Dyke–Davidoff–Masson syndrome: A rare cause of cerebral hemiatrophy in children

2020 ◽  
Vol 17 (3) ◽  
pp. 58-60
Author(s):  
Surendar Penumuri ◽  
Keyword(s):  
Cerebral Hemiatrophy

scholarly journals MR and CT imaging in the Dyke-Davidoff-Masson syndrome: report of three cases and contribution to pathogenesis and differential diagnosis

1998 ◽  
Vol 56 (4) ◽  
pp. 803-807 ◽  
Author(s):  
PAULO HENRIQUE AGUIAR ◽  
WEI LIU CHING ◽  
HELIO LEITÃO ◽  
F. ISSA ◽  
GUILHERME LEPSKI ◽  
...  
Keyword(s):  
Differential Diagnosis ◽  
Mental Retardation ◽  
Brain Injury ◽  
Paranasal Sinuses ◽  
Facial Asymmetry ◽  
Cerebral Injury ◽  
Radiological Features ◽  
Cerebral Hemiatrophy ◽  
The Brain ◽  
Syndrome Report

Cerebral hemiatrophy or Dyke-Davidoff-Masson syndrome is a condition characterized by seizures, facial asymmetry, contralateral hemiplegia or hemiparesis, and mental retardation. These findings are due to cerebral injury that may occur early in life or in utero. The radiological features are unilateral loss of cerebral volume and associated compensatory bone alterations in the calvarium, like thickening, hyperpneumatization of the paranasal sinuses and mastoid cells and elevation of the petrous ridge. The authors describe three cases. Classical findings of the syndrome are present in variable degrees according to the extent of the brain injury. Pathogenesis is commented.

Unilateral cerebral polymicrogyria with ipsilateral cerebral hemiatrophy

2002 ◽  
Vol 12 (10) ◽  
pp. 2542-2547 ◽  
Author(s):  
Katsumi Hayakawa ◽  
Toyoko Kanda ◽  
Yuriko Yamori
Keyword(s):  
Cerebral Hemiatrophy

MR Imaging of Cerebral Hemiatrophy

1988 ◽  
Vol 12 (4) ◽  
pp. 640-643 ◽  
Author(s):  
Jacob Zeiss ◽  
Ray A. Brinker
Keyword(s):  
Mr Imaging ◽  
Cerebral Hemiatrophy

scholarly journals Dyke-Davidoff-Masson-Syndrome Manifested by seizures and learning difficulties: A Case Report

2013 ◽  
Vol 5 (2) ◽  
pp. 111-113
Author(s):  
Mohammad Ibrahim Khalil ◽  
Maliha Hakim ◽  
Afzal Momin ◽  
Abu Nayeem ◽  
Md. Mohitul Islam ◽  
...  
Keyword(s):  
Case Report ◽  
Learning Difficulties ◽  
Facial Asymmetry ◽  
Behavioral Changes ◽  
Clinical Feature ◽  
Present Case Report ◽  
Cerebral Hemiatrophy ◽  
Generalized Seizures ◽  
Spastic Hemiplegia ◽  
Magnetic Resonance Imaging Mri

Dyke-Davidoff-Masson Syndrome (DDMS), also known as cerebral hemiatrophy, is a rare clinical condition characterized by seizures, facial asymmetry, contralateral spastic hemiplegia or hemiparesis, with learning difficulties and behavioral changes. It is commonly diagnosed in presence of clinical feature associated radiological findings which include cerebral hemiatrophy with homolateral hypertrophy of the skull and sinuses. In this present case report a 12 year old teenager female patient was diagnosed as DDMS with recurrent generalized seizures, learning difficulties and right sided hemiparesis. Magnetic resonance imaging (MRI) of the brain showed hemiatrophy involving the left cerebral hemisphere and EEG showed generalized epileptiform discharged. An X-ray of the paranasal air sinuses was normal.DOI: http://dx.doi.org/10.3329/jssmc.v5i2.20768J Shaheed Suhrawardy Med Coll 2013;5(2):111-113

Spontaneous resolution of invasive cerebral aspergillosis following partial resection in a medically untreated infant

2012 ◽  
Vol 10 (1) ◽  
pp. 71-74 ◽  
Author(s):  
Sumit Thakar ◽  
Yasha T. Chickabasaviah ◽  
Alangar S. Hegde
Keyword(s):  
Emergency Services ◽  
Mass Effect ◽  
Cerebral Hemiatrophy ◽  
Right Cerebral Hemisphere ◽  
History Of ◽  
Subcortical Regions ◽  
The Right ◽  
Mri Study ◽  
The Brain

Invasive craniocerebral aspergillosis, often encountered in an immunocompromised setting, is almost uniformly fatal despite radical surgical and medical management, and is frequently a necropsy finding. The authors report a unique, self-resolving clinical course of this aggressive infection in a 10-month-old infant. The infant was brought to the emergency services in altered sensorium with a 1-week history of left-sided hemiparesis, excessive irritability, and vomiting. An MRI study of the brain revealed multiple, heterogeneously enhancing lesions in the right cerebral hemisphere with mass effect. The largest lesion in the frontotemporal cortical and subcortical regions was decompressed on an emergent basis. Histopathological findings were suggestive of invasive aspergillosis, although there was no evidence of the infection in the lungs or paranasal sinuses. Computed tomography–guided aspiration of the remaining lesions and follow-up antifungal therapy were recommended. The parents, however, requested discharge without further treatment. The child was seen at a follow-up visit 3 years later without having received any antifungal treatment. Imaging showed resolution of the infection and features of Dyke-Davidoff-Masson syndrome (cerebral hemiatrophy). This report of invasive cerebral aspergillosis resolving without medical therapy is the first of its kind. Its clinicoradiological aspects are discussed in light of previously reported cases.

Cerebral hemiatrophy caused by multiple developmental venous anomalies involving nearly the entire cerebral hemisphere

2001 ◽  
Vol 25 (2) ◽  
pp. 82-85 ◽  
Author(s):  
Akira Uchino ◽  
Akihiro Sawada ◽  
Yukinori Takase ◽  
Masamitsu Abe ◽  
Sho Kudo
Keyword(s):  
Cerebral Hemisphere ◽  
Venous Anomalies ◽  
Cerebral Hemiatrophy ◽  
Developmental Venous Anomalies

Double Ventricular Shift in a Case of Cerebral Hemiatrophy

1949 ◽  
Vol 16 (1) ◽  
pp. 17-20
Author(s):  
R. M. GEIST ◽  
C. R. HUGHES
Keyword(s):  
Cerebral Hemiatrophy

scholarly journals Differential Diagnoses of Cerebral Hemiatrophy in Childhood: A Review of Literature with Illustrative Report of Two Cases

2013 ◽  
Vol 5 (3) ◽  
Author(s):  
Felix Uduma Uduma ◽  
Jude-Kennedy C. Emejulu ◽  
Mathieu Motah ◽  
Philip C. N. Okere ◽  
Pierre C. Ongolo ◽  
...  
Keyword(s):  
Differential Diagnoses ◽  
Review Of Literature ◽  
Cerebral Hemiatrophy

Left cerebral hemiatrophy and schizophrenia-like psychosis in an adolescent

1996 ◽  
Vol 20 (1-2) ◽  
pp. 231-234 ◽  
Author(s):  
William G. Honer ◽  
Lili C. Kopala ◽  
Jake J. Locke ◽  
Jocelyne S. Lapointe
Keyword(s):  
Cerebral Hemiatrophy
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