Primary Intestinal Lymphangiectasia: A case report

2019 ◽  
Vol 7 (0) ◽  
Author(s):  
Ridwaan Albeiruti ◽  
Patrick Gleeson ◽  
Ted Kelbel ◽  
Tracy Fausnight
Keyword(s):  
Case Report ◽  
Intestinal Lymphangiectasia

scholarly journals Intestinal lymphangiectasia: case report

2019 ◽  
Vol 6 (5) ◽  
pp. 1678
Author(s):  
Reham Mohmmad Aljohnei ◽  
Hawazen Yousef Abdullah Alani
Keyword(s):  
Case Report ◽  
Rare Disease ◽  
Present Report ◽  
Abdominal Distention ◽  
Intestinal Lymphangiectasia ◽  
Peripheral Edema ◽  
Long Duration ◽  
White Spots ◽  
Intestinal Lymphatics ◽  
History Of

Primary intestinal lymphangiectasia (PIL) was first described by Waldmann et al, in 1961. PIL is a rare disease with several hundred reported cases. It is rarely reported in adults because it is presumably a congenital disorder and when present in adults it typically produces a long duration of manifestation such as diarrhea, abdominal distention from ascites, and peripheral edema. This disorder is characterized by markedly dilated intestinal lymphatics, hypoproteinemia, generalized edema, lymphocytopenia hypogammaglobinemia, and immunologic anomalies. The loss of protein into the from dilated intestinal lymphatics leads to the development of hypoproteinemia in these patients and its demonstration is important in the diagnosis of intestinal lymphangiectasia. The disease can be secondary to congenital, secondary or idiopathic defects in the formation of the lymphatic ducts. In the present report, we describe a case of 15 years old female presented to our hospital with history of generalized edema, bilateral hand spasm, and diarrhea. Endoscopy of the patient revealed White spots (dilated lacteals), white nodules, and submucosal elevations were observed. Changes suggestive of the disease includes White villi and/or spots (dilated lacteals), white nodules, and submucosal elevations are observed. Xanthomata’s plaques are often visualized, there are no specific treatments for patients with PIL. treatment of patients with primary intestinal lymphangiectasia involves control of symptoms with the use of dietary, pharmaceutical, and behavioral modifications.

Digital clubbing in primary intestinal lymphangiectasia: a case report

2010 ◽  
Vol 160 (15-16) ◽  
pp. 431-436 ◽  
Author(s):  
Christian J. Wiedermann ◽  
Michael Kob ◽  
Stefano Benvenuti ◽  
Rodolfo Carella ◽  
Lucio Lucchin ◽  
...  
Keyword(s):  
Case Report ◽  
Intestinal Lymphangiectasia ◽  
Digital Clubbing

scholarly journals Tuberous sclerosis complex presenting as primary intestinal lymphangiectasia: A case report

2020 ◽  
Vol 8 (10) ◽  
pp. 1995-2000
Author(s):  
Wen-Hao Lin ◽  
Zu-Han Zhang ◽  
Hong-Li Wang ◽  
Lu Ren ◽  
Lan-Lan Geng
Keyword(s):  
Case Report ◽  
Tuberous Sclerosis ◽  
Tuberous Sclerosis Complex ◽  
Intestinal Lymphangiectasia

A Preterm Infant with Intestinal Lymphangiectasia: A Diagnostic Dilemma

2009 ◽  
Vol 28 (1) ◽  
pp. 29-36 ◽  
Author(s):  
Karen McDonald ◽  
Christina Bears
Keyword(s):  
Case Report ◽  
Preterm Infant ◽  
Rare Disease ◽  
Current Literature ◽  
Lymphatic System ◽  
Diagnostic Workup ◽  
Intestinal Lymphangiectasia ◽  
Proper Treatment ◽  
Diagnostic Dilemma ◽  
Peripheral Edema

Intestinal lymphangiectasia (IL) is a potentially fatal disorder of the lymphatic system if it is not recognized and proper treatment initiated. The disease is characterized by lymphocytopenia, peripheral edema, and hypoalbuminemia. Because IL is a rare disease, the symptoms, diagnostic workup, and treatment are unfamiliar to many clinicians. Current literature documents only a few reported cases of IL in a preterm infant. This case report of a preterm infant reviews history, symptomatology, and the diagnostic workup performed. The steps in making the diagnosis, the treatment, and the prognosis of this condition are also presented.

scholarly journals Congenital intestinal lymphangiectasia: a case report

2019 ◽  
Vol 9 (3) ◽  
pp. 305-308
Author(s):  
Giuliana Aroso ◽  
Maria Cavalcante ◽  
Ivana Ferro
Keyword(s):  
Case Report ◽  
Intestinal Lymphangiectasia

Refractory primary intestinal lymphangiectasia effectively managed with subcutaneous octreotide

2021 ◽  
Vol 14 (4) ◽  
pp. e238457
Author(s):  
Amir Halim ◽  
Philippa Youd ◽  
Jill Thorpe ◽  
Irfan Halim
Keyword(s):  
Case Report ◽  
Gastrointestinal Symptoms ◽  
Medium Chain Triglyceride ◽  
Well Being ◽  
Intestinal Lymphangiectasia ◽  
Curative Therapy ◽  
Medium Chain ◽  
History Of ◽  
Medium Chain Triglyceride Diet ◽  
Conventional Medium

This case report describes a young man with a history of lymphoedema and long-standing gastrointestinal symptoms since childhood. After undergoing extensive investigations, he was diagnosed with primary intestinal lymphangiectasia (IL). The patient’s condition was refractory to conventional medium-chain triglyceride diet but responded well to treatment with subcutaneous octreotide. We have shown octreotide to be effective in improving the pathological effects of primary IL, associated with improved clinical well-being and serology, but it is not a curative therapy.

Primary Intestinal Lymphangiectasia in an Infant with a History of Cowʼs Milk Protein Allergy—A Case Report

2009 ◽  
Vol 104 ◽  
pp. S550-S551
Author(s):  
Doron Kahana ◽  
Dave Paek ◽  
Kenny Kwong ◽  
Samuel French ◽  
George Gershman
Keyword(s):  
Case Report ◽  
Milk Protein ◽  
Intestinal Lymphangiectasia ◽  
History Of

Abdominal Lymphangiomatosis With Intestinal Lymphangiectasia Diagnosed by Magnetic Resonance Lymphangiography: A Case Report

2018 ◽  
Vol 47 (3) ◽  
pp. 200-202 ◽  
Author(s):  
Jineesh Valakada ◽  
Kumble S. Madhusudhan ◽  
Gyan Ranjan ◽  
Pramod Kumar Garg ◽  
Raju Sharma ◽  
...  
Keyword(s):  
Case Report ◽  
Magnetic Resonance ◽  
Intestinal Lymphangiectasia
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