scholarly journals Acute Acalculous Cholecystitis: A Rare Presentation of Autoimmune Hepatitis and Primary Sclerosing Cholangitis Overlap Syndrome

2018 ◽  
Vol 9 (10) ◽  
pp. 332-337
Author(s):  
Feng Yin ◽  
Peter V. Draganov ◽  
Jinping Lai ◽  
Steven J. Hughes ◽  
Roberto J. Firpi-Morell ◽  
...  
Keyword(s):  
Autoimmune Hepatitis ◽  
Primary Sclerosing Cholangitis ◽  
Sclerosing Cholangitis ◽  
Acalculous Cholecystitis ◽  
Overlap Syndrome ◽  
Acute Acalculous Cholecystitis ◽  
Rare Presentation

scholarly journals Autoimmune Hepatitis and Primary Sclerosing Cholangitis: An Overlap Syndrome Resistant to Azathioprine and Intolerant to Tacrolimus with Sepsis Mimicking Flare UP-A Clinical Dilemma

2020 ◽  
Vol 07 (02) ◽  
pp. 11-14
Author(s):  
Sharon T Mathews ◽  
Keyword(s):  
Liver Disease ◽  
Autoimmune Hepatitis ◽  
Primary Sclerosing Cholangitis ◽  
Sclerosing Cholangitis ◽  
Kidney Injury ◽  
Scoring Systems ◽  
Overlap Syndrome ◽  
Rare Presentation ◽  
First Line Therapy ◽  
Progressive Liver Disease

Patients with autoimmune liver disease in a frequency of 7% -18% fit into the diagnostic criteria for more than one condition. Up to 12.5% of Autoimmune Hepatitis (AIH) and Primary Sclerosing Cholangitis (PSC) cohorts have a label of AIH/PSC overlap. There can be an unpredictable interval of many years between the diagnosis of the two conditions. There are scoring systems but no established criteria for the diagnosis of AIH/PSC overlap. Therefore, a diagnosis based on combination of biochemistry, autoantibody profile, cholangiogram, and liver histologyis made. Histopathology staging of AIH/PSC overlap influences therapeutic options and prognosis. There is beneficial role of immunosuppression, even though there is a higher relapse rate and evidence of progressive liver disease despite immunosuppression in some cases. Liver related outcomes in this overlap are better than PSC alone but are poorer than AIH. We herein report a rare presentation of an overlap syndrome with AIH and PSC in a patient in whom, treatment with first line therapy showed incomplete response and the salvage therapy was not tolerated, presenting with Acute Kidney Injury (AKI) and a clinical picture of sepsis resembling AIH flare.

scholarly journals Autoimmune Hepatitis-Primary Sclerosing Cholangitis Overlap Syndrome Complicated by Crohn’s Disease

Digestion ◽  
2010 ◽  
Vol 82 (1) ◽  
pp. 24-26 ◽  
Author(s):  
Talha A. Malik ◽  
Alexandra M. Gutierrez ◽  
Brendan McGuire ◽  
Jessica G. Zarzour ◽  
Faisal Mukhtar ◽  
...  
Keyword(s):  
Crohn’S Disease ◽  
Crohn's Disease ◽  
Autoimmune Hepatitis ◽  
Primary Sclerosing Cholangitis ◽  
Sclerosing Cholangitis ◽  
Overlap Syndrome

scholarly journals Light chain amyloidosis presenting with autoimmune hepatitis-primary sclerosing cholangitis overlap syndrome

2020 ◽  
Vol 1 (1) ◽  
pp. e0013
Author(s):  
Hammad Shabir Chaudhry ◽  
Fateen Ata ◽  
Muhammad Yasir ◽  
Rohit Sharma ◽  
Mohammed Gaber ◽  
...  
Keyword(s):  
Autoimmune Hepatitis ◽  
Primary Sclerosing Cholangitis ◽  
Light Chain ◽  
Sclerosing Cholangitis ◽  
Overlap Syndrome ◽  
Light Chain Amyloidosis

scholarly journals Innumerable Liver Masses in a Patient with Autoimmune Hepatitis and Primary Sclerosing Cholangitis Overlap Syndrome

2017 ◽  
Vol 18 ◽  
pp. 131-135
Author(s):  
Alireza Gharibpoor ◽  
Fariborz Mansour-Ghanaei ◽  
Mahbobe Sadeghi ◽  
Faeze Gharibpoor ◽  
Farahnaz Joukar ◽  
...  
Keyword(s):  
Autoimmune Hepatitis ◽  
Primary Sclerosing Cholangitis ◽  
Sclerosing Cholangitis ◽  
Overlap Syndrome

Clinical case: autoimmune hepatitis and primary sclerosing cholangitis overlap syndrome

Therapy ◽  
2021 ◽  
Vol 5_2021 ◽  
pp. 127-135
Author(s):  
Аlieva А.М. Аlieva ◽  
Аlmazova I.I. Аlmazova ◽  
Brutskaya L.А. Brutskaya ◽  
Baykova I.Е. Baykova I ◽  
Аrakelyan R.А. Аrakelyan ◽  
...  
Keyword(s):  
Autoimmune Hepatitis ◽  
Primary Sclerosing Cholangitis ◽  
Sclerosing Cholangitis ◽  
Clinical Case ◽  
Overlap Syndrome
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