scholarly journals Inflammatory Cerebral Amyloid Angiopathy, Amyloid-β–Related Angiitis, and Primary Angiitis of the Central Nervous System

Stroke ◽  
2015 ◽  
Vol 46 (9) ◽  
Author(s):  
Aimen Moussaddy ◽  
Ariel Levy ◽  
Daniel Strbian ◽  
Sophia Sundararajan ◽  
France Berthelet ◽  
...  
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Cerebral Amyloid Angiopathy ◽  
Amyloid Β ◽  
Amyloid Angiopathy ◽  
Primary Angiitis ◽  
The Central Nervous System ◽  
Cerebral Amyloid

Clinicopathological Review: Primary Angiitis of the Central Nervous System in Association with Cerebral Amyloid Angiopathy

Neurosurgery ◽  
2003 ◽  
Vol 53 (1) ◽  
pp. 136-143 ◽  
Author(s):  
Rafael J. Tamargo ◽  
E. Sander Connolly ◽  
Guy M. McKhann ◽  
Alexander Khandji ◽  
Yuan Chang ◽  
...  
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Cerebral Amyloid Angiopathy ◽  
Amyloid Angiopathy ◽  
Primary Angiitis ◽  
The Central Nervous System ◽  
Cerebral Amyloid

Serial CT and MRI findings in a patient with isolated angiitis of the central nervous system associated with cerebral amyloid angiopathy

Amyloid ◽  
2002 ◽  
Vol 9 (4) ◽  
pp. 256-262 ◽  
Author(s):  
Takashi Oide ◽  
Takahiko Tokuda ◽  
Yo-Ichi Takei ◽  
Hitoshi Takahashi ◽  
Kenjiro Ito ◽  
...  
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Cerebral Amyloid Angiopathy ◽  
Amyloid Angiopathy ◽  
Mri Findings ◽  
The Central Nervous System ◽  
Serial Ct ◽  
Cerebral Amyloid ◽  
Ct And Mri

scholarly journals Multiple infarcts and hemorrhages in the central nervous system of a dog with cerebral amyloid angiopathy: a case report

2018 ◽  
Vol 14 (1) ◽  
Author(s):  
Laís Limeira Rodrigues ◽  
Leonardo Pereira Mesquita ◽  
Rafael Carneiro Costa ◽  
Raquel Gonçalves Gomes ◽  
Daniel Arrais Biihrer ◽  
...  
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Case Report ◽  
Cerebral Amyloid Angiopathy ◽  
Amyloid Angiopathy ◽  
The Central Nervous System ◽  
Cerebral Amyloid

scholarly journals Primary central nervous system vasculitis: comparison of patients with and without cerebral amyloid angiopathy

Rheumatology ◽  
2008 ◽  
Vol 47 (11) ◽  
pp. 1671-1677 ◽  
Author(s):  
C. Salvarani ◽  
R. D. Brown ◽  
K. T. Calamia ◽  
T. J. H. Christianson ◽  
J. Huston ◽  
...  
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Cerebral Amyloid Angiopathy ◽  
Amyloid Angiopathy ◽  
Central Nervous System Vasculitis ◽  
Cerebral Amyloid

scholarly journals Amyloid β-related Angiitis of the Central Nervous System: Report of 3 Cases

2011 ◽  
Vol 38 (4) ◽  
pp. 626-630 ◽  
Author(s):  
Heather Rigby ◽  
Alexander Easton ◽  
Virender Bhan
Keyword(s):  
Alzheimer’S Disease ◽  
Alzheimer's Disease ◽  
Central Nervous System ◽  
Nervous System ◽  
Tertiary Care ◽  
Amyloid Β ◽  
Amyloid Angiopathy ◽  
Radiographic Findings ◽  
The Central Nervous System ◽  
Vessel Walls

Objective:Amyloid-β (Aβ) related angiitis (ABRA) is a recently described clinicopathological entity characterized by cerebrovascular Aβ deposition and arteritis. Cerebral Aβ deposition is commonly present in cerebal amyloid angiopathy (CAA) and Alzheimer's disease (AD) but is rarely associated with inflammatory infiltration of vessel walls. Our objective is to help clarify the clinical spectrum, radiographic findings, response to treatment, and outcomes of ABRA. The neuropathological relationship between ABRA, cerebral amyloid angiopathy, and Alzheimer's disease is discussed.Methods:We present three cases of ABRA managed at a tertiary care centre.Results:All three patients presented with seizures and cognitive dysfunction; one had multifocal neurologic findings. Brain biopsies revealed inflammatory arteritis with Aβ deposits in the vessel walls. All were treated with steroids and cyclophosphamide. Two had favorable outcomes and one stabilized but with severe residual neurologic disability.Conclusions:ABRA is an unusual but likely under-recognized and potentially treatable disorder. As in other reported cases, our findings suggest that many patients respond favorably to immunosuppressive therapy. We believe that all biopsy specimens consistent with primary angiitis of the central nervous system (CNS) should be further examined for vascular Aβ deposition.

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