scholarly journals Deferiprone Reduces Hemosiderin Deposits in the Brain of a Patient with Superficial Siderosis: Fig 1.

2010 ◽  
Vol 32 (1) ◽  
pp. E1-E2 ◽  
Author(s):  
M. Levy ◽  
R.H. Llinas
Keyword(s):  
Superficial Siderosis ◽  
The Brain ◽  
Hemosiderin Deposits

scholarly journals Unusual Presentation in Infratentorial Superficial Siderosis: Acute Intracranial Hypertension

2021 ◽  
pp. 9-16
Author(s):  
Maria Sheila Guimarães Rocha ◽  
Hugo Salomão Grangeiro Mirô ◽  
Gregori Manfroi ◽  
Arthur de Medeiros Dias ◽  
Raphaella Cardoso ◽  
...  
Keyword(s):  
Spinal Cord ◽  
Intracranial Hypertension ◽  
Cranial Nerves ◽  
Superficial Siderosis ◽  
Brain Iron ◽  
Progressive Hearing Loss ◽  
Atypical Case ◽  
Neurological Features ◽  
The Brain ◽  
Hemosiderin Deposits

Superficial siderosis (SS) of the nervous system is a rare acquired condition related to hemosiderin deposits in subpial layers of the brain, brainstem, cerebellum, cranial nerves, and spinal cord, leading to brain iron-mediated neurodegeneration. The cardinal neurological features are slowly progressive hearing loss, ataxia, and pyramidal signs. Here we describe an atypical case of infratentorial SS evolving with acute intracranial hypertension in the absence of typical chronic signs.

Superficial siderosis of the brain following unexplained subarachnoid hemorrhage: MRI diagnosis and clinical significance

1992 ◽  
Vol 34 (5) ◽  
pp. 407-410 ◽  
Author(s):  
P. M. Bourgouin ◽  
D. Tampieri ◽  
D. Melancon ◽  
R. del Carpio ◽  
R. Ethier
Keyword(s):  
Subarachnoid Hemorrhage ◽  
Clinical Significance ◽  
Superficial Siderosis ◽  
Mri Diagnosis ◽  
The Brain

scholarly journals Hemosiderosis of Central Nervous System: a case report of a rare and underdiagnosed disease

2021 ◽  
Vol 10 (11) ◽  
pp. e270101119579
Author(s):  
Cássio Marques Perlin ◽  
Lanusa Alquino Colombo ◽  
Anderson Dillmann Groto ◽  
Bruno Gleizer da Silva Rigon
Keyword(s):  
Spinal Cord ◽  
Central Nervous System ◽  
Nervous System ◽  
Superficial Siderosis ◽  
Medical Clinic ◽  
Resonance Imaging ◽  
System A ◽  
Magnetic Resonance Imaging Mri ◽  
Brain And Spinal Cord ◽  
The Brain

Superficial Siderosis (SS) of Central Nervous System is a rare disease characterized by the deposit of hemosiderin in the brain and spinal cord. Clinically, it is characterized by progressive sensorineural ataxia and deafness associated with injury of superior motor neuron. The diagnosis is made by magnetic resonance imaging (MRI) of the encephalon and spinal cord. The objective of the study is to report the case of a patient with characteristic elements of the syndrome, accompanied in a private medical clinic.

Superficial Siderosis of the Brain as a Late Complication of Subarachnoid Haemorrhage

2003 ◽  
Vol 17 (1) ◽  
pp. 87-87 ◽  
Author(s):  
Konstantinos Spengos ◽  
Marios Panas ◽  
Sofia Sameli ◽  
Konstantinos Vemmos ◽  
Konstantinos Sfangos ◽  
...  
Keyword(s):  
Subarachnoid Haemorrhage ◽  
Late Complication ◽  
Superficial Siderosis ◽  
The Brain

scholarly journals Clinical Significance of T2*gradient-recalled Echo/susceptibility-weighted Imaging Sequences in Evaluating Superficial Siderosis in the Setting of Intracerebral Tumors: Pilocytic Astrocytoma

2018 ◽  
Vol 8 ◽  
pp. 36
Author(s):  
Sankarsh N. Jetty ◽  
Zain Badar ◽  
Douglas Drumsla ◽  
Rajiv Mangla
Keyword(s):  
Magnetic Resonance Imaging ◽  
Spinal Cord ◽  
Pilocytic Astrocytoma ◽  
Superficial Siderosis ◽  
Susceptibility Weighted Imaging ◽  
Resonance Imaging ◽  
Gradient Echo ◽  
Common Cause ◽  
Brain And Spinal Cord ◽  
The Brain

Superficial siderosis is the slow accumulation of hemosiderin on the pial surfaces of the brain and spinal cord. The most common cause of intracranial superficial siderosis is secondary to subarachnoid hemorrhage. Rarely, superficial siderosis can also be caused by tumors. Superficial siderosis presents clinically as hearing loss and gait instability that progressively worsen. The diagnosis is primarily made by magnetic resonance imaging; however, susceptibility-weighted imaging (SWI) and T2* gradient echo (GRE) sequences demonstrate the highest sensitivity in detecting this condition. To the best of our knowledge, there has been only one previous case of superficial siderosis secondary to a pilocytic astrocytoma of the spine. However, we present a case of intracerebral pilocytic astrocytoma resulting in superficial siderosis, with emphasis on acquisition and use of T2*GRE/SWI sequences.

Superficial siderosis of the central nervous system: an underestimated cause of hearing loss

1997 ◽  
Vol 111 (1) ◽  
pp. 60-62 ◽  
Author(s):  
M. L. Castelli ◽  
A. Husband
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Hearing Loss ◽  
Cranial Nerves ◽  
Sensorineural Deafness ◽  
Superficial Siderosis ◽  
Brain Surface ◽  
The Central Nervous System ◽  
Magnetic Resonance Imaging Mri ◽  
The Brain

AbstractSuperficial siderosis of the central nervous system (CNS) is a rare disease resulting in the accumulation of haemosiderin in the meninges, the brain surface, the spinal cord and the cranial nerves. The pigment is deposited as a result of chronic bleeding in the subarachnoid space. This produces a clinical picture of deafness, ataxia, cranial nerve deficits and in the latest stages dementia. In some cases the source of bleeding can be identified, whilst in others it can not. Despite its rarity the disease should be considered in the differential diagnosis of sensorineural deafness, particularly as it is a progressive and in some cases curable disease which is easily diagnosed by magnetic resonance imaging (MRI). In this case report the haemosiderin was derived from an ependymoma of the fourth ventricle with extension into the cerebello-pontine angle. The first symptom was a worsening sensorineural hearing loss.

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