Primary Pulmonary Artery Sarcoma Presenting as a Massive Pulmonary Embolism

CHEST Journal ◽  
2015 ◽  
Vol 148 (4) ◽  
pp. 981A
Author(s):  
Umair Tariq ◽  
Marina Dolina
Keyword(s):  
Pulmonary Embolism ◽  
Pulmonary Artery ◽  
Massive Pulmonary Embolism ◽  
Pulmonary Artery Sarcoma ◽  
Primary Pulmonary Artery Sarcoma

scholarly journals A Case Report of Primary Pulmonary Artery Intimal Sarcoma

2021 ◽  
Author(s):  
Xiaofang Bai ◽  
Litao Ruan
Keyword(s):  
Pulmonary Embolism ◽  
Pulmonary Artery ◽  
Surgical Excision ◽  
Final Diagnosis ◽  
Initial Symptom ◽  
Pulmonary Artery Sarcoma ◽  
Intimal Sarcoma ◽  
Delayed Treatment ◽  
Primary Pulmonary Artery Sarcoma ◽  
Relationship Of

Abstract Background: Pulmonary artery intimal sarcoma(PAS) is a very rare disease, the prevalence of it is about 0.001%-0.003%1. PAS is often misdiagnosed as acute or chronic pulmonary thromboembolism due to its clinical presentation and radiological findings. Thus early diagnosis is very crucial and may improve patient outcome.Case presentation: Here we report a case in a Chinese male which the symptom as presentation was episodes of shortness of breath. Transthoracic echocardiography showed a solid mass in the pulmonary valve orifice, which was demonstrated to be a pulmonary artery intimal sarcoma diagnosed by histopathology2. In this case the initial differential diagnosis included pulmonary embolism. Because the initial symptom of primary pulmonary artery sarcoma is extremely similiar to the pulmonary embolism. Half of them may be misdiagnosed as pulmonary embolism. Imaging studies are very helpful. Ultrasound and CT are the best due to their resolution and ability to assess the relationship of the mass with the surrounding structures. The final diagnosis is mostly made after surgical excision and this is the most effective treatment. At the same time, radiotherapy and chemotherapy after surgery is also a adjuvant treatment3.Conclusion: We report a very rare case of pulmonary artery intimal sarcoma, due to late diagnosis and delayed treatment in this case, the patient display a poor prognostic. Early diagnosis and right treatment can improve the prognosis of PAS and optimize overall health.

scholarly journals Primary pulmonary artery sarcoma masquerading as pulmonary embolism: role of cardiac MRI

2016 ◽  
Vol 37 (18) ◽  
pp. 1479-1479 ◽  
Author(s):  
Prabhjot Singh Nijjar ◽  
Fahad M. Iqbal ◽  
M. Chadi Alraies ◽  
Uma S. Valeti ◽  
S. Murthy Tadavarthy
Keyword(s):  
Pulmonary Embolism ◽  
Pulmonary Artery ◽  
Cardiac Mri ◽  
Pulmonary Artery Sarcoma ◽  
Primary Pulmonary Artery Sarcoma

Primary Pulmonary Artery Sarcoma Masquerades as Pulmonary Embolism: 20 Year Observational Analysis

CHEST Journal ◽  
2014 ◽  
Vol 146 (4) ◽  
pp. 833A
Author(s):  
Debabrata Bandyopadhyay ◽  
Mathew Bunte ◽  
Tanmay Panchabhai ◽  
Navkaran Bajaj ◽  
Nicholas Smedira ◽  
...  
Keyword(s):  
Pulmonary Embolism ◽  
Pulmonary Artery ◽  
Pulmonary Artery Sarcoma ◽  
Observational Analysis ◽  
Primary Pulmonary Artery Sarcoma

scholarly journals A case report of primary pulmonary artery intimal sarcoma

2021 ◽  
Vol 26 (1) ◽  
Author(s):  
Xiaofang Bai ◽  
Litao Ruan
Keyword(s):  
Pulmonary Embolism ◽  
Early Diagnosis ◽  
Pulmonary Artery ◽  
Surgical Excision ◽  
Final Diagnosis ◽  
Initial Symptom ◽  
Pulmonary Artery Sarcoma ◽  
Intimal Sarcoma ◽  
Delayed Treatment ◽  
Primary Pulmonary Artery Sarcoma

