Bone Morphogenetic Protein Type II Receptor Mutations Causing Protein Misfolding in Heritable Pulmonary Arterial Hypertension

W. Li; B. J. Dunmore; N. W. Morrell

doi:10.1513/pats.201002-024aw

Bone Morphogenetic Protein Type II Receptor Mutations Causing Protein Misfolding in Heritable Pulmonary Arterial Hypertension

Proceedings of the American Thoracic Society ◽

10.1513/pats.201002-024aw ◽

2010 ◽

Vol 7 (6) ◽

pp. 395-398 ◽

Cited By ~ 23

Author(s):

W. Li ◽

B. J. Dunmore ◽

N. W. Morrell

Keyword(s):

Pulmonary Arterial Hypertension ◽

Arterial Hypertension ◽

Bone Morphogenetic Protein ◽

Protein Misfolding ◽

Type Ii ◽

Morphogenetic Protein ◽

Pulmonary Arterial ◽

Heritable Pulmonary Arterial Hypertension

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Role of Bone Morphogenetic Protein Type II Receptor Signaling in Pulmonary Arterial Hypertension

Cardiovascular Pharmacology Open Access ◽

10.4172/2329-6607.1000e120 ◽

2013 ◽

Vol 02 (04) ◽

Author(s):

Qiwei Yang Miranda Sun

Keyword(s):

Pulmonary Arterial Hypertension ◽

Arterial Hypertension ◽

Bone Morphogenetic Protein ◽

Type Ii ◽

Receptor Signaling ◽

Morphogenetic Protein ◽

Pulmonary Arterial

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A10450 Cathepsin L Contributes to the development of pulmonary arterial hypertension via degradation of Bone Morphogenetic Protein Type II Receptor

Journal of Hypertension ◽

10.1097/01.hjh.0000548227.65957.e8 ◽

2018 ◽

Vol 36 ◽

pp. e59 ◽

Cited By ~ 1

Author(s):

Zhouyf Peng

Keyword(s):

Pulmonary Arterial Hypertension ◽

Arterial Hypertension ◽

Bone Morphogenetic Protein ◽

Cathepsin L ◽

Type Ii ◽

Morphogenetic Protein ◽

Pulmonary Arterial

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Bone Morphogenetic Protein Receptor Type II and Inflammation Are Bringing Old Concepts into the New Pulmonary Arterial Hypertension World

American Journal of Respiratory and Critical Care Medicine ◽

10.1164/rccm.201506-1115ed ◽

2015 ◽

Vol 192 (7) ◽

pp. 777-779 ◽

Cited By ~ 5

Author(s):

Frédéric Perros ◽

Sébastien Bonnet

Keyword(s):

Pulmonary Arterial Hypertension ◽

Arterial Hypertension ◽

Bone Morphogenetic Protein ◽

Receptor Type ◽

Type Ii ◽

Bone Morphogenetic Protein Receptor ◽

Protein Receptor ◽

Morphogenetic Protein ◽

Pulmonary Arterial

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BETA-ARRESTINS REGULATE SIGNALING BY BONE MORPHOGENETIC PROTEIN TYPE II RECEPTOR IN PULMONARY ARTERIAL HYPERTENSION

Journal of the American College of Cardiology ◽

10.1016/s0735-1097(11)62046-9 ◽

2011 ◽

Vol 57 (14) ◽

pp. E2046 ◽

Cited By ~ 2

Author(s):

Sudarshan Rajagopal ◽

Jeff Kovacs ◽

Cristian Badea ◽

G. Allan Johnson ◽

Howard A. Rockman ◽

...

Keyword(s):

Pulmonary Arterial Hypertension ◽

Arterial Hypertension ◽

Bone Morphogenetic Protein ◽

Type Ii ◽

Morphogenetic Protein ◽

Pulmonary Arterial ◽

Beta Arrestins

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The Relationship Of Bone Morphogenetic Protein Receptor Type II (BMPR2) Mutations With Reversible Versus Non-Reversible Disease In Pulmonary Arterial Hypertension

10.1164/ajrccm-conference.2011.183.1_meetingabstracts.a6128 ◽

2011 ◽

Author(s):

Benjamin P. Smith ◽

Lynette M. Brown ◽

D H. Best ◽

Charles G. Elliott ◽

David S. Collingridge

Keyword(s):

