Vestibular Schwannoma ◽  
The Body ◽  
Vestibular Evoked Myogenic Potentials ◽  
Laboratory Findings ◽  
Superior Canal Dehiscence ◽  
Vestibular Tests ◽  
Imaging Results ◽  
Canal Dehiscence

AbstractDizziness is a common complaint that can arise from multiple systems in the body. Objective vestibular tests are used to understand the underlying function of the vestibular system and whether or not it may be contributing to the dizziness symptoms experienced by the patient. Even when comprehensive case history is consistent with an otologic etiology, audiometric and vestibular tests are ordered to objectively characterize inner ear function to help further refine the differential diagnoses and aid in guiding treatment options. Few reports in the literature describe audiometric and vestibular results in patients with multiple concurrent otologic etiologies.This case provides a description of audiometric, vestibular, and imaging results in a case of concurrent bilateral superior canal dehiscence, right-sided vestibular schwannoma, and right-sided posterior canal benign paroxysmal positional vertigo. The patient’s symptoms and laboratory findings are described in detail and, where appropriate, highlight challenges that may arise in interpretation.A case report.The patient presented for evaluation of dizziness, asymmetric hearing loss, and autophony. Comprehensive audiometric evaluation shows asymmetric sensorineural hearing loss and an air-bone gap at 250 Hz in the right ear. Vestibular evaluation shows right caloric asymmetry along with abnormal cervical vestibular– and ocular vestibular–evoked myogenic potentials, with the left ear showing results consistent with the third-window pathology.Comprehensive assessment of symptoms and critical thinking while performing testing are necessary when examining multiple concurrent otologic etiologies in a patient. Knowledge of anticipated test results and physiology may help the audiologist to synthesize results and make appropriate clinical recommendations as part of the multidisciplinary team.

Bilateral superior semicircular canal dehiscence: bilateral conductive hearing loss with subtle vestibular symptoms

2020 ◽  
Vol 13 (3) ◽  
pp. e233042
Author(s):  
Diogo Pereira ◽  
Abílio Leonardo ◽  
Delfim Duarte ◽  
Nuno Oliveira
Keyword(s):  
Hearing Loss ◽  
Semicircular Canal ◽  
Conductive Hearing Loss ◽  
Vestibular Evoked Myogenic Potentials ◽  
Caucasian Woman ◽  
Superior Semicircular Canal Dehiscence ◽  
Superior Semicircular Canal ◽  
Vestibular Symptoms ◽  
Conductive Hearing ◽  
Canal Dehiscence

Superior semicircular canal dehiscence is caused by a bone defect on the roof of the superior semicircular canal. The estimated prevalence when unilateral varies between 0.4% and 0.7% and is still unknown when bilateral. Patients may present with audiologic and vestibular symptoms that may vary from asymptomatic to disabling. We report a case of a 72-year-old Caucasian woman presented to otolaryngology department reporting imbalance, bilateral pulsatile tinnitus, hypoacusis while being very sensitive to certain sounds. Physical examination was unremarkable, except for the Rinne test that was negative in both sides. The patient underwent an audiometry revealing a mild bilateral conductive hearing loss. A temporal bone CT scan was performed which evidenced bilateral superior semicircular canal dehiscence. Cervical vestibular evoked myogenic potentials and electrocochleography confirmed diagnosis. Although rare, superior semicircular canal dehiscence shall be considered in conductive hearing loss with vestibular symptoms.

Ocular vestibular evoked myogenic potentials (OVEMPs) in superior canal dehiscence

2008 ◽  
Vol 119 (3) ◽  
pp. e23-e24
Author(s):  
S.M. Rosengren ◽  
S.T. Aw ◽  
G.M. Halmagyi ◽  
N.P.M. Todd ◽  
J.G. Colebatch
Keyword(s):  
Vestibular Evoked Myogenic Potentials ◽  
Superior Canal Dehiscence ◽  
Canal Dehiscence

Vestibular-Evoked Myogenic Potential Testing in Vestibular Localization and Diagnosis

