scholarly journals Cerebellar liponeurocytoma

2020 ◽  
Author(s):  
Keyword(s):  
Cerebellar Liponeurocytoma

scholarly journals Cerebellar liponeurocytoma: a rare intracranial tumor with possible familial predisposition. Case report

2016 ◽  
Vol 125 (1) ◽  
pp. 57-61 ◽  
Author(s):  
Amparo Wolf ◽  
Huda Alghefari ◽  
Daria Krivosheya ◽  
Michael D. Staudt ◽  
Gregory Bowden ◽  
...  
Keyword(s):  
Tumor Development ◽  
Healthy Woman ◽  
Intracranial Tumor ◽  
Intracranial Tumors ◽  
Histopathological Changes ◽  
Biological Origin ◽  
Familial Predisposition ◽  
History Of ◽  
Cerebellar Liponeurocytoma ◽  
Supracerebellar Infratentorial Approach

The biological origin of cerebellar liponeurocytomas is unknown, and hereditary forms of this disease have not been described. Here, the authors present clinical and histopathological findings of a young patient with a cerebellar liponeurocytoma who had multiple immediate family members who harbored similar intracranial tumors. A 37-year-old otherwise healthy woman presented with a history of progressive headaches. Lipomatous medulloblastoma had been diagnosed previously in her mother and maternal grandfather, and her maternal uncle had a supratentorial liponeurocytoma. MRI revealed a large, poorly enhancing, lipomatous mass emanating from the superior vermis that produced marked compression of posterior fossa structures. An uncomplicated supracerebellar infratentorial approach was used to resect the lesion. Genetic and histopathological analyses of the lesion revealed neuronal, glial, and lipomatous differentiation and confirmed the diagnosis of cerebellar liponeurocytoma. A comparison of the tumors resected from the patient and, 22 years previously, her mother revealed similar features. Cerebellar liponeurocytoma is a poorly understood entity. This report provides novel evidence of an inheritable predisposition for tumor development. Accurate diagnosis and reporting of clinical outcomes and associated genetic and histopathological changes are necessary for guiding prognosis and developing recommendations for patient care.

scholarly journals Cerebellar liponeurocytoma with atypical histological features – a rare example of a glioneuronal tumor

2017 ◽  
Vol 3 ◽  
pp. 227-234 ◽  
Author(s):  
Blanka Hermann ◽  
Michal Woznica ◽  
Wojciech Kloc ◽  
Piotr Borkowski ◽  
Witold Libionka ◽  
...  
Keyword(s):  
Glioneuronal Tumor ◽  
Histological Features ◽  
Cerebellar Liponeurocytoma

scholarly journals Central liponeurocytoma: Case report and review of literature

2012 ◽  
Vol 01 (01) ◽  
pp. 083-085 ◽  
Author(s):  
Pankaj Ailawadhi ◽  
M.C. Sharma ◽  
A.K. Mahapatra ◽  
P. Sarat Chandra
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Tumor Classification ◽  
Central Nervous System Tumor ◽  
The Central Nervous System ◽  
Cerebellar Liponeurocytoma ◽  
Classification Of Tumors ◽  
System Tumor ◽  
Well Differentiated ◽  
Glioneuronal Tumors

Abstract Cerebellar liponeurocytoma consists of well-differentiated neurons with the cytology of neurocytes in addition to a population of lipidized cells. Hence it is biphasic in appearance and has been included in the category of glioneuronal tumors of the central nervous system by the WHO working group on the Classification of Tumors of the Nervous System. However, liponeurocytoma is not exclusive to the cerebellar or fourth ventricular location. Since its inclusion in the central nervous system tumor classification, nine cases with similar histological and immunohistochemical features have also been described in the lateral ventricles. We describe here such a lateral ventricular tumour in a 30-year-old woman, characteristically showing divergent glio-neuronal differentiation and lipidized neoplastic cells. Therefore, we suggest that future WHO tumor classification should consider that liponeurocytomas are not entirely restricted to the cerebellum and henceforth change of nomenclature might be considered, as also pointed out by other authors.

scholarly journals Cerebellar Liponeurocytoma: A Rare Fatty Tumor and its Literature Review

2019 ◽  
Vol 10 (02) ◽  
pp. 360-363 ◽  
Author(s):  
Harsh Deora ◽  
A. R. Prabhuraj ◽  
Jitender Saini ◽  
T. C. Yasha ◽  
Arivazhagan Arimappamagan
Keyword(s):  
Magnetic Resonance Imaging ◽  
Computed Tomography ◽  
Magnetic Resonance ◽  
Intracranial Pressure ◽  
Gait Ataxia ◽  
Imaging Features ◽  
Rare Entity ◽  
Raised Intracranial Pressure ◽  
Resonance Imaging ◽  
Cerebellar Liponeurocytoma