Abstract Background Pulmonary artery intimal sarcoma (PAS) is a very rare disease, its prevalence is about 0.001–0.003%. PAS is often misdiagnosed as acute or chronic pulmonary thromboembolism due to its clinical presentation and radiological findings. Thus, early diagnosis is very crucial and may improve patient outcome. Case presentation Here, we report a case in a Chinese male where the symptom presentation was episodes of shortness of breath. Transthoracic echocardiography showed a solid mass in the pulmonary valve orifice, which was demonstrated to be a pulmonary artery intimal sarcoma diagnosed by histopathology. In this case, the initial differential diagnosis included pulmonary embolism. Because the initial symptom of primary pulmonary artery sarcoma is extremely similar to the pulmonary embolism, half of them may be misdiagnosed as pulmonary embolism. Imaging studies are very helpful. Ultrasound and CT are the best due to their resolution and ability to assess the relationship of the mass with the surrounding structures. The final diagnosis is mostly made after surgical excision and this is the most effective treatment. At the same time, radiotherapy and chemotherapy after surgery is also an adjuvant treatment. Conclusion We report a very rare case of pulmonary artery intimal sarcoma. Due to late diagnosis and delayed treatment in this case, the patient displayed a poor prognostic. Early diagnosis and right treatment can improve the prognosis of PAS and optimize overall health.

scholarly journals Primary pulmonary artery sarcoma: a close associate of pulmonary embolism—20-year observational analysis

2016 ◽  
Vol 8 (9) ◽  
pp. 2592-2601 ◽  
Author(s):  
Debabrata Bandyopadhyay ◽  
Tanmay S. Panchabhai ◽  
Navkaranbir S. Bajaj ◽  
Pradnya D. Patil ◽  
Matthew C. Bunte
Keyword(s):  
Pulmonary Embolism ◽  
Pulmonary Artery ◽  
Pulmonary Artery Sarcoma ◽  
Observational Analysis ◽  
Primary Pulmonary Artery Sarcoma

scholarly journals Pulmonary Artery Sarcoma Mimicking Pulmonary Embolism

2014 ◽  
Vol 41 (5) ◽  
pp. 515-517 ◽  
Author(s):  
Magdy M. El-Sayed Ahmed ◽  
Muhammad Aftab ◽  
Raed M. Al-Najjar ◽  
Kim I. de la Cruz ◽  
Robert S. Benjamin ◽  
...  
Keyword(s):  
Pulmonary Embolism ◽  
Pulmonary Artery ◽  
Right Ventricular Outflow Tract ◽  
Poor Response ◽  
Ventricular Outflow Tract ◽  
Large Mass ◽  
Massive Pulmonary Embolism ◽  
Acute Onset ◽  
Pulmonary Artery Sarcoma ◽  
Native Valve

Primary sarcomas that arise from major blood vessels are exceedingly rare, and some of the published cases have been autopsy reports. Most patients are adults. We report a case of pulmonary artery sarcoma in a 77-year-old man who presented with acute onset of dyspnea. Magnetic resonance imaging of the chest revealed a large mass within the pulmonary trunk and its main branches. Because massive pulmonary embolism was suspected, both anticoagulant and thrombolytic therapies were initiated. The patient responded poorly to these therapies, which then necessitated resection of both the mass and the pulmonary valve. A bioprosthetic porcine valve replaced the native valve, and we reconstructed the right ventricular outflow tract with a Dacron patch. Histopathologic examination revealed a high-grade sarcoma with focal myogenic and chondrogenic differentiation. The patient tolerated the procedure well and was discharged from the hospital on postoperative day 7. He was subsequently treated with chemotherapy and radiation and continued to show no evidence of disease. The diagnosis of pulmonary artery sarcoma should be suspected in patients who present with manifestations of pulmonary embolism, especially when there is no evidence of deep venous thrombosis and poor response to anticoagulant therapy. Multimodal therapy can provide prolonged survival.

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