Atypical presentation in Rasmussen encephalitis: delayed late-onset periodic epileptic spasms

2011 ◽  
Vol 13 (3) ◽  
pp. 321-325 ◽  
Author(s):  
Taíssa P.F. Ferrari ◽  
Ana P.A. Hamad ◽  
Luís Otávio S.F. Caboclo ◽  
Ricardo S. Centeno ◽  
Ana Luiza Zaninotto ◽  
...  
Keyword(s):  
Late Onset ◽  
Atypical Presentation ◽  
Rasmussen Encephalitis ◽  
Epileptic Spasms

Late-onset Rasmussen encephalitis in Parry-Romberg syndrome: a case report

2021 ◽  
Author(s):  
Giacomo Evangelista ◽  
Fedele Dono ◽  
Claudia Carrarini ◽  
Mirella Russo ◽  
Laura Bonanni
Keyword(s):  
Case Report ◽  
Late Onset ◽  
Rasmussen Encephalitis ◽  
Parry Romberg Syndrome

Are Epileptic Spasms a Seizure Type for the Insular Region?

2020 ◽  
Vol 51 (04) ◽  
pp. 295-297 ◽  
Author(s):  
Volodymyr Kharytonov ◽  
Olivier Dulac
Keyword(s):  
Slow Wave ◽  
Late Onset ◽  
Motor Program ◽  
High Amplitude ◽  
The Other ◽  
Seizure Type ◽  
Wave Characteristic ◽  
The Third ◽  
Epileptic Spasms ◽  
Insular Region

AbstractTwo patients with insular and striatal postnatal scar had epileptic spasms (ES) that were asymmetrical and the only seizure type, whereas none of the usual ictal symptoms of insular seizures occurred. Ictal electroencephalography (EEG) showed the high-amplitude slow-wave characteristic of ES. Vigabatrin remained efficient for over 4 years for one patient and right into the third decade for the other one. Such ES are distinct from infantile and late onset spasms. Furthermore, these observations suggest that in ES insular epilepsy triggers paroxysmal activation of the striatum, and that vigabatrin inhibits the striatal startle motor program, thus interrupting the corticostriatal loop.

Eating Epilepsy: Pathophysiologic Models, Electroclinical Phenotypes, and Outcome

2019 ◽  
Vol 08 (04) ◽  
pp. 094-099
Author(s):  
Alessandro Iodice
Keyword(s):  
Late Onset ◽  
Age At Onset ◽  
Brain Magnetic Resonance Imaging ◽  
Reflex Epilepsy ◽  
Resonance Imaging ◽  
Rare Form ◽  
Epileptic Spasms ◽  
Generalized Seizures ◽  
Impaired Awareness ◽  
Interictal Discharges

AbstractEating epilepsy (EE) is a rare form of reflex epilepsy precipitated by food. Ictal semiology may vary depending on the etiology, age at onset, and cerebral areas involved in the epileptogenic network. In childhood, EE could manifest as tonic head drop seizures, generalized seizures, or late-onset epileptic spasms. However, in teenagers or adults, seizures are often preceded by aura and commonly manifest as focal seizures with or without impaired awareness. Brain magnetic resonance imaging abnormalities are seen in less than half of the reported cases. Posterior or multifocal interictal discharges can be seen in patients with EE. No randomized data about treatment are available. Structural epilepsies or coexistent unprovoked seizures other than eating seizures are poor prognostic factors for pharmacological outcome.

scholarly journals Late-onset fibrodysplasia ossificans progressiva with atypical presentation: A case report

2019 ◽  
Vol 23 ◽  
pp. e00134
Author(s):  
Conor M. Cunningham ◽  
J. Matthew Royeca ◽  
Samuel W. King ◽  
Hemant Pandit
Keyword(s):  
Case Report ◽  
Late Onset ◽  
Fibrodysplasia Ossificans Progressiva ◽  
Atypical Presentation

scholarly journals Cryptogenic Late-onset Epileptic Spasms: An Overlooked Syndrome of Early Childhood?

Epilepsia ◽  
2006 ◽  
Vol 47 (6) ◽  
pp. 1035-1042 ◽  
Author(s):  
Monika M. Eisermann ◽  
Dorothee Ville ◽  
Christine Soufflet ◽  
Perrine Plouin ◽  
Catherine Chiron ◽  
...  
Keyword(s):  
Early Childhood ◽  
Late Onset ◽  
Epileptic Spasms

Late-onset Pompe disease with atypical presentation: What else is going on?

2017 ◽  
Vol 120 (1-2) ◽  
pp. S49-S50 ◽  
Author(s):  
Jaya Ganesh ◽  
Maria I. Scarano ◽  
Michael Hardiman ◽  
Priya Kishnani
Keyword(s):  
Pompe Disease ◽  
Late Onset ◽  
Atypical Presentation

scholarly journals High-dose prednisone therapy for infantile spasms and late-onset epileptic spasms in China: The addition of topiramate provides no benefit

Seizure ◽  
2019 ◽  
Vol 71 ◽  
pp. 174-178 ◽  
Author(s):  
Zhaoshi Yi ◽  
Huaping Wu ◽  
Xiongying Yu ◽  
Jian Zha ◽  
Hui Chen ◽  
...  
Keyword(s):  
Late Onset ◽  
Infantile Spasms ◽  
High Dose ◽  
Prednisone Therapy ◽  
Epileptic Spasms ◽  
Dose Prednisone
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