scholarly journals Case Report: A Rare Case of Right-Sided Papillary Fibroelastoma in a 1-Year-Old With Congenital Heart Disease

2021 ◽  
Vol 7 ◽  
Author(s):  
Ali Ahmad ◽  
Edward A. El-Am ◽  
Reto D. Kurmann ◽  
Donald J. Hagler ◽  
Melanie C. Bois ◽  
...  
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Case Report ◽  
Mitral Regurgitation ◽  
Rare Case ◽  
Congenital Heart ◽  
Cardiac Tumors ◽  
Atrioventricular Canal ◽  
Case Summary ◽  
Atrioventricular Canal Defect

Introduction: Cardiac papillary fibroelastomas (PFEs) are the most common primary benign cardiac tumors, although they are somewhat unusual in children and typically seen on the left-sided cardiac valves.Case summary: A 10-week-old patient was found to have a partial atrioventricular canal defect, with associated tricuspid and mitral regurgitation. He was medically managed until 1 year of age, when surgical correction was done. During the procedure, a PFE was found incidentally on the TV.Conclusion: This is one of the youngest patients to be reported with PFE, thus adding to the literature of these unusual cases in children.

Cardiac involvement in genetic disease

2010 ◽  
pp. 2834-2841
Author(s):  
Thomas A. Traill
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Family History ◽  
Genetic Disease ◽  
Congenital Heart ◽  
Cardiac Involvement ◽  
Atrioventricular Canal ◽  
Marfan's Syndrome ◽  
Atrioventricular Canal Defect ◽  
History Of

Many clinicians find themselves faced, from time to time, with a patient who has a family history of a known disorder, such as Marfan’s syndrome, or who has noncardiac features that suggest a syndrome. Down’s syndrome—25 to 50% have congenital heart disease, most characteristically atrioventricular canal defect....

scholarly journals Nutritional status correction options in children with congenital heart disease

2015 ◽  
Vol 96 (4) ◽  
pp. 654-659
Author(s):  
L A Gandaeva ◽  
E N Basargina ◽  
T E Borovik ◽  
N G Zvonkova
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Nutritional Status ◽  
Total Protein ◽  
Congenital Heart ◽  
Interventricular Septum ◽  
Atrioventricular Canal ◽  
Protein Losing Enteropathy ◽  
Atrioventricular Canal Defect ◽  
Status Assessment

Aim. To justify the need of nutritional status assessment and correction in children with congenital heart disease. Methods. Clinical examination, somatometric methods (height, weight, head and chest circumference measuring) were used. Anthropometric data were evaluated using the WHO Anthro, WHO AnthroPlus (2009) programm. The following parameters were analyzed: weight/age, weight/height, height/age, body mass index/age. Results. The review summarizes the existing data on the etiology and pathogenesis of protein-losing enteropathy and methods of its correction. Own observation is described. A girl, born in 1999 from the fifth pregnancy, occurring on the background of toxicosis and threat of abortion, premature second delivery. Birth weight was 1280 g, length 34 cm. Congenital heart disease (double discharge of the right ventricle main vessels, common open atrioventricular canal, defect of interventricular septum, common atrium, the «riding» mitral valve, left ventricle hypoplasia) is diagnosed in maternity hospital. One year after the Fontan surgery was conducted (in August, 2011) hypoproteinemia (total protein content of 44 g/l) was noticed for the first time in the biochemical blood analysis, and swelling appeared on her feet. Intravenous administration of 20% albumin solution was performed numerously, however without positive changes, plasma protein level was low (37 g/l). According to the guidelines, the child was assigned to a specialized diet with «Nutrien standard» 200 ml/dayas an additional source of protein. The child was discharged from the hospital with improvement and recommendations to continue treatment as an outpatient. At follow-up examination in 6 months at our center (November, 2012) the condition was stable, we managed to stop manifestations of exudative enteropathy and to normalize the total protein levels (November, 2012 - 73 g/l), albumin (46 g/l), and blood electrolytes; the girl gained body weight by 2 kg and height increased by 9 cm. Conclusion. Complex examination and treatment of children with congenital heart disease should include nutritional status assessment and, if necessary, its correction.

scholarly journals A Very Rare Case of Cor Triatriatum with Severe Mitral Regurgitation

2018 ◽  
Vol 6 (5) ◽  
pp. 848-850 ◽  
Author(s):  
Selman Dumani ◽  
Ermal Likaj ◽  
Edlira Ruci ◽  
Ervin Bejko ◽  
Ali Refatllari
Keyword(s):  
Heart Failure ◽  
Congenital Heart Disease ◽  
Heart Disease ◽  
Mitral Valve ◽  
Mitral Regurgitation ◽  
Rare Case ◽  
Congenital Heart ◽  
Cor Triatriatum ◽  
Severe Mitral Regurgitation ◽  
Cor Triatriatum Sinister

BACKGROUND: Cor triatriatum sinister is rare congenital heart disease. It is mainly presented in childhood and often accompanied with other congenital anomalies. The cases with cor triatriatum treated surgically in adults and accompanied with severe mitral regurgitation are very rare.CASE REPORT: We present a case with diagnosed cor triatriatum and severe mitral regurgitation. The diagnose was made by echocardiography. She was a female 25 years that was hospitalised with signs of heart failure NYHA II-III.CONCLUSION: We performed the resection of the membrane in the left atrium and repair of a mitral valve according to Alfieri. The patient did very well after the surgery.

scholarly journals Tetralogy of fallot in addition to anomalous aortic origin of a coronary artery in a 1-year-old boy: a case report

BMC Surgery ◽  
2021 ◽  
Vol 21 (1) ◽  
Author(s):  
Lihua Deng ◽  
Tiange Li ◽  
Yunfei Ling ◽  
Menglin Tang
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Case Report ◽  
Coronary Artery ◽  
Tetralogy Of Fallot ◽  
Rare Case ◽  
Congenital Heart ◽  
Common Type ◽  
Case Presentation ◽  
The Right

Abstract Background Anomalous aortic origin of a coronary artery (AAOCA) is a rare congenital heart disease, characterized by the coronary artery inappropriately originates from the aorta. It is usually classified according to the sinus where the coronary artery arises from, while anomalous origin of the right coronary being the most common type. Case presentation In this case report, we described a rare case of Tetralogy of Fallot (TOF) in a 1-year-old boy, who also had the anomalous right coronary artery that originated from the left coronary sinus without an intramural segment. Besides TOF repair, lateral pulmonary translocation was undertaken in order to avoid risks of myocardial ischemia. Conclusion We successfully completed a one-stage operation consisting of TOF repair and pulmonary artery translocation in a 1-year-old boy. We advocated early operation of pulmonic translocation for AAOCA patients without an intramural segment instead of unroofing procedure.

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