scholarly journals Rapunzel syndrome: a rare form of trichobezoar in the stomach with some extension into the small intestine

2018 ◽  
Vol 27 (3) ◽  
Author(s):  
Anja Blejc Novak ◽  
Živa Zupančič ◽  
Domen Plut ◽  
Diana Gvardijančič ◽  
Matjaž Homan
Keyword(s):  
Small Intestine ◽  
Rare Form ◽  
Rapunzel Syndrome

scholarly journals Rapunzel Syndrome: A Rare Presentation with Giant Gastric Ulcer

2014 ◽  
Vol 2014 ◽  
pp. 1-4 ◽  
Author(s):  
Antonios Athanasiou ◽  
Adamantios Michalinos ◽  
Demetrios Moris ◽  
Eleftherios Spartalis ◽  
Nikolaos Dimitrokallis ◽  
...  
Keyword(s):  
Weight Loss ◽  
Gastric Ulcer ◽  
Small Intestine ◽  
Abdominal Pain ◽  
Young Female ◽  
Rare Form ◽  
Rare Presentation ◽  
Rapunzel Syndrome ◽  
History Of ◽  
Small Intestines

The Rapunzel syndrome refers to an uncommon and rare form of trichobezoar that extends past the stomach into the small intestines. The Rapunzel syndrome is usually found in young female patients with a history of psychiatric disorders, mainly trichotillomania and trichophagia. We describe a case of Rapunzel syndrome in a 15-year-old girl who presented with abdominal pain, vomiting, and weight loss. We performed a surgical laparotomy and successfully removed a huge trichobezoar extending into the small intestine.

scholarly journals Rapunzel syndrome

2012 ◽  
Vol 69 (8) ◽  
pp. 717-720 ◽  
Author(s):  
Gordana Petrovic ◽  
Aleksandar Nagorni ◽  
Goran Bjelakovic ◽  
Daniela Benedeto-Stojanov ◽  
Biljana Radovanovic-Dinic ◽  
...  
Keyword(s):  
Computed Tomography ◽  
Foreign Bodies ◽  
Psychiatric Treatment ◽  
Abdominal Mass ◽  
Rare Form ◽  
Rapunzel Syndrome ◽  
Younger Women ◽  
Palpable Abdominal Mass ◽  
Over Time

Introduction. Trichobezoars are foreign bodies in gastrointestinal tract, composed of hair. They occur mainly in children and adolescents suffering from trichotillophagia. They commonly occur in the stomach, but as they enlarge over time, they can extend through the pylorus into distal parts of the small intestine resembling a tail. This rare form of trichobezoar is named Rapunzel syndrome. Case report. We presented a 19-year-old female patient, who suffered from trichotillomania and trichotillophagia, which led to trichobezoar formation. Intra-abdominal tumour was suspected after initial clinical examination. Abdominal echosonography, endoscopy and abdominal computed tomography (CT scan) in the pre-operational period revealed trichobezoar formation. The patient was operated on and subjected to further psychiatric treatment. Conclusion. Trichobezoar should be differentially diagnostically taken into consideration in younger women with abdominal pain, nausea, vomiting, palpable abdominal mass and psychiatric disorders. Most trichobezoar cases require surgical treatment, whereas the patients need long-term psychiatric treatment and monitoring.

scholarly journals Jejunal perforation secondary to trichobezoar (Rapunzel syndrome): a rare presentation

2019 ◽  
Vol 6 (8) ◽  
pp. 3002
Author(s):  
Jitendra Kumar Saroj ◽  
Arshad Ahmad ◽  
Pankaj Kumar ◽  
Sandeep Verma
Keyword(s):  
Small Intestine ◽  
Psychiatric Illness ◽  
Adolescent Females ◽  
The Other ◽  
Surgical Removal ◽  
Gi Tract ◽  
Rare Presentation ◽  
Rapunzel Syndrome ◽  
Protein Losing Enteropathy ◽  
Mucosal Erosion

