Saethre-Chotzen syndrome, Pro136His TWIST mutation, hearing loss, and external and middle ear structural anomalies. Report on a Brazilian family

2010 ◽  
pp. 100611121139056
Author(s):  
Dionísia Lamônica ◽  
Luciana Maximino ◽  
Mariza Feniman ◽  
Greyce Silva ◽  
Sthella Zanchetta ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Middle Ear ◽  
Structural Anomalies

Saethre-Chotzen Syndrome, Pro136His TWIST Mutation, Hearing Loss, and External and Middle Ear Structural Anomalies: Report on a Brazilian Family

2010 ◽  
Vol 47 (5) ◽  
pp. 548-552 ◽  
Author(s):  
Dionísia A.C. Lamônica ◽  
Luciana P. Maximino ◽  
Mariza Ribeiro Feniman ◽  
Greyce K. Silva ◽  
Sthella Zanchetta ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Middle Ear ◽  
Structural Anomalies

scholarly journals Design Study of a Round Window Piezoelectric Transducer for Active Middle Ear Implants

Sensors ◽  
2021 ◽  
Vol 21 (3) ◽  
pp. 946
Author(s):  
Dong Ho Shin
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Middle Ear ◽  
Piezoelectric Transducer ◽  
Round Window ◽  
Piezoelectric Element ◽  
Sensorineural Hearing ◽  
Flat Band ◽  
Middle Ear Implants ◽  
Output Characteristics

This report describes the design of a new piezoelectric transducer for round window (RW)-driven middle ear implants. The transducer consists of a piezoelectric element, gold-coated copper bellows, silicone elastomer (polydimethylsiloxane, PDMS), metal cylinder (tungsten), and titanium housing. The piezoelectric element is fixed to the titanium housing and mechanical resonance is generated by the interaction of the bellows, PDMS, and tungsten cylinder. The dimensions of PDMS and the tungsten cylinder with output characteristics suitable for compensation of sensorineural hearing loss were derived by mechanical vibrational analysis (equivalent mechanical model and finite element analysis (FEA)). Based on the results of FEA, the RW piezoelectric transducer was implemented, and bench tests were performed under no-load conditions to confirm the output characteristics. The transducer generates an average displacement of 219.6 nm in the flat band (0.1–1 kHz); the resonance frequency is 2.3 kHz. To evaluate the output characteristics, the response was compared to that of an earlier transducer. When driven by the same voltage (6 Vp), the flat band displacement averaged 30 nm larger than that of the other transducer, and no anti-resonance was noted. Therefore, we expect that the new transducer can serve as an output device for hearing aids, and that it will improve speech recognition and treat high-frequency sensorineural hearing loss more effectively.

The role of middle ear muscles in the development of resistance to noise induced hearing loss

1994 ◽  
Vol 74 (1-2) ◽  
pp. 22-28 ◽  
Author(s):  
Donald Henderson ◽  
Malini Subramaniam ◽  
Martin Papazian ◽  
Vlasta P. Spongr
Keyword(s):  
Hearing Loss ◽  
Middle Ear ◽  
Noise Induced Hearing Loss ◽  
Development Of Resistance

Ataxia and Hearing Loss Secondary to Perilymphatic Fistula

PEDIATRICS ◽  
1978 ◽  
Vol 61 (2) ◽  
pp. 238-241
Author(s):  
Gerald B. Healy ◽  
Jules M. Friedman ◽  
Joseph DiTroia
Keyword(s):  
Hearing Loss ◽  
Soft Tissue ◽  
Head Trauma ◽  
Middle Ear ◽  
Vestibular System ◽  
Perilymphatic Fistula ◽  
Labyrinthine Fistula ◽  
First Case ◽  
The Absolute ◽  
Physical Findings

Ataxia is rarely attributed to lesions of the peripheral vestibular system. In 1973, the first case of ataxia and hearing loss secondary to a labyrinthine fistula was reported. Until now, this syndrome has not been reported in patients under the age of 10 years. A case is presented of a 5-year-old boy with symptoms of ataxia and hearing loss as well as vertigo and tinnitus after head trauma. Three physical findings appear to be most characterisitic of patients with perilymphatic fistulas: a positive fistula response, positive positional testing with the involved ear down, and evidence of vestibular ataxia when testing station and gait. The absolute diagnosis of perilymphatic fistula can only be established by exploration of the middle ear space. If a fistula is found, it may be sealed with soft tissue and, if this fails, actual stapedectomy may be required.

Use of hearing AIDS

1976 ◽  
Vol 14 (12) ◽  
pp. 45-46
Keyword(s):  
Hearing Loss ◽  
Middle Ear ◽  
Hearing Aids ◽  
Conductive Hearing Loss ◽  
Auditory Training ◽  
Lip Reading ◽  
Conductive Hearing

Up to 3 million people in Britain might be helped by hearing aids.1 2 Most are over 65 years of age, but some are infants. All should be referred to specialist centres for assessment as soon as possible. Hearing aids generally help most in disorders of the middle ear (conductive hearing loss); they can also help those with sensorineural and other forms of hearing loss. The use of an aid often needs to be supplemented by lip reading and other means of auditory training.1 3

A new semi-implantable middle ear implant for sensorineural hearing loss: three-years follow-up in a pilot patient’s group

2017 ◽  
Vol 138 (1) ◽  
pp. 31-35 ◽  
Author(s):  
Maurizio Barbara ◽  
Luigi Volpini ◽  
Chiara Filippi ◽  
Francesca Atturo ◽  
Simonetta Monini
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Middle Ear ◽  
Sensorineural Hearing ◽  
Middle Ear Implant

scholarly journals Classification and clinical features of chronic purulent otitis media

2019 ◽  
Vol 40 (1) ◽  
pp. 66-74
Author(s):  
A. D. Gusakov ◽  
A. A. Gusakova
Keyword(s):  
Hearing Loss ◽  
Otitis Media ◽  
Middle Ear ◽  
Personal Experience ◽  
Clinical Course ◽  
Point Of View ◽  
Control Data ◽  
Retraction Pocket ◽  
Radiological Control ◽  
Chronic Course

In this lecture information on the etiology, pathogenesis, and clinical course of chronic inflammation of the middle ear is systematized. The authors focus on the nature of the manifestations of otitis media, depending on the size and location of the perforation of the eardrum. Based on personal experience and accumulated knowledge, in detail reveal the issue of cholesteatoma, its precursors and possible complications. A lot of attention is paid to methods of examination and interpretation of audiometric and radiological control data. Speaking about the chronic course of the ear disease, the article describes frequently encountered situations such as tympanosclerosis, fistula, etc. In addition to their own point of view on the problem, the authors present literature data reflecting the views of other otorhinolaryngologists. Keywords: chronic otitis, hearing loss, cholesteatoma, retraction pocket, tympanosclerosis.

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