Pulmonary Arterial Hypertension ◽

Arterial Hypertension ◽

Bone Morphogenetic Protein ◽

Type Ii ◽

Bone Morphogenetic Protein Receptor ◽

Protein Receptor ◽

Morphogenetic Protein ◽

Pulmonary Arterial ◽

Relationship Of ◽

The Relationship

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Estrogen Metabolite 16α-Hydroxyestrone Exacerbates Bone Morphogenetic Protein Receptor Type II–Associated Pulmonary Arterial Hypertension Through MicroRNA-29–Mediated Modulation of Cellular Metabolism

Circulation ◽

10.1161/circulationaha.115.016133 ◽

2016 ◽

Vol 133 (1) ◽

pp. 82-97 ◽

Cited By ~ 54

Author(s):

Xinping Chen ◽

Megha Talati ◽

Joshua P. Fessel ◽

Anna R. Hemnes ◽

Santhi Gladson ◽

...

Keyword(s):

Pulmonary Arterial Hypertension ◽

Arterial Hypertension ◽

Bone Morphogenetic Protein ◽

Cellular Metabolism ◽

Receptor Type ◽

Type Ii ◽

Bone Morphogenetic Protein Receptor ◽

Protein Receptor ◽

Morphogenetic Protein ◽

Pulmonary Arterial

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Defective cellular trafficking of the bone morphogenetic protein receptor type II by mutations underlying familial pulmonary arterial hypertension

Gene ◽

10.1016/j.gene.2015.02.038 ◽

2015 ◽

Vol 561 (1) ◽

pp. 148-156 ◽

Cited By ~ 16

Author(s):

Anne John ◽

Praseetha Kizhakkedath ◽

Lihadh Al-Gazali ◽

Bassam R. Ali

Keyword(s):

Pulmonary Arterial Hypertension ◽

Arterial Hypertension ◽

Bone Morphogenetic Protein ◽

Receptor Type ◽

Cellular Trafficking ◽

Type Ii ◽

Bone Morphogenetic Protein Receptor ◽

Protein Receptor ◽

Morphogenetic Protein ◽

Pulmonary Arterial

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Failure of bone morphogenetic protein receptor trafficking in pulmonary arterial hypertension: potential for rescue

Human Molecular Genetics ◽

10.1093/hmg/ddn214 ◽

2008 ◽

Vol 17 (20) ◽

pp. 3180-3190 ◽

Cited By ~ 57

Author(s):

A. Sobolewski ◽

N. Rudarakanchana ◽

P. D. Upton ◽

J. Yang ◽

T. K. Crilley ◽

...

Keyword(s):

Pulmonary Arterial Hypertension ◽

Arterial Hypertension ◽

Bone Morphogenetic Protein ◽

Receptor Trafficking ◽

Bone Morphogenetic Protein Receptor ◽

Protein Receptor ◽

Morphogenetic Protein ◽

Pulmonary Arterial

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Dysregulated Bone Morphogenetic Protein Signaling in Monocrotaline-Induced Pulmonary Arterial Hypertension

Arteriosclerosis Thrombosis and Vascular Biology ◽

10.1161/atvbaha.107.141200 ◽

2007 ◽

Vol 27 (5) ◽

pp. 1072-1078 ◽

Cited By ~ 97

Author(s):

Rory E. Morty ◽

Bozena Nejman ◽

Grazyna Kwapiszewska ◽

Matthias Hecker ◽

Anka Zakrzewicz ◽

...

Keyword(s):

Pulmonary Arterial Hypertension ◽

Arterial Hypertension ◽

Bone Morphogenetic Protein ◽

Protein Signaling ◽

Bone Morphogenetic Protein Signaling ◽

Morphogenetic Protein ◽

Pulmonary Arterial

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In Vivo Interactions With Serotonin And Bone Morphogenetic Protein Receptor 2 Deficiency In The Development Of Pulmonary Arterial Hypertension

10.1164/ajrccm-conference.2010.181.1_meetingabstracts.a6312 ◽

2010 ◽

Author(s):

Neil A. MacRitchie ◽

Yvonne Dempsie ◽

Margaret Nilsen ◽

Nicholas W. Morrell ◽

Margaret R. MacLean

Keyword(s):

Pulmonary Arterial Hypertension ◽

Arterial Hypertension ◽

Bone Morphogenetic Protein ◽

Bone Morphogenetic Protein Receptor ◽

Protein Receptor ◽

Morphogenetic Protein ◽

Pulmonary Arterial

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