scholarly journals A Case Series of X-Linked Deafness-2 with Sensorineural Hearing Loss, Stapes Fixation, and Perilymphatic Gusher: MR Imaging and Clinical Features of Hypothalamic Malformations

2020 ◽  
Vol 41 (6) ◽  
pp. 1087-1093
Author(s):  
J.-A. Prat Matifoll ◽  
M. Wilson ◽  
R. Goetti ◽  
C. Birman ◽  
B. Bennett ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Mr Imaging ◽  
Sensorineural Hearing Loss ◽  
Clinical Features ◽  
Case Series ◽  
Sensorineural Hearing ◽  
Stapes Fixation

scholarly journals Sudden sensorineural hearing loss in patients with vestibular schwannoma

2021 ◽  
Vol 11 (1) ◽  
Author(s):  
Koichiro Wasano ◽  
Naoki Oishi ◽  
Masaru Noguchi ◽  
Ko Hentona ◽  
Seiichi Shinden ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Clinical Features ◽  
Vestibular Schwannoma ◽  
Recovery Rate ◽  
Treatment Plan ◽  
Full Range ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Recurrence Time

AbstractClinical features of sudden sensorineural hearing loss (SSNHL) associated with vestibular schwannoma (VS) are not fully understood. Determining a treatment plan and explaining it to patients requires clinicians to clearly understand the clinical features related to the tumor, including SSNHL. To identify the full range of clinical features of VS-associated SSNHL, especially recovery of hearing following multiple episodes of SSNHL and what factors predict recovery and recurrence. A multicenter retrospective chart review was conducted in seven tertiary care hospitals between April 1, 2011, and March 31, 2020. We collected and analyzed dose of administered steroid, pure-tone audiometry results, and brain MRIs of patients diagnosed with VS-associated SSNHL. Seventy-seven patients were included. They experienced 109 episodes of audiogram-confirmed SSNHL. The highest proportion of complete recoveries occurred in patients with U-shaped audiograms. The recovery rates for the first, second, and third and subsequent episodes of SSNHL were 53.5%, 28.0%, and 9.1%, respectively. Recovery rate decreased significantly with increasing number of SSNHL episodes (P =0 .0011; Cochran-Armitage test). After the first episode of SSNHL, the recurrence-free rate was 69.9% over 1 year and 57.7% over 2 years; the median recurrence time was 32 months. Logarithmic approximation revealed that there is a 25% probability that SSNHL would recur within a year. SSNHL in patients with VS is likely to recur within one year in 25% of cases. Also, recovery rate decreases as a patient experiences increasing episodes of SSNHL.

scholarly journals MR Imaging in Sudden Sensorineural Hearing Loss. Time to Talk

2017 ◽  
Vol 38 (8) ◽  
pp. 1475-1479 ◽  
Author(s):  
G. Conte ◽  
F. Di Berardino ◽  
C. Sina ◽  
D. Zanetti ◽  
E. Scola ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Mr Imaging ◽  
Sensorineural Hearing Loss ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing

scholarly journals Clinical Features and Prognosis of Sudden Sensorineural Hearing Loss Secondary to Intralabyrinthine Hemorrhage

2016 ◽  
Vol 20 (1) ◽  
pp. 31 ◽  
Author(s):  
Jae Woo Lee ◽  
Yoon Ah Park ◽  
Sang Man Park ◽  
Tae Hoon Kong ◽  
Sang Yoo Park ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Clinical Features ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing

Audiologist-led screening of acoustic neuromas in patients with asymmetrical sensorineural hearing loss and/or unilateral tinnitus: our experience in 1126 patients

2018 ◽  
Vol 132 (9) ◽  
pp. 786-789
Author(s):  
Y Abbas ◽  
G Smith ◽  
A Trinidade
Keyword(s):  
Magnetic Resonance Imaging ◽  
Hearing Loss ◽  
Magnetic Resonance ◽  
Sensorineural Hearing Loss ◽  
Acoustic Neuroma ◽  
Case Series ◽  
Cost Savings ◽  
Sensorineural Hearing ◽  
Resonance Imaging ◽  
Tertiary Referral Centre

AbstractObjectiveTo determine whether patients within an otolaryngology department presenting with asymmetrical sensorineural hearing loss and/or unilateral tinnitus can be safely and cost-efficiently screened for acoustic neuroma by audiologists as a first or only point of contact.MethodsA prospective case series and cost analysis were conducted at a tertiary referral centre. Between April 2013 and March 2017, 1126 adult patients presented to the audiology department with asymmetrical sensorineural hearing loss and/or unilateral tinnitus. All were screened for acoustic neuroma with magnetic resonance imaging, based on pre-determined criteria. The main outcome measure was the presence of acoustic neuroma or other pathology on magnetic resonance imaging.ResultsTwenty-five patients (2.22 per cent) were found to have an acoustic neuroma (size range: 3–20 mm) and were referred to the otolaryngologist for further assessment. The remaining patients were appropriately managed and discharged by the audiologists without ENT input. This resulted in an overall cost saving of £164 850.ConclusionPatients with asymmetrical sensorineural hearing loss and/or unilateral tinnitus can be safely screened for acoustic neuroma and independently managed by audiologists as a first or only point of contact, resulting in considerable departmental cost savings.

Clinical Features of Sudden Sensorineural Hearing Loss in Diabetic Patients

2005 ◽  
Vol 115 (9) ◽  
pp. 1676-1680 ◽  
Author(s):  
Shuen-Fu Weng ◽  
Yuh-Shyang Chen ◽  
Chuan-Jen Hsu ◽  
Fen-Yu Tseng
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Clinical Features ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Diabetic Patients

MR Imaging of 495 Consecutive Cases with Sensorineural Hearing Loss

1995 ◽  
Vol 36 (4-6) ◽  
pp. 603-609 ◽  
Author(s):  
W. Wu ◽  
K.-Å. Thuomas
Keyword(s):  
Hearing Loss ◽  
Mr Imaging ◽  
Sensorineural Hearing Loss ◽  
Spin Echo ◽  
Superior Temporal Gyrus ◽  
Auditory Pathway ◽  
Sensorineural Hearing ◽  
Fast Spin Echo ◽  
Fast Spin ◽  
Internal Acoustic Canal

Purpose: To examine patients with sensorineural hearing loss (SNHL) with MR. Material and Methods: 495 consecutive patients with SNHL and 120 age-matched healthy controls were examined. Spin-echo (SE) and fast spin-echo (FSE) images were used with 1.5 T equipment. Results: An intracranial abnormality was found in 211 (42.6%) of the patients with 95 (19.2%) along the acoustic pathway. Eleven of the 95 patients had sensory hearing loss while 84 had neural hearing loss with the retrocochlear auditory pathway affected by lesions. In 62 of the 84 patients, the internal acoustic canal and cerebellopontine angle were involved. Twenty-two patients had intra-axial lesions. The controls had no pathologic changes along the auditory pathway. Conclusion: MR imaging in a patient with SNHL must cover the entire acoustic pathway from the cochlea to the superior temporal gyrus, and all the components of the auditory pathway should be scrutinized. The FSE-technique can be used to detect the lesions causing SNHL. FSE-sequences can replace SE-sequences.

Sign in / Sign up

Export Citation Format

Share Document