scholarly journals An adult patient with congenital pulmonary airway malformation and an esophageal cyst

2019 ◽  
Vol 7 (16) ◽  
pp. 396-396
Author(s):  
Hanlu Zhang ◽  
Xin He ◽  
Shangfu Zhang ◽  
Long-Qi Chen ◽  
Yun Wang
Keyword(s):  
Adult Patient ◽  
Congenital Pulmonary Airway Malformation ◽  
Esophageal Cyst ◽  
Pulmonary Airway

Congenital pulmonary airway malformation in adult: report of two rare cases and literature review

2019 ◽  
Vol 58 (1) ◽  
Author(s):  
Antonio Sidoti Pinto ◽  
Alberto Bruno ◽  
Giuseppe Cutaia ◽  
Domenico Albano ◽  
Claudio Leto ◽  
...  
Keyword(s):  
Literature Review ◽  
Congenital Pulmonary Airway Malformation ◽  
Pulmonary Airway

Pleuropulmonary Blastoma Developing in a Case of Misinterpreted Congenital Pulmonary Airway Malformation: a Case Report

2018 ◽  
Vol 37 (5) ◽  
pp. 377-386 ◽  
Author(s):  
Moupali Ghosh ◽  
Nelofar Islam ◽  
Arindam Ghosh ◽  
Priyanka Maity Chaudhuri ◽  
Koushik Saha ◽  
...  
Keyword(s):  
Case Report ◽  
Pleuropulmonary Blastoma ◽  
Congenital Pulmonary Airway Malformation ◽  
Pulmonary Airway

Congenital Pulmonary Airway Malformation Presenting as Unilateral Cystic Lung Disease

2013 ◽  
Vol 188 (8) ◽  
pp. 1030-1031 ◽  
Author(s):  
Eric D. McLoney ◽  
Philip T. Diaz ◽  
Jerry Tran ◽  
Konstantin Shilo ◽  
Subha Ghosh
Keyword(s):  
Lung Disease ◽  
Congenital Pulmonary Airway Malformation ◽  
Cystic Lung ◽  
Cystic Lung Disease ◽  
Pulmonary Airway

Neonatal Congenital Pulmonary Airway Malformation Associated with Mucinous Adenocarcinoma and KRAS Mutations

2021 ◽  
Author(s):  
Ancuta Muntean ◽  
Liliana-Elena Banias ◽  
Niyi Ade-Ajayi ◽  
Shailesh B Patel ◽  
Olivia McKinney ◽  
...  
Keyword(s):  
Mucinous Adenocarcinoma ◽  
Congenital Pulmonary Airway Malformation ◽  
Kras Mutations ◽  
Pulmonary Airway

scholarly journals Current Management of Congenital Pulmonary Airway Malformations: A “European Pediatric Surgeons' Association” Survey

2017 ◽  
Vol 28 (01) ◽  
pp. 001-005 ◽  
Author(s):  
Francesco Morini ◽  
Augusto Zani ◽  
Andrea Conforti ◽  
Ernest van Heurn ◽  
Simon Eaton ◽  
...  
Keyword(s):  
Pregnancy Termination ◽  
Congenital Pulmonary Airway Malformation ◽  
Prenatal Counseling ◽  
Fetal Hydrops ◽  
Online Questionnaire ◽  
Current Management ◽  
Asymptomatic Patients ◽  
Pulmonary Airway ◽  
Thoracoamniotic Shunt

Aim To define current management of congenital pulmonary airway malformation (CPAM). Methods A total of 181 European Pediatric Surgeons' Association members (91% senior) from 48 countries completed an online questionnaire. Main Results Prenatal: 93% respondents work in centers with prenatal diagnosis facilities, and 27% in centers offering in utero surgery. Prenatal counseling is performed by 86% respondents, 22% of whom see >10 cases per year. Risk of single pre-/postnatal complications is deemed low (<5%) by more than 60% of respondents. Eighty-six percent respondents do not offer pregnancy termination for prenatally diagnosed CPAM. Fetal hydrops is the most frequent indication for termination (87%), followed by parental willingness (52%). Prenatal surgery is an option for 44% respondents, preferring thoracoamniotic shunt (82%).Postnatal: 75% respondents operate on asymptomatic patients, 18% before 6 months of age, 62% between 6 and 12 months of age, and 20% after 12 months of age. Risk of infection (86%), cancer (63%), and symptoms development (62%) are indications for surgery in asymptomatic CPAM. Sixty-three percent prefer a thoracotomy. Lobectomy is the preferred procedure (58% respondents). Motivations against surgery include lesion <1 cm (64%), risk of postoperative complications (37%), and lack of evidence favoring surgery (27%). Seventeen percent respondents have seen at least one patient with CPAM with lung cancer, in 89% of the cases within the CPAM. Of all the respondents, 83% and 22% offered dedicated follow-up and genetic screening, respectively. Conclusion Current pre- and postnatal management of CPAM lacks uniformity, particularly for surgical indication, timing, and approach. Efforts should be made toward standardization. Risk of CPAM-associated cancer is not clear.

Sign in / Sign up

Export Citation Format

Share Document