ABSTRACTCerebellar liponeurocytoma is a rare oncological entity, and the knowledge about the treatment and outcome of these rare tumors is still evolving. Very few cases have been described in literature. We report a middle-aged male who presented with raised intracranial pressure features and gait ataxia. His imaging features revealed classical features of liponeurocytoma in cerebellar vermis, with abundant fat component evident in both computed tomography and magnetic resonance imaging. He underwent resection of the lesion and has been asymptomatic for 4 years. This report describes the classical radiological and immunohistochemical features of this rare entity with favorable outcome and reviews the existing literature.

scholarly journals Cerebellar liponeurocytoma: A case report and review of the literature

2015 ◽  
Vol 11 (2) ◽  
pp. 1061-1064 ◽  
Author(s):  
KE WANG ◽  
MING NI ◽  
LIANG WANG ◽  
GUIJUN JIA ◽  
ZHEN WU ◽  
...  
Keyword(s):  
Case Report ◽  
Review Of The Literature ◽  
Cerebellar Liponeurocytoma

Cerebellar liponeurocytoma

2001 ◽  
Vol 95 (4) ◽  
pp. 700-703 ◽  
Author(s):  
Thad R. Jackson ◽  
William F. Regine ◽  
Dianne Wilson ◽  
Daron G. Davis
Keyword(s):  
World Health ◽  
Treatment Modalities ◽  
Central Nervous System Neoplasms ◽  
Content Type ◽  
Biological Potential ◽  
Cerebellar Liponeurocytoma ◽  
Pertinent Information ◽  
Health Organization ◽  
Nervous System Neoplasms

✓ Cerebellar liponeurocytoma is a rare tumor of the posterior fossa that has many morphological similarities to medulloblastoma and neurocytoma. Recently the World Health Organization working group for classification of central nervous system neoplasms adopted the term “cerebellar liponeurocytoma” to provide a unified nomenclature for a tumor variously labeled in the literature as lipomatous medulloblastoma, lipidized medulloblastoma, medullocytoma, neurolipocytoma, lipomatous glioneurocytoma, and lipidized mature neuroectodermal tumor of the cerebellum. The rarity of this tumor and paucity of pertinent information regarding its biological potential and natural history have resulted in the application of various treatment modalities. It is suggested in the available literature that these lesions have a much more favorable prognosis than typical medulloblastomas, and that adjuvant therapy for liponeurocytoma need not be as extensive as that administered for medulloblastomas.

scholarly journals Cerebellar liponeurocytoma – a rare entity: a case report

2018 ◽  
Vol 12 (1) ◽  
Author(s):  
Oliver Gembruch ◽  
Andreas Junker ◽  
Yahya Ahmadipour ◽  
Ulrich Sure ◽  
Elias Lemonas
Keyword(s):  
Case Report ◽  
Rare Entity ◽  
Cerebellar Liponeurocytoma

scholarly journals Cerebellar Liponeurocytoma Mimicking Medulloblastoma: Case Report of a Childhood and Literature Review

2021 ◽  
Vol 11 ◽  
Author(s):  
Changhui Dong ◽  
Yining Jiang ◽  
Liyan Zhao ◽  
Yubo Wang ◽  
Yang Bai ◽  
...  
Keyword(s):  
Postoperative Radiotherapy ◽  
Tumor Resection ◽  
Treatment Strategies ◽  
Benign Neoplasm ◽  
World Health ◽  
Pathological Examination ◽  
Long Term Follow Up ◽  
The Central Nervous System ◽  
Cerebellar Liponeurocytoma ◽  
Health Organization

BackgroundCerebellar liponeurocytoma is a rare benign neoplasm of the central nervous system, which arises mainly in adult patients with only 3 cases reported in children. Due to its rarity, the diagnosis and treatment strategies for cerebellar liponeurocytoma remain unclear. The purpose of this study was to explore the epidemiology, clinical features, imaging findings, pathological characteristics, different diagnoses, treatment, and prognosis of cerebellar liponeurocytoma in juveniles.Case DescriptionA 5-year-old boy was admitted to the department of neurosurgery due to a 5-month history of headaches, nausea, vomiting, dizziness, dysphoria, as well as visual blurring associated with the peak of the headache. Magnetic resonance imaging showed a 4.9×5.4×6.2 cm mass located in the fourth ventricle and cerebellar vermis combined with hydrocephalus and periventricular edema. The mass was completely removed, and pathological examination indicated a cerebellar liponeurocytoma of the World Health Organization Grade II classification.ConclusionThe present study was the first to report a cerebellar liponeurocytoma with total tumor resection and adjuvant radiotherapy in a pediatric patient. Total tumor resection and postoperative radiotherapy together with close and long-term follow-up seem to be the optimal treatment strategy for juvenile patients. However, the side-effect of radiation needs to be considered.

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