scholarly journals Clinical Features of Unilateral Moyamoya Disease

2010 ◽  
Vol 50 (5) ◽  
pp. 378-385 ◽  
Author(s):  
Kentaro HAYASHI ◽  
Kazuhiko SUYAMA ◽  
Izumi NAGATA
2016 ◽  
Vol 96 ◽  
pp. 474-482 ◽  
Author(s):  
Qian Zhang ◽  
Rong Wang ◽  
Yaping Liu ◽  
Yan Zhang ◽  
Shuo Wang ◽  
...  

2008 ◽  
Vol 26 (3) ◽  
pp. 244-249 ◽  
Author(s):  
Toshiyasu Ogata ◽  
Masahiro Yasaka ◽  
Tooru Inoue ◽  
Kotaro Yasumori ◽  
Setsuro Ibayashi ◽  
...  

2010 ◽  
Vol 283 (S1) ◽  
pp. 19-22 ◽  
Author(s):  
Jun Kakogawa ◽  
Miyuki Sadatsuki ◽  
Norio Masuya ◽  
Hideto Gomibuchi ◽  
Hiroyasu Ohno ◽  
...  

Stroke ◽  
1998 ◽  
Vol 29 (7) ◽  
pp. 1347-1351 ◽  
Author(s):  
David Chiu ◽  
Peter Shedden ◽  
Patti Bratina ◽  
James C. Grotta

2011 ◽  
Vol 49 (1) ◽  
pp. 65 ◽  
Author(s):  
Tae-Wan Kim ◽  
Bo-Ra Seo ◽  
Jae Hyoo Kim ◽  
Young Ok Kim

1984 ◽  
Vol 24 (1) ◽  
pp. 30-34 ◽  
Author(s):  
Shizuya KASAMO ◽  
Tetsuhiko ASAKURA ◽  
Yukio YAMAMOTO ◽  
Eiki KOBAYASHI

2013 ◽  
Vol 12 (2) ◽  
pp. 175-180 ◽  
Author(s):  
Maki Mukawa ◽  
Tadashi Nariai ◽  
Yoshiharu Matsushima ◽  
Kikuo Ohno

Object The authors compared the clinical features between familial and sporadic cases of moyamoya disease (MMD) by retrospectively analyzing data on patients with MMD registered in the database of Tokyo Medical and Dental University over a period of 28 years. Methods In total, 383 patients with hospital records at Tokyo Medical and Dental University from 1980 to 2007 were registered into the database. The data on all of these patients were retrospectively reviewed to clarify the occurrence of familial cases. Clinical features of child or adolescent patients (< 20 years of age) with MMD were compared between familial and sporadic cases in a subgroup of patients who were registered after 1995, initially diagnosed using MR angiography, and assessed using an intelligence scale. Results Familial occurrence was observed in 59 patients (15.4%) in 40 pedigrees. The clinical features of juvenile patients were analyzed in 124 patients, 22 (17.7%) of whom had familial histories. In comparison with the sporadic cases, patients with familial histories were significantly younger at onset (4.7 vs 6.6 years old), had significantly more cortical infarction (59.1% vs 25.5%), and had significantly more stenoocclusive lesions in the posterior cerebral artery (45.4% vs 24.5%). The rate of patients with intellectual disturbance (intelligence quotient < 75) was significantly larger in the familial cases (47.4%) than in the sporadic cases (17.8%). Conclusions This survey of the clinical features of familial MMD suggests that patients with familial MMD had a more serious clinical course in childhood than the sporadic MMD cases.


Sign in / Sign up

Export Citation Format

Share Document