scholarly journals Acquired hemophilia A associated with bullous pemphigoid and multiple myeloma: a case report

2019 ◽  
Vol 77 (2) ◽  
pp. 179-183 ◽  
Author(s):  
Élise Sourdeau ◽  
Sylvain Clauser ◽  
Romain Prud’Homme ◽  
Valérie Bardet ◽  
Leyla Calmette
Keyword(s):  
Multiple Myeloma ◽  
Case Report ◽  
Bullous Pemphigoid ◽  
Hemophilia A ◽  
Acquired Hemophilia A ◽  
Acquired Hemophilia

scholarly journals Diagnosis dan Tata Laksana Acquired Hemophilia A (AHA) dengan Pemfigoid Bulosa

2017 ◽  
Vol 3 (4) ◽  
pp. 218
Author(s):  
Rasco Sandy Sihombing ◽  
Henry Ratno Diono Silalahi ◽  
Hamzah Shatri ◽  
Lugyanti Sukrisman ◽  
Ikhwan Rinaldi ◽  
...  
Keyword(s):  
Case Report ◽  
Factor Viii ◽  
Bullous Pemphigoid ◽  
Skin Disorder ◽  
Hemophilia A ◽  
Coagulation Factor ◽  
Acquired Hemophilia A ◽  
Acquired Hemophilia ◽  
Faktor Viii ◽  
Autoantibody Formation

Acquired hemophilia A merupakan kondisi dimana faktor koagulasi VIII menjadi tidak aktif akibat pembentukan autoantibodi. Kondisi ini dikaitkan dengan kehamilan, keganasan, dan penyakit auitoimun dengan kelainan kulit. Pada kasus ini, seorang wanita berusia 66 tahun, datang dengan keluhan perdarahan paska tindakan yang disertai dengan lesi kulit. Pasien didiagnosis dengan acquired hemophilia A dengan ditemukannya inhibitor faktor VIII terkait dengan pemfigoid bulosa.Kata Kunci: Acquired hemophilia A, diagnosis, pemfigoid bulosa, tata laksana  Diagnosis and Treatment of Acquired Hemophilia A (AHA) with Bullous PemphigoidAcquired hemophilia A is a condition in which coagulation factor VIII become inactive due to autoantibody formation. This condition is related to pregnancy, malignancy, and autoimmune disease with skin disorder. In this case report, a 66 years woman with a post procedural bleeding with skin disorder. Later on, patient diagnosed with acquired hemophilia A with a factor VIII inhibitors related to bullous pemphigoid. Keywords : Acquired hemophilia A, bullous pemphigoid, diagnosis, treatment

scholarly journals Successful Management of Acquired Hemophilia A Associated with Bullous Pemphigoid: A Case Report and Review of the Literature

2017 ◽  
Vol 2017 ◽  
pp. 1-7 ◽  
Author(s):  
Quentin Binet ◽  
Catherine Lambert ◽  
Laurine Sacré ◽  
Stéphane Eeckhoudt ◽  
Cedric Hermans
Keyword(s):  
Bullous Pemphigoid ◽  
Neutralizing Antibodies ◽  
Hemophilia A ◽  
Rare Condition ◽  
Term Treatment ◽  
Acquired Hemophilia A ◽  
Acquired Hemophilia ◽  
Short Term Treatment ◽  
Life Threatening ◽  
Dose Levels

Background. Acquired hemophilia A (AHA) is a rare condition, due to the spontaneous formation of neutralizing antibodies against endogenous factor VIII. About half the cases are associated with pregnancy, postpartum, autoimmune diseases, malignancies, or adverse drug reactions. Symptoms include severe and unexpected bleeding that may prove life-threatening.Case Study. We report a case of AHA associated with bullous pemphigoid (BP), a chronic, autoimmune, subepidermal, blistering skin disease. To our knowledge, this is the 25th documented case of such an association. Following treatment for less than 3 months consisting of methylprednisolone at decreasing dose levels along with four courses of rituximab (monoclonal antibody directed against the CD20 protein), AHA was completely cured and BP well-controlled.Conclusions. This report illustrates a rare association of AHA and BP, supporting the possibility of eradicating the inhibitor with a well-conducted short-term treatment.

Acquired hemophilia A in chronic lymphocytic leukemia: A case report

2019 ◽  
Vol 58 (4) ◽  
pp. 447-448
Author(s):  
Volkan Karakuş ◽  
Egemen Kaya ◽  
Yelda Dere ◽  
Erdal Kurtoğlu
Keyword(s):  
Case Report ◽  
Chronic Lymphocytic Leukemia ◽  
Hemophilia A ◽  
Lymphocytic Leukemia ◽  
Acquired Hemophilia A ◽  
Acquired Hemophilia

scholarly journals Perioperative Management of Acquired Hemophilia A: A Case Report and Review of Literature

2013 ◽  
Vol 3 (3) ◽  
Author(s):  
Yashar Ilkhchoui ◽  
Eugene Koshkin ◽  
Jimmy J Windsor ◽  
Timothy R Petersen ◽  
Matthew Charles ◽  
...  
Keyword(s):  
Case Report ◽  
Perioperative Management ◽  
Hemophilia A ◽  
Review Of Literature ◽  
Acquired Hemophilia A ◽  
Acquired Hemophilia

Acquired hemophilia: a case report

2008 ◽  
Vol 118 (4) ◽  
pp. 228-233
Author(s):  
Mariusz Flisiński ◽  
Jerzy Windyga ◽  
Ewa Stefańska ◽  
Sławomir Huszcza ◽  
Rafał Donderski ◽  
...  
Keyword(s):  
Case Report ◽  
Hemophilia A ◽  
Acquired Hemophilia A ◽  
Acquired Hemophilia
Sign in / Sign up

Export Citation Format

Share Document