Trichobezoar is a rare disorder. It usually occurs in young and adolescent females associated with some psychiatric illness. Trichobezoar usually accumulate in the GI tract and most commonly in stomach but it can migrate through the pylorus into the jejunum, ileum and colon. Once the bezoars extends from the stomach into the jejunum or further on, it is referred to as “Rapunzel syndrome”. Though initially asymptomatic but over a period of time it may cause gastric mucosal erosion, ulceration, and perforation of the stomach or the small intestine. If unrecognized, tichobezoar may present with intussusceptions, obstructive jaundice, protein-losing enteropathy, pancreatitis and even death. Small trichobezoar may be extracted by endoscopic fragmentation but bezoars like Rapunzel Syndrome, on the other hand, need open surgical removal. Counseling by a psychiatrist is an important part of management to prevent recurrence.

scholarly journals Rapunzel syndrome

2015 ◽  
Vol 3 (2) ◽  
pp. 79-81 ◽  
Author(s):  
Ahmed Youssef Altonbary ◽  
Monir Hussein Bahgat
Keyword(s):  
Gastrointestinal Tract ◽  
Small Bowel ◽  
Psychiatric Disorders ◽  
Rare Form ◽  
Rapunzel Syndrome ◽  
Long Tail ◽  
Documented Case ◽  
Vegetable Fibers ◽  
Gastric Trichobezoar

Abstract Bezoars are concretions of human or vegetable fibers that accumulate in the gastrointestinal tract. Trichobezoars are common in patients with underlying psychiatric disorders who chew and swallow their own hair. Rapunzel syndrome is a rare form of gastric trichobezoar with a long tail extending into the small bowel. This syndrome was first described in 1968 by Vaughan et al. and since then till date just 64 cases have been described in the literature. We present the only documented case with Rapunzel syndrome in Egypt.

scholarly journals Unusual trichobezor of stomach and intestines as a manifestation of Rapunzel syndrome: a rare case report

2019 ◽  
Vol 6 (12) ◽  
pp. 4569
Author(s):  
Tejinder Pal Singh Sodhi ◽  
Sameer Pundeer ◽  
Maneshwar Singh Utaal ◽  
Kirti Savyasacchi Goyal
Keyword(s):  
Computed Tomography ◽  
Rare Case ◽  
Proximal Jejunum ◽  
Rare Form ◽  
Rapunzel Syndrome ◽  
Contrast Enhanced ◽  
Rare Case Report ◽  
Enhanced Computed Tomography ◽  
Contrast Enhanced Computed Tomography ◽  
Entire Stomach

Rapunzel syndrome is a rare form of trichobezoar with accumulation of large amounts of hair extending from stomach to variable portion of small intestine. An 18 year old girl was brought to surgery opd with complaints of vomiting on and off since 3 months. Contrast enhanced computed tomography abdomen showed a bezoar extending from stomach into the duodenum and proximal jejunum suggestive of Rapunzel syndrome with 3rd and 4th part of duodenum along with duodenojejunal junction. On laparotomy, a trichobezoar occupying the entire stomach measured 100 cm in length and 700 grams in weight. Since the mass formed in Rapunzel syndrome is generally too large to be removed endoscopically or laparoscopically, it requires removal by open gastrostomy. 

scholarly journals Revisión sistemática del Síndrome de Rapunzel

2020 ◽  
Vol 31 (1) ◽  
Author(s):  
Reinhard Janssen-Aguilar ◽  
Andrea Rochel-Pérez ◽  
Osman Jesús Cuevas-Koh ◽  
Kassandra Desiré Santos-Zaldivar ◽  
Melissa Rodríguez-Cuevas ◽  
...  
Keyword(s):  
Small Intestine ◽  
Case Report ◽  
Clinical Case ◽  
Psychiatric Treatment ◽  
Clinical Manifestations ◽  
Surgical Removal ◽  
Age Group ◽  
Rapunzel Syndrome ◽  
Revisión Sistemática ◽  
Cuerpos Extraños

