scholarly journals Uterus didelphys with obstructed hemivagina and ipsilateral renal agenesis

2007 ◽  
Vol 54 (3) ◽  
pp. 137-139 ◽  
Author(s):  
Lj. Mirkovic ◽  
D. Mirkovic ◽  
V. Boskovic ◽  
Z. Markovic
Keyword(s):  
Abdominal Pain ◽  
Case Report ◽  
Magnetic Resonance ◽  
Mr Imaging ◽  
Clinical Examination ◽  
Renal Agenesis ◽  
Clinical Manifestations ◽  
Uterus Didelphys ◽  
Rare Anomaly ◽  
Obstructed Hemivagina

This is a case report of two patients how have uterus didelphys with obstructed hemivagina and ipsilateral renal agenesis with different clinical manifestations. Progressive abdominal pain after menarche, anuria or obstipation with the existing paravaginal tumor indicates this rare anomaly. Initially, the anomaly remains unrecognized, while patients most frequently referred to surgeons for assistance. The method of choice for diagnosis is clinical examination, ultrasonography and magnetic resonance (MR) imaging. Transvaginal excision of the septum is appropriate mode of treatment.

scholarly journals Uterus didelphys with obstructed hemivagina with chronic presentation: a case report

2017 ◽  
Vol 5 (6) ◽  
pp. 2809
Author(s):  
Monika Anant ◽  
Bibekanand Das ◽  
Avishek Bhadra ◽  
Joydev Mukherji
Keyword(s):  
Abdominal Pain ◽  
Case Report ◽  
Clinical Examination ◽  
Clinical Manifestations ◽  
Uterus Didelphys ◽  
Rare Anomaly ◽  
Obstructed Hemivagina

This is a case report of a 24-year patient who had uterus didelphys with obstructed hemivagina. Clinical manifestations of this case were of progressive dysmenorrhea, abdominal pain after menarche, cyclic difficulty in urination and constipation, with the existing paravaginal tumor indicated this rare anomaly. The diagnosis was by clinical examination and ultrasonography.  The patient underwent successful transvaginal septoplasty and drainage of the hematocolpos and hematometra, which is the appropriate mode of treatment in such cases.  

scholarly journals Herlyn-Werner-Wunderlich syndrome presenting with dysmenorrhea: a case report

2019 ◽  
Vol 13 (1) ◽  
Author(s):  
Dilruba Sharmen Nishu ◽  
Md. Monir Uddin ◽  
Khadija Akter ◽  
Shameema Akter ◽  
Monira Sarmin ◽  
...  
Keyword(s):  
Magnetic Resonance Imaging ◽  
Abdominal Pain ◽  
Case Report ◽  
Magnetic Resonance ◽  
Magnetic Resonance Imaging Finding ◽  
Resonance Imaging ◽  
Pelvic Magnetic Resonance Imaging ◽  
Endometrial Cavity ◽  
Obstructed Hemivagina ◽  
The Right

Abstract Background Herlyn-Werner-Wunderlich syndrome is a rare congenital anomaly characterized by uterus didelphys, obstructed hemivagina, and ipsilateral renal agenesis. The most common presentation is abdominal pain, dysmenorrhea, and abdominal mass secondary to hematocolpos. We present the first case report on Herlyn-Werner-Wunderlich syndrome from Bangladesh. Case presentation A 15-year-old Asian girl presented with lower abdominal pain of 3 months’ duration. She had had menarche 3 months earlier and had a regular menstrual cycle with cyclical abdominal pain. Abdominal examination found a tender mass on the right iliac fossa. Further evaluation with ultrasound revealed distended endometrial cavity filled with complex fluid and nonvisualization of the right kidney. Pelvic magnetic resonance imaging showed absent right kidney and two separate endometrial stripes surrounded by endometrium and a muscular layer. The right endometrial cavity and cervix were distended with blood. This magnetic resonance imaging finding is consistent with Herlyn-Werner-Wunderlich syndrome with uterine didelphyis, right-sided hematometra resulting from obstructed hemivagina, and ipsilateral agenesis of the right kidney. The vaginal septum was resected for vaginoplasty. She was discharged 5 days after surgery and came for follow-up after 7 days. Vaginal examination revealed a healthy wound with no adhesion of the vaginal wall. She also informed us that she had started regular menstruation without any pain 30 days after the operation. Conclusion An unusual presentation of regular menstruation and nonspecific abdominal pain delays the diagnosis, which can lead to complications such as endometriosis and infertility. Awareness is required; otherwise, misdiagnosis clearly can occur.

scholarly journals Management of Hematometra in Single Horn of Didelphic Uterus with Obstructed Hemivagina and Ipsilateral Renal Agenesis Syndrome: A Case Report with Brief Review of Literature

2016 ◽  
Vol 8 (3) ◽  
pp. 231-235
Author(s):  
Ritu Agarwal
Keyword(s):  
Case Report ◽  
South Asian ◽  
Renal Agenesis ◽  
Rare Entity ◽  
Review Of Literature ◽  
Resonance Imaging ◽  
Uterus Didelphys ◽  
Future Fertility ◽  
Ohvira Syndrome ◽  
Obstructed Hemivagina

