scholarly journals Lip And Palate Reconstruction On Median Cerebrofacial Malformation Patient

1970 ◽  
Vol 2 (2) ◽  
Author(s):  
Nur Anindhawati ◽  
Prasetyanugraheni Kreshanti ◽  
Siti Handayani ◽  
Kristaninta Bangun
Keyword(s):  
Cleft Lip ◽  
Cleft Lip And Palate ◽  
Perinatal Care ◽  
Functional Limitation ◽  
Clinical Manifestations ◽  
Care Patient ◽  
Post Surgery ◽  
First Case ◽  
Patient Reported ◽  
Median Cleft

Background: Median cerebrofacial malformations are developmental anomalies of the midline brain and facial structures. The clinical manifestations ranges from holoprosencephaly with agenesis of central facial structures, to those seen in median facial dysplasia. Patients who survive are usually born with severe functional limitation and die during infancy. Nowadays, with improved perinatal care, patient with severe midline craniofacial abnormalities can be expected to live longer. The purpose of this paper is to show how reconstruction of the lip and palate on patient with median cerebrofacial malformation is done. Patient and Method: Reporting 2 cases of child with cleft median cerebrofacial malformations. First case was a 2 year-old child with complete median cleft lip and palate. Clinical examinations and CT scan revealed a holoprosencephaly. She was also diagnosed with laryngomalacia. The second case was a 4 month-old patient with median cleft lip and palate also microcephaly. We performed labioplasty in both patients and did the palatoplasty in the first patient. Result: Both cases showed no sign of complication after the operation. They both discharged one day after the operation. The first patient reported dead 1 week after the surgery at home. The cause was unknown. Discussion: Disturbed maxillary growth is postulated to be caused by the manipulation and suturing of the maxillary vomer, and scarring of the dentoalveoli post-surgery. Another contributing factor is the intrinsic tissue deficiency. Summary: With proper perinatal care and holistic teamwork that expand the survival rate we expect those with the best prognosis deserve to appear as normal as possible. Keywords: Holoprosencephaly, median facial dysplasia, median cleft lip and palate  

Outcome assessment in cleft lip and palate surgery

2021 ◽  
pp. 761-766
Author(s):  
Marc C. Swan ◽  
Conrad J. Harrison ◽  
Tim E.E. Goodacre
Keyword(s):  
Outcome Assessment ◽  
Cleft Lip ◽  
Cleft Lip And Palate ◽  
Outcome Evaluation ◽  
Future Trends ◽  
Facial Growth ◽  
Patient Reported ◽  
Patient Reported Measures ◽  
High Degree ◽  
Over Time

Outcome assessment for cleft management is complex due to the diverse elements of function affected by the condition, and the variation in effect on patients over time. Methods of assessment are broadly separated into objectively measurable variables that can be independently validated, and patient-reported measures that are necessarily more subjective. Validated tools to evaluate outcomes are now widely adopted for speech and facial growth, with other areas of outcome presenting greater problems in development of suitable measures. In recent years, the emphasis of outcome evaluation has turned towards greater reliance on patient-reported measures that require extensive preliminary research to develop if a high degree of validity is to be ensured. Existing outcome measures that are widely used are described in this chapter, along with a perspective for future trends and a forthcoming internationally applicable tool for comparative studies (ICHOM).

scholarly journals Intranasal Ectopic Tooth in Adult and Pediatric Patients: A Report of Two Cases

2019 ◽  
Vol 2019 ◽  
pp. 1-5
Author(s):  
Isabela Polesi Bergamaschi ◽  
Bernardo Olsson ◽  
Aline Monise Sebastiani ◽  
Guilherme dos Santos Trento ◽  
Nelson Luis Barbosa Rebellato ◽  
...  
Keyword(s):  
Cleft Lip ◽  
Cleft Lip And Palate ◽  
Case Reports ◽  
Facial Trauma ◽  
Surgical Removal ◽  
Safe Procedure ◽  
Main Complaint ◽  
First Case ◽  
Ectopic Tooth

The aim of this study was to report two rare cases of ectopic tooth into the nasal cavity. The first case reports a 32-year-old female patient with the main complaint of having a tooth inside her nose. According to her, this condition causes pain and sporadic nosebleed. The patient had a facial trauma when she was 6 years old. The second case refers to an 8-year-old girl with left incomplete unilateral cleft lip and palate. The main complaint was left-sided nasal obstruction by a white hard mass. The treatment for both cases was surgical removal of the ectopic erupted tooth under general anesthesia. In conclusion, we can state that the surgical removal of intranasal tooth is a safe procedure and improves patient’s quality of life.

Lobar Holoprosencephaly with a Median Cleft: Case Report

2009 ◽  
Vol 46 (5) ◽  
pp. 549-554 ◽  
Author(s):  
Elżbieta Gawrych ◽  
Joanna Janiszewska-Olszowska ◽  
Anna Walecka ◽  
Maria Syryńska ◽  
Hanna Chojnacka
Keyword(s):  
Cleft Lip ◽  
Cleft Lip And Palate ◽  
Brain Abnormalities ◽  
Facial Deformity ◽  
Unique Case ◽  
Craniofacial Malformations ◽  
Live Births ◽  
Facial Defects ◽  
Median Cleft

Holoprosencephaly is a congenital abnormality of the prosencephalon associated with median facial defects. Its frequency is 1 in 250 pregnancies and 1 in 16,000 live births. The degree of facial deformity usually correlates with the severity of brain malformation. Early mortality is prevalent in severe forms. This report presents a child with lobar holoprosencephaly accompanied by median cleft lip and palate. The treatment and 9 months’ follow-up are presented. This unique case shows that holoprosencephaly may present different manifestations of craniofacial malformations, which are not always parallel to the severity of brain abnormalities. Patients with mild to moderate brain abnormalities may survive into childhood and beyond.