RESUMEN. Introducción: El síndrome de Rapunzel es una forma inusual de tricobezoar gástrico, se localiza desde el estómago llegando a traspasar el píloro y extendiéndose hasta el intestino delgado y/o colon derecho. Se le llama bezoar a la formación de cuerpos extraños, debido a la ingestión de uno o varios materiales no digeribles. El tricobezoar, uno de los bezoares que más se presentan en la práctica clínica consisten en una masa formada por cabello debido a la ingestión de este.Objetivo: describir la frecuencia de signos y síntomas del síndrome de Rapunzel en los reportes de caso y ofrecer una comparación en edad pediátrica y adulta.Método. Revisión sistemática en la base de datos PubMed, Google Académico, EBSCO y Scopus, empleando los términos “Rapunzel syndrome” AND “case report” OR “Clinical case”Resultados. Un total de 110 artículos de reporte de caso fueron analizados, encontrando diferencias por sexo y edad. La tricotilomanía se distribuyó sin predominancia por grupo de edad. Se identificaron diferencias en el reporte de algunas manifestaciones clínicas al analizarlas por grupo de edad, incluyendo diarrea, constipación, vómitos y dolor abdominal. Los casos recidivantes representaron un 9%.Conclusiones: El síndrome de Rapunzel es una entidad que se encuentra en pacientes con patologías psiquiátricas como la tricotilomanía y la tricofagia. Es más frecuente en mujeres que en hombres. La técnica diagnóstica por elección fue la endoscopía y el tratamiento elegido incluyó la remoción quirúrgica con psicoterapia. Palabras clave: síndrome de Rapunzel, signos y síntomas, bezoar, diagnóstico, tricotilomanía, adolescencia. Introduction: Rapunzel syndrome is an unusual type of gastric trichobezoar, which is located from the stomach through the pylorus and extends into the small intestine and/or right colon. Tricobezoar is a collection of foreign bodies that can form in the stomach, small intestine or colon, due to the ingestion of one or more indigestible materials. trichobezoar, one of the most present bezoars in Clinical practice consists of a mass formed by hair due to the ingestion of it, either consciously or unconsciously. Objective: To compile case reports to identify and analyze little-known aspects of Rapunzel syndrome, as well as patient characteristics along with the best and most documented methods of diagnosis and treatment. Method. Systematic review in the Pubmed, Google Scholar, EBSCO and Scopus databases using as search terms: "Rapunzel syndrome" AND "case report" OR "Clinical case" Results: A total of 110 case report articles were analyzed, finding differences by sex and age. Trichotillomania was distributed without predominance by age group. Differences were identified in the reporting of some clinical manifestations when analyzed by age group, including diarrhea, constipation, vomiting and abdominal pain. Recidivist cases were 9%. Conclusion: Throughout the review of reported cases, we found that part of the patient's recovery includes psychiatric treatment; Rapunzel syndrome is not a mental disorder, however, both trichotillomania and pica as factors of it. The entity is more frequent in women than in men, the technique for diagnosis by choice was the endoscopy and the chosen treatment included surgical removal with psychotherapy. Keywords: Rapunzel Syndrome, Signs and Symptoms, Bezoar, Diagnosis Trichotillomania, Adolescence.

scholarly journals RAPUNZEL SYNDROME IN A 2 YEAR OLD FEMALE CHILD: A RARE PRESENTATION OF A RARE DISEASE.

2020 ◽  
pp. 1-2
Author(s):  
Tapan Patel ◽  
Shivani Patel ◽  
Shreya Dholakia
Keyword(s):  
Small Intestine ◽  
Rare Disease ◽  
Rare Variant ◽  
Rare Case ◽  
Female Child ◽  
Rare Presentation ◽  
Rapunzel Syndrome

Rapunzel syndrome is a very rare variant of trichobezoar in which the mass in stomach extends into small intestine and sometimes into the colon. Here we report an extremely rare case of a 55 centimeter long trichobezoar in a female child at an age of 2 years and 4 months. This is the youngest reported case of Rapunzel syndrome.

