scholarly journals Practical Recommendations for Diagnosis and Management of Respiratory Muscle Weakness in Late-Onset Pompe Disease

2016 ◽  
Vol 17 (10) ◽  
pp. 1735 ◽  
Author(s):  
Matthias Boentert ◽  
Hélène Prigent ◽  
Katalin Várdi ◽  
Harrison Jones ◽  
Uwe Mellies ◽  
...  
Keyword(s):  
Muscle Weakness ◽  
Pompe Disease ◽  
Respiratory Muscle ◽  
Late Onset ◽  
Respiratory Muscle Weakness ◽  
Diagnosis And Management ◽  
Practical Recommendations

The nature of respiratory muscle weakness in patients with late-onset Pompe disease

2019 ◽  
Vol 29 (8) ◽  
pp. 618-627 ◽  
Author(s):  
Jens Spiesshoefer ◽  
Carolin Henke ◽  
Hans Joachim Kabitz ◽  
Tobias Brix ◽  
Dennis Görlich ◽  
...  
Keyword(s):  
Muscle Weakness ◽  
Pompe Disease ◽  
Respiratory Muscle ◽  
Late Onset ◽  
Respiratory Muscle Weakness

The nature of respiratory muscle weakness in patients with late-onset-pompe disease

2020 ◽  
Author(s):  
J Spießhöfer ◽  
HJ Kabitz ◽  
SD Herkenrath ◽  
WJ Randerath ◽  
P Young ◽  
...  
Keyword(s):  
Muscle Weakness ◽  
Pompe Disease ◽  
Respiratory Muscle ◽  
Late Onset ◽  
Respiratory Muscle Weakness

Effects of respiratory muscle training (RMT) in children with infantile-onset Pompe disease and respiratory muscle weakness

2014 ◽  
Vol 7 (3) ◽  
pp. 255-265 ◽  
Author(s):  
Harrison N. Jones ◽  
Kelly D. Crisp ◽  
Tronda Moss ◽  
Katherine Strollo ◽  
Randy Robey ◽  
...  
Keyword(s):  
Muscle Weakness ◽  
Pompe Disease ◽  
Respiratory Muscle ◽  
Respiratory Muscle Training ◽  
Muscle Training ◽  
Respiratory Muscle Weakness

scholarly journals Respiratory Muscle Weakness as a Risk Factor for Pneumonia in Older People

Gerontology ◽  
2021 ◽  
pp. 1-10
Author(s):  
Tatsuma Okazaki ◽  
Yoshimi Suzukamo ◽  
Midori Miyatake ◽  
Riyo Komatsu ◽  
Masahiro Yaekashiwa ◽  
...  
Keyword(s):  
Risk Factor ◽  
Muscle Strength ◽  
Older People ◽  
Serum Albumin ◽  
Muscle Mass ◽  
Muscle Weakness ◽  
Fat Mass ◽  
Respiratory Muscle ◽  
Respiratory Muscle Strength ◽  
Respiratory Muscle Weakness

Introduction: The respiratory muscle strength regulates the effectiveness of coughing, which clears the airways and protects people from pneumonia. Sarcopenia is an aging-related loss of muscle mass and function, the worsening of which is associated with malnutrition. The loss of respiratory and swallowing muscle strength occurs with aging, but its effect on pneumonia is unclear. This study aimed to determine the risks of respiratory muscle weakness on the onset and relapse of pneumonia in older people in conjunction with other muscle-related factors such as malnutrition. Methods: We conducted a longitudinal study with 47 pneumonia inpatients and 35 non-pneumonia controls aged 70 years and older. We evaluated the strength of respiratory and swallowing muscles, muscle mass, and malnutrition (assessed by serum albumin levels and somatic fat) during admission and confirmed pneumonia relapse within 6 months. The maximal inspiratory and expiratory pressures determined the respiratory muscle strength. Swallowing muscle strength was evaluated by tongue pressure. Bioelectrical impedance analysis was used to evaluate the muscle and fat mass. Results: The respiratory muscle strength, body trunk muscle mass, serum albumin level, somatic fat mass, and tongue pressure were significantly lower in pneumonia patients than in controls. Risk factors for the onset of pneumonia were low inspiratory respiratory muscle strength (odds ratio [OR], 6.85; 95% confidence interval [CI], 1.56–30.11), low body trunk muscle mass divided by height2 (OR, 6.86; 95% CI, 1.49–31.65), and low serum albumin level (OR, 5.46; 95% CI, 1.51–19.79). For the relapse of pneumonia, low somatic fat mass divided by height2 was a risk factor (OR, 20.10; 95% CI, 2.10–192.42). Discussion/Conclusions: Respiratory muscle weakness, lower body trunk muscle mass, and malnutrition were risk factors for the onset of pneumonia in older people. For the relapse of pneumonia, malnutrition was a risk factor.

Lambert Eaton Syndrome: A Unique Presentation of the Disease With Isolated Respiratory Muscle Weakness

CHEST Journal ◽  
2013 ◽  
Vol 144 (4) ◽  
pp. 326A
Author(s):  
Urooj Fatima ◽  
Tasneem Shah ◽  
Paras Dedhia ◽  
Muhammad Ebrahim Khan ◽  
Sean Devine
Keyword(s):  
Muscle Weakness ◽  
Respiratory Muscle ◽  
Respiratory Muscle Weakness

Respiratory Muscle Weakness in Patients with Heart Failure with Preserved Ejection Fraction

2014 ◽  
Vol 20 (10) ◽  
pp. S136
Author(s):  
Yoshiharu Kinugasa ◽  
Kensaku Yamada ◽  
Takeshi Sota ◽  
Mari Miyaki ◽  
Shinobu Sugihara ◽  
...  
Keyword(s):  
Heart Failure ◽  
Ejection Fraction ◽  
Muscle Weakness ◽  
Respiratory Muscle ◽  
Preserved Ejection Fraction ◽  
Respiratory Muscle Weakness ◽  
Patients With Heart Failure

Intermittent Positive Pressure Breathing in Patients with Respiratory Muscle Weakness

CHEST Journal ◽  
1986 ◽  
Vol 90 (4) ◽  
pp. 546-552 ◽  
Author(s):  
F. Dennis McCool ◽  
Raymond F. Mayewski ◽  
David S. Shayne ◽  
Charles J. Gibson ◽  
Robert C. Griggs ◽  
...  
Keyword(s):  
Muscle Weakness ◽  
Respiratory Muscle ◽  
Positive Pressure ◽  
Respiratory Muscle Weakness ◽  
Intermittent Positive Pressure Breathing

Respiratory muscle weakness and inefficient ventilation in heart failure due to light-chain amyloidosis

Amyloid ◽  
2008 ◽  
Vol 15 (2) ◽  
pp. 129-136
Author(s):  
Arnt V. Kristen ◽  
Thomas J. Dengler ◽  
J. H. Kristen ◽  
Stefan O. Schonland ◽  
Ute Hegenbart ◽  
...  
Keyword(s):  
Heart Failure ◽  
Muscle Weakness ◽  
Light Chain ◽  
Respiratory Muscle ◽  
Respiratory Muscle Weakness ◽  
Light Chain Amyloidosis

Respiratory problems in neuromuscular disease

2007 ◽  
pp. 237-240
Keyword(s):  
Muscle Weakness ◽  
Neuromuscular Disease ◽  
Respiratory Muscle ◽  
Neuromuscular Disorders ◽  
Respiratory Muscle Weakness ◽  
Respiratory Problems ◽  
Alveolar Hypoventilation ◽  
Ventilatory Failure ◽  
End Stage

Introduction 238 Assessment 239 Treatment 240 A variety of neuromuscular disorders may affect the ventilatory pump at different sites (Table 37.1). Most of these disorders result in respiratory muscle weakness, which results in alveolar hypoventilation and impaired cough. Patients with known neuromuscular disease may present acutely with a presentation related to their underlying neuromuscular disease (such as infection) or occasionally in end-stage ventilatory failure....

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