scholarly journals Maxillary Growth Evaluation After Cleft Palate Repair Using Goslon Criteria: Preliminary Study

1970 ◽  
Vol 1 (3) ◽  
Author(s):  
Huntal Simamora ◽  
Evie Lamtiur ◽  
Nur A. ◽  
Siti Handayani ◽  
Kristaninta Bangun
Keyword(s):  
Cleft Lip ◽  
Cleft Lip And Palate ◽  
Alveolar Bone ◽  
Mean Value ◽  
Treatment Result ◽  
Maxillary Hypoplasia ◽  
Post Surgery ◽  
Cleft Lip Palate ◽  
Palate Repair ◽  
Maxillary Growth

Background: The goal of palatoplasty is to achieve normal maxillofacial growth, normal speech, and prevent hearing loss. Disturbance of maxillary growth may occur in cleft lip palate patients after palatoplasty. To determine how many patients later developed a disrupted maxillary growth following operations, a retrospective study was designed to evaluate patients with complete unilateral cleft lip and palate who have undergone two-flap palatoplasty.Methods:A retrospective analytic study evaluated the maxillary growth of 15 consecutive unilateral cleft lip and palate patient aged around 8-year-old treated in the Division of Plastic Surgery Cipto Mangunkusumo Hospital, Jakarta. Cephalogram and dental study models were used to assess growth. Cleft lip and palate repair were performed to all patients without alveolar bone graft or any orthodontic treatment. Result: The cephalogram shows that 53,3% of the patients developed maxillary hypoplasia post palatoplasty. Mean value of the Goslon Yardstick was 3,53 (intermediate category by Goslon criteria).No patient fell into the Goslon 1 or 5 categories. Discussion: Disturbed maxillary growth is postulated to be caused by the manipulation and suturing of the maxillary vomer, and scarring of the dentoalveoli post-surgery. Another contributing factor is the intrinsic tissue deficiency. Conclusion: Maxillary hypoplasia is a possible complication following two !ap palatopasty, affecting either anteroposterior, transversal and vertical maxillary growth. This finding needs to be proven especially after the process of growth ceased. It is highly probable that maxillary disruption is higher when the two flap palatoplasty technique leaves lateral areas of denuded bone on the maxillary tuberosity.

scholarly journals The correlation between the severity of anterior crossbite and skeletal deformities in post-surgery cleft lip and palate among children

2020 ◽  
Vol 32 (3) ◽  
pp. 227
Author(s):  
Prastiwi Setianingtyas ◽  
Risti Saptarini Primarti ◽  
Lucky Riawan ◽  
Fahmi Oscandar
Keyword(s):  
Cleft Lip ◽  
Cleft Lip And Palate ◽  
Rank Correlation ◽  
Primary Dentition ◽  
Congenital Deformity ◽  
P Value ◽  
Weak Correlation ◽  
Skeletal Deformities ◽  
Post Surgery ◽  
High Level

Introduction: Cleft lip and palate is the most common craniofacial malformations, which is a congenital deformity of lip and palate or both. Anterior crossbite is occlusal characteristics that are often found in patients with cleft lip and palate who had surgery, caused by dentoalveolar or skeletal abnormalities, can be distinguished based on the cephalometric analysis. This research was aimed to analyse the correlation between the severity of anterior crossbite and skeletal deformities in post-surgery cleft lip and palate among children. Methods: The research design was an analytic correlation with the sample selection based on purposive sampling. The research was conducted from 14 cleft lip and palate patients in the primary dentition (aged 4-6 years old) who had surgery (for 2-3 years) using analysis of study models and cephalometric digital. Statistical analysis was conducted by Spearman Rank Correlation Coefficient test to analyse the relationship between the severity of anterior crossbite with skeletal deformities. Results: Statistic test showed that 42.86% of the anterior crossbite in the cleft lip and palate post-surgery in primary dentition had a very high level of severity, thus leading to very poor occlusion. As many as 21.43% had a high level of severity, which leads to poor occlusion, and 35.71% had a moderate level of severity, which leads to fair occlusion. The Spearman Coefficient of Rank Correlation test results showed a weak correlation between the severity of anterior crossbite with skeletal deformities with coefficient relation of 0.13 and p-value of 0.48 (p<0.05). Conclusion: There is a weak correlation between the severity of anterior crossbite with skeletal deformities in post-surgery cleft lip and palate among children.

Sphenoethmoidal meningoencephalocele associated with agenesis of corpus callosum and median cleft lip and palate

1979 ◽  
Vol 51 (3) ◽  
pp. 397-401 ◽  
Author(s):  
Katsuaki Sakoda ◽  
Susumu Ishikawa ◽  
Tohru Uozumi ◽  
Katsuhiro Hirakawa ◽  
Hideo Okazaki ◽  
...  
Keyword(s):  
Congenital Anomaly ◽  
Corpus Callosum ◽  
Cleft Lip ◽  
Cleft Lip And Palate ◽  
Distinct Type ◽  
Agenesis Of Corpus Callosum ◽  
Content Type ◽  
Median Cleft ◽  
Fine Print

✓ A case of sphenoethmoidal meningoencephalocele associated with agenesis of the corpus callosum and median cleft lip and palate in a baby boy is reported. Two other cases have been reported previously presenting exactly the same findings. It is possible that these malformations constitute a distinct type of congenital anomaly.

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