2020 ◽  
Vol 40 (01) ◽  
pp. 018-032 ◽  
Author(s):  
Rachael L. Taylor ◽  
Miriam S. Welgampola ◽  
Benjamin Nham ◽  
Sally M. Rosengren
Keyword(s):  
Vestibular System ◽  
Vestibular Evoked Myogenic Potentials ◽  
Vestibular Disorders ◽  
Complementary Information ◽  
Vestibular Evoked Myogenic Potential ◽  
Myogenic Potential ◽  
Superior Canal Dehiscence ◽  
Otolith Function ◽  
Utricular Function ◽  
Canal Dehiscence

AbstractVestibular-evoked myogenic potentials (VEMPs) are short-latency, otolith-dependent reflexes recorded from the neck and eye muscles. They are widely used in neuro-otology clinics as tests of otolith function. Cervical VEMPs are recorded from the neck muscles and reflect predominantly saccular function, while ocular VEMPs are reflexes of the extraocular muscles and reflect utricular function. They have an important role in the diagnosis of superior canal dehiscence syndrome and provide complementary information about otolith function that is useful in the diagnosis of other vestibular disorders. Like other evoked potentials, they can provide important localizing information about lesions that may occur along the VEMP pathway. This review will describe the VEMP abnormalities seen in common disorders of the vestibular system and its pathways.

P70-F Vestibular-evoked myogenic potentials for the diagnosis of superior canal dehiscence syndrome

2019 ◽  
Vol 130 (7) ◽  
pp. e87
Author(s):  
Esmeralda Rocío Martín ◽  
Rybel Wix ◽  
Salvador Delis Gómez ◽  
Marleny Macario ◽  
Jesús Pastor Gómez
Keyword(s):  
Vestibular Evoked Myogenic Potentials ◽  
Superior Canal Dehiscence ◽  
Canal Dehiscence

scholarly journals Assessment of the Effects of Superior Canal Dehiscence Location and Size on Intracochlear Sound Pressures

2014 ◽  
Vol 20 (1) ◽  
pp. 62-71 ◽  
Author(s):  
Marlien E.F. Niesten ◽  
Christof Stieger ◽  
Daniel J. Lee ◽  
Julie P. Merchant ◽  
Wilko Grolman ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Temporal Bone ◽  
Semicircular Canal ◽  
Low Frequency ◽  
Low Frequencies ◽  
Superior Canal Dehiscence ◽  
Superior Semicircular Canal ◽  
Wide Range ◽  
Before And After ◽  
Canal Dehiscence

Superior canal dehiscence (SCD) is a defect in the bony covering of the superior semicircular canal. Patients with SCD present with a wide range of symptoms, including hearing loss, yet it is unknown whether hearing is affected by parameters such as the location of the SCD. Our previous human cadaveric temporal bone study, utilizing intracochlear pressure measurements, generally showed that an increase in dehiscence size caused a low-frequency monotonic decrease in the cochlear drive across the partition, consistent with increased hearing loss. This previous study was limited to SCD sizes including and smaller than 2 mm long and 0.7 mm wide. However, the effects of larger SCDs (>2 mm long) were not studied, although larger SCDs are seen in many patients. Therefore, to answer the effect of parameters that have not been studied, this present study assessed the effect of SCD location and the effect of large-sized SCDs (>2 mm long) on intracochlear pressures. We used simultaneous measurements of sound pressures in the scala vestibuli and scala tympani at the base of the cochlea to determine the sound pressure difference across the cochlear partition - a measure of the cochlear drive in a temporal bone preparation - allowing for assessment of hearing loss. We measured the cochlear drive before and after SCDs were made at different locations (e.g. closer to the ampulla of the superior semicircular canal or closer to the common crus) and for different dehiscence sizes (including larger than 2 mm long and 0.7 mm wide). Our measurements suggest the following: (1) different SCD locations result in similar cochlear drive and (2) larger SCDs produce larger decreases in cochlear drive at low frequencies. However, the effect of SCD size seems to saturate as the size increases above 2-3 mm long and 0.7 mm wide. Although the monotonic effect was generally consistent across ears, the quantitative amount of change in cochlear drive due to dehiscence size varied across ears. Additionally, the size of the dehiscence above which the effect on hearing saturated varied across ears. These findings show that the location of the SCD does not generally influence the amount of hearing loss and that SCD size can help explain some of the variability of hearing loss in patients. i 2014 S. Karger AG, Basel

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