scholarly journals A giant trichobezoar with Rapunzel syndrome: a case report

2018 ◽  
Vol 5 (8) ◽  
pp. 2939
Author(s):  
Gaurav Wadhawan ◽  
Kailash C. Vyas ◽  
Ravi Bhatia
Keyword(s):  
Small Intestine ◽  
Case Report ◽  
Psychiatric Disorder ◽  
Children And Adolescents ◽  
Intestinal Tract ◽  
Foreign Material ◽  
Short Segment ◽  
Rapunzel Syndrome

Bezoar is a conglomeration of foreign material in the intestinal tract. Trichobezoar is accumulation of hairs in the gastric chamber and Rapunzel Syndrome is accumulation of hairs in the small intestine. This commonly occurs in children and adolescents who are commonly suffering from a psychiatric disorder called Trichotillomania in which they have the habit of eating hairs which is called Trichophagia. Authors are presenting a case of a fourteen years old girl who kept on eating her hairs and nails to develop a giant Trichobezoar with a short segment of Rapunzel Syndrome.

scholarly journals Rapunzel syndrome: how to orient the diagnosis

2018 ◽  
Vol 10 (2) ◽  
Author(s):  
Enrico Finale ◽  
Piergiorgio Franceschini ◽  
Cesare Danesino ◽  
Michelangelo Barbaglia ◽  
Andrea Guala
Keyword(s):  
Surgical Intervention ◽  
Ectodermal Dysplasia ◽  
Clinical Suspicion ◽  
Clinical Diagnostics ◽  
Surgical Removal ◽  
Rare Form ◽  
Rapunzel Syndrome ◽  
History Of ◽  
Genetic Consultation

Rapunzel syndrome is a rare form of tricobezoar with a tail extending from the stomach into the small bowel; surgical removal is generally required. About 60 cases have been reported and described in the literature since 1968. We present the case of an 8-year-old girl who, during the course of a genetic consultation, was initially assigned with a clinical suspicion of ectodermal dysplasia. Surgical intervention, which resulted in the extraction of a tricobezoar of enormous size and extension, led us to the diagnosis of Rapunzel syndrome. The possibility of a tricobezoar should be considered in all cases of adolescent patients who present signs of intestinal occlusion or sub-occlusion, suffer from psychiatric disorders, and have a history of trichotillomania. Endoscopic methodology, medical imaging and clinical diagnostics are fundamental for a differential diagnosis. Psychiatric follow-up is advised to prevent recurrence.

scholarly journals Rapunzel syndrome – A rare form of trichobezoar: A case report

2013 ◽  
Vol 04 (01) ◽  
pp. 019-021
Author(s):  
Thayumanavan L. ◽  
Rajkumar K. ◽  
Kennan M.
Keyword(s):  
Hair Pulling ◽  
Rare Form ◽  
Rapunzel Syndrome ◽  
Long Tail ◽  
Upper Gi ◽  
Gastric Trichobezoar ◽  
Number Of Patients ◽  
History Of ◽  
Upper Gi Endoscopy ◽  
The Subject

ABSTRACTHair ball in the GI tract is called trichobezoar and the Rapunzel syndrome is a very rare form of trichobezoar found in patients with psychiatric illness in whom the ingested hair extends from the stomach into the small intestine. Trichotillomania (hair pulling) and trichophagia (chewing of hair) are intrinsic to the development of Rapunzel syndrome. A small number of patients have been reported in whom the gastric trichobezoar has a long tail and extends throughout the small bowel to the cecum. This condition, known as the Rapunzel syndrome, occurs almost exclusively in young girls. We report a case Rapunzel syndrome who presented with history of upper GI obstruction and weight loss. Upper GI endoscopy revealed a large trichobezoar occupying fundus of stomach extending along the whole stomach into duodenum beyond its 3rd part. It was treated successfully with surgery followed by psychiatric consultation. We will review the literature on the subject as well. (J Dig Endosc 2013;4(1):19–21)

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