ABSTRACT The triad of uterus didelphys with obstructed hemivagina and ipsilateral renal agenesis (OHVIRA) syndrome is a rare entity. These cases are difficult to diagnose due to heterogeneous presentation and rarity of the condition. Ultrasonography and magnetic resonance imaging are important for initial diagnosis; however, laparoscopy is required for the confirmation of the diagnosis. Early and accurate diagnosis of this condition followed by prompt surgical therapy is essential to prevent complications and to preserve future fertility. Here we report a case of uterus didelphys with hemivagina and ipsilateral renal agenesis with hematometra and hematosalpinx in a young girl. How to cite this article Mishra VV, Agarwal R, Bandwal P, Choudhary S, Gandhi K. Management of Hematometra in Single Horn of Didelphic Uterus with Obstructed Hemivagina and Ipsilateral Renal Agenesis Syndrome: A Case Report with Brief Review of Literature. J South Asian Feder Obst Gynae 2016;8(3):231-235.

scholarly journals Herlyn Werner Wunderlich Syndrome with Hematocolpos Symptom

2019 ◽  
Vol 7 (16) ◽  
pp. 2679-2681
Author(s):  
Muhammad Rusda ◽  
Amru Umara ◽  
Andrina Yunita Murni Rambe
Keyword(s):  
Congenital Anomaly ◽  
Abdominal Pain ◽  
Renal Agenesis ◽  
Symptomatic Relief ◽  
Definitive Diagnosis ◽  
Lower Abdomen ◽  
Rare Congenital Anomaly ◽  
Uterus Didelphys ◽  
Mullerian Ducts ◽  
Obstructed Hemivagina

BACKGROUND: Uterodidelphys with obstructed hemivagina and ipsilateral renal agenesis is referred to as the Herlyn Werner Wunderlich (HWW) syndrome. Herlyn-Werner-Wunderlich (HWW) syndrome is a very rare congenital anomaly of the urogenital tract involving Müllerian ducts and Wolffian structures, and it is Werner by the triad of uterus didelphys, obstructed hemivagina and ipsilateral renal agenesis. CASE REPORT: Here, we describe a 17-year-old female patient presented with severe and increasing cyclical abdominal pain. She attained menarche 3 years back. The patient had irregular and scanty menstruation associated with dysmenorrhoea. On physical examination, secondary sexual characters were well developed, and on palpation, lower abdomen tenderness was not present. Diagnosed with HWW syndrome, who was taken up for diagnostic sonography and MRI, followed by vaginal septal resection, CONCLUSION: In addition to a definitive diagnosis, this approach helped in symptomatic relief to the patient.

Abdominopelvic Pain in Patient with Uterus Didelphys and Unilateral Obstructed Hemivagina and Ipsilateral Renal Agenesis (OHVIRA Syndrome)

2021 ◽  
Author(s):  
Zahra Tavoli ◽  
Ali Montazeri
Keyword(s):  
Renal Agenesis ◽  
Primary Diagnosis ◽  
Case Presentation ◽  
Uterus Didelphys ◽  
Future Fertility ◽  
History Of ◽  
Ohvira Syndrome ◽  
Obstructed Hemivagina ◽  
Magnetic Resonance Imaging Mri

Introduction: Uterus didelphys with obstructed hemivagina associated with ipsilateral renal agenesis (OHVIRA syndrome) is a rare female urogenital malformation and delay in its diagnosis could lead to several complications. Case presentation: A 21-year-old virgin woman was admitted to the emergency department (ED) with severe abdominal pain, without fever and vaginal discharge. She reported a history of cyclic abdominopelvic pain and dysmenorrhea for 5 years. The primary diagnosis (OHVIRA syndrome) was made using ultrasonography, spiral computed tomography (CT) and magnetic resonance imaging (MRI). In addition, laparoscopy was performed to confirm diagnosis and drain hematosalpinx. Then, hysteroscopy was carried out for septum resection and catheter insertion. At one-month follow-up the ultrasonography showed normal left hemicavity of uterus associated with significant decrease in dysmenorrhea. Conclusion: Being aware of OHVIRA syndrome and clinical suspicion of this rare anomaly are essential for making a timely diagnosis, preventing complications, relieving symptoms, and preserving future fertility.

scholarly journals Hysteroscopic Resection of the Vaginal Septum in Uterus Didelphys with Obstructed Hemivagina: A Case Report

2007 ◽  
Vol 22 (4) ◽  
pp. 766 ◽  
Author(s):  
Tae Eun Kim ◽  
Gyoung Hoon Lee ◽  
Young Min Choi ◽  
Byung Chul Jee ◽  
Seung-Yup Ku ◽  
...  
Keyword(s):  
Case Report ◽  
Vaginal Septum ◽  
Uterus Didelphys ◽  
Obstructed Hemivagina ◽  
Hysteroscopic Resection
Sign in / Sign up

Export Citation Format

Share Document