scholarly journals A COUGH IN A PATIENT WITH CHOLANGITIS IN THE COURSE OF CAROLI’S DISEASE. CASE REPORT

2019 ◽  
Vol 72 (2) ◽  
pp. 294-297
Author(s):  
Aleksandra Kaszyńska ◽  
Tadeusz M. Zielonka ◽  
Katarzyna Życińska
Keyword(s):  
Digestive System ◽  
Underlying Disease ◽  
Infectious Complications ◽  
Acute Cough ◽  
Rapid Improvement ◽  
Caroli's Disease ◽  
Caroli’S Disease ◽  
Intrahepatic Bile Ducts ◽  
Liver Abscesses ◽  
Disease Case

Cough may be a manifestation of pulmonary and extra-pulmonary diseases. However, rarely liver disease is suspected as a cause of acute cough. A case of a 34-year-old patient with diagnosed Caroli’s disease has been described, in which cough with fever was the main manifestation of cholangitis in the course of complications of the underlying disease. Caroli’s disease is a congenital pathology of intrahepatic bile ducts, causing their cysts to widen. It usually has an asymptomatic course, however it promotes infectious complications such as liver abscesses and recurrent cholangitis. The patient was admitted to the ward because of high fever and cough, without any symptoms from the digestive system. On the basis of laboratory, microbiological and visual examinations, various causes of cough were excluded and a diagnosis of cholangitis was made. After appropriate antibiotic therapy, a rapid improvement in the clinical condition and resolution of symptoms was achieved.

scholarly journals Diffuse Oligosymptomatic Caroli’s Disease: Case Report

2020 ◽  
Vol 31 (2) ◽  
pp. 107-110
Author(s):  
Lemfadli Y ◽  
Bouchrit S ◽  
Ait Errami A ◽  
Oubaha S ◽  
Samlani Z ◽  
...  
Keyword(s):  
Case Report ◽  
Female Patient ◽  
Bile Ducts ◽  
Clinical Case ◽  
Caroli's Disease ◽  
Caroli’S Disease ◽  
Caroli Disease ◽  
Intrahepatic Bile Ducts ◽  
Disease Case

This article describes a case of Caroli’s disease in a 53-year-old female patient who complained nonspecificabdominal pain without cholestasis or cholangitis. Ultrasound and hepatic magnetic resonanceimaging showed segmental saccular dilations connected to intrahepatic bile ducts without hepaticfibrosis. This clinical case shows the possibility of having oligosymptomatic forms in the diffuse formsof Caroli disease, therefore the interest to consider this diagnosis in case of non-specific abdominalsigns and to request a hepatic ultrasound. Bangladesh J Medicine July 2020; 31(2) : 107-110

scholarly journals Caroli’s disease complicated by liver abscesses

2012 ◽  
Vol 6 ◽  
pp. 397-400
Author(s):  
Maciej Krasnodębski ◽  
Łukasz Masior ◽  
Piotr Hevelke ◽  
Mariusz Frączek
Keyword(s):  
Caroli's Disease ◽  
Caroli’S Disease ◽  
Liver Abscesses

scholarly journals Caroli’s disease: a diagnostic challenge

2018 ◽  
Vol 5 (11) ◽  
pp. 3750
Author(s):  
Padmini Yadav ◽  
Shailesh Adhikari ◽  
Narendra Pandit ◽  
Lalijen Awale ◽  
Keerthi Vasan ◽  
...  
Keyword(s):  
Bile Duct ◽  
Open Cholecystectomy ◽  
Poor Performance ◽  
Left Lobe ◽  
Tube Placement ◽  
Diagnostic Challenge ◽  
Caroli's Disease ◽  
Caroli’S Disease ◽  
T Tube ◽  
Intrahepatic Bile Ducts

Caroli’s disease is a rare congenital hepatobiliary disease characterized by multifocal segmental dilatation of intrahepatic bile ducts affecting all or parts of the liver. It predisposes to biliary stasis and consequent lithiasis, cholangitis, abscesses, and septicemia. Sometimes it is difficult to diagnose and differentiate it from other similar disease conditions. 60-year-old female presented with features of recurrent cholangitis with hepatolithiasis and multiple cyst in liver, cholelithiasis was planned for cholecystectomy and drainage procedure. Patient underwent open cholecystectomy with common bile duct (CBD) exploration with T-tube placement due to intraoperative instability. Post-operative T tube cholangiogram was done. Post-operative T tube cholangiogram showed bilobar major duct cystic dilatation with predominant left lobe involvement, with few cysts containing calculi. Patient was planned for left hepatectomy with bile duct excision but patient refused to undergo aforementioned surgery. Therefore ERCP and sphincterotomy was done in view of poor performance status.Caroli’s disease being a rare disease is sometimes difficult to diagnose and treat in an old age patient with bilobar involvement and poor general conditions.

Congenital Dilatation of the Intrahepatic Bile Ducts (Caroli's Disease)

Radiology ◽  
1978 ◽  
Vol 127 (3) ◽  
pp. 746-746 ◽  
Author(s):  
Javier Lucaya ◽  
Jose Luis Gomez ◽  
Ceferino Molino ◽  
Juan Gonzalez Atienza
Keyword(s):  
Bile Ducts ◽  
Caroli's Disease ◽  
Caroli’S Disease ◽  
Intrahepatic Bile Ducts

scholarly journals Caroli's disease (clinical observation)

2021 ◽  
Vol 13 (3) ◽  
pp. 150-152
Author(s):  
G. G. Kuttykuzhanova ◽  
A. Zh. Tanirbergenova ◽  
S. Zh. Abdirazakova ◽  
Z. Zh. Urikbaeva
Keyword(s):  
Early Diagnosis ◽  
Rare Diseases ◽  
Medical Practice ◽  
Bile Ducts ◽  
Clinical Observation ◽  
Diagnostic Methods ◽  
Caroli's Disease ◽  
Caroli’S Disease ◽  
Intrahepatic Stones ◽  
Intrahepatic Bile Ducts

In their medical practice doctors deal with rare diseases which present difficulties in making a clinical diagnosis, in this case additional diagnostic methods are required. One of these diseases is Caroli's disease (syndrome), characterized by cystic enlargement of the intrahepatic bile ducts with frequent formation of intrahepatic stones. Taking into account the difficulties of early diagnosis, we present our own observation.

scholarly journals Congenital dilatation of the large and segmental intrahepatic bile ducts (Caroli's disease) in two Golden retriever littermates : clinical communication

2006 ◽  
Vol 77 (4) ◽  
Author(s):  
R.D. Last ◽  
J.M. Hill ◽  
M. Roach ◽  
T. Kaldenberg
Keyword(s):  
Bile Ducts ◽  
Autosomal Recessive ◽  
Autosomal Recessive Inheritance ◽  
Golden Retriever ◽  
Portal Fibrosis ◽  
Clinical Communication ◽  
Caroli's Disease ◽  
Caroli’S Disease ◽  
Intrahepatic Bile Ducts ◽  
Collecting Ducts

Two, sibling, male Golden retriever puppies, 13 weeks of age, were presented with congenital biliary cysts of the liver involving both hepatic and segmental bile ducts, as well as bilateral polycystic kidney disease. Ultrasonography of the livers of both pups demonstrated segmental cystic lesions that were contiguous with the bile ducts. Histopathology revealed cystic ectatic bile duct hyperplasia and dysplasia with variable portal fibrosis in the liver, while in the kidneys there were radially arranged, cylindrically dilated cysts of the collecting ducts, which extended through the medulla and cortex. This pathology was compatible with that of congenital dilatation of the large and segmental bile ducts (Caroli's disease) described in humans, dogs and rats. In humans Caroli's disease has an autosomal recessive inheritance pattern, while in rats activation of the MEK5/ERK cascade initiates the biliary dysgenesis of Caroli's disease in this species. However, the exact mode of inheritance and pathogenesis of Caroli's disease in dogs is as yet unknown. Previous reports on congenital hepatic cystic diseases of the dog have described Caroli's disease like lesions in various breeds, but these are believed to be the 1st reported cases in the Golden retriever breed.

scholarly journals Diffuse oligosymptomatic Caroli’s disease: Case report

2020 ◽  
pp. 064-066
Author(s):  
Y Lemfadli ◽  
S Bouchrit ◽  
Lairani Fatimezzhara ◽  
A Ait Errami ◽  
S Oubaha ◽  
...  
Keyword(s):  
Case Report ◽  
Caroli's Disease ◽  
Caroli’S Disease ◽  
